Table 7. [Recommended Surveillance for Individuals with Usher Syndrome Type II]. - GeneReviews®

System/Concern	Evaluation	Frequency
Hearing loss	Audiometry & tympanometry w/hearing aids or cochlear implant to assure adequate auditory stimulation	Annually, incl testing w/hearing aids in place
Cataracts	Ophthalmologic eval	Annually from age 20 yrs or age of diagnosis
Cystoid macular edema	Ophthalmologic eval
Retinitis pigmentosa	Fundus photography, VA, VF (Goldmann perimetry, Humphrey perimetry, dark adapted rod perimetry), ERG, OCT, FAF	Annually from age 10 yrs or age of diagnosis

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