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GM00436 female affected XPD sample

Identifiers
BioSample: SAMN00795056; Coriell: GM00436
Organism
Homo sapiens (human)
cellular organisms; Eukaryota; Opisthokonta; Metazoa; Eumetazoa; Bilateria; Deuterostomia; Chordata; Craniata; Vertebrata; Gnathostomata; Teleostomi; Euteleostomi; Sarcopterygii; Dipnotetrapodomorpha; Tetrapoda; Amniota; Mammalia; Theria; Eutheria; Boreoeutheria; Euarchontoglires; Primates; Haplorrhini; Simiiformes; Catarrhini; Hominoidea; Hominidae; Homininae; Homo
Attributes
cell lineGM00436
sexFemale
cell typeFibroblast
raceCaucasian
age22 YR
GeneERCC2
affected_byXPD
Mutation45 bp deletion (c.2224-2268)
MutationGLY47ARG
MutationLEU461VAL
collectionNIGMS Human Genetic Cell Repository
Tags
XPD
Xeroderma pigmentosum, complementation group d
Excision-repair: complementing defective in chinese hamster 2
ERCC2
Description

XP1NE;near normal post UV unscheduled DNA synthesis;no neoplasias;donor subject is a compound heterozygote for several mutations in the ERCC2 gene: one allele carries a G-to-A substitution at nucleotide 217 (217G>A) which results in a change of Gly-47 to Arg GLY47ARG (G47R);a second allele carries a C-to-G transversion at nucleotide position 1411 (1411C>G) which results in a change of Leu-461 to Val Leu461Val (L461V);as well as a splicing mutation resulting in the deletion of 45 bases (2224_2268) in the cDNA and the loss of amino acids 716_730 from the protein (DEL 716_730).

Submission
Coriell; 2012-03-05
Accession:
SAMN00795056
ID:
795056

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