Table 6.

Treatment of Manifestations in Individuals with Usher Syndrome Type II

Manifestation/
Concern		TreatmentConsiderations/Other
Hearing loss Hearing aidsYoung children benefit from early fitting of hearing aids & speech training.
Cochlear implantationChildren w/incomplete speech & sentence rehabilitation w/hearing aids & older persons w/severe-to-profound hearing loss: consider for cochlear implantation.
Retinitis
pigmentosa
  • See Retinitis Pigmentosa Overview, Management.
  • Argus II prosthesis 1
Tunnel vision & night blindness can ↑ likelihood of accidental injury.
Imbalance Vestibular rehabNeurologically active medications or sedatives can aggravate mild vestibular dysfunction.
1.

Nadal & Iglesias [2018] describe the visual outcomes and rehabilitation of a one individual with USH2 that underwent Argus II prosthesis surgery.

From: Usher Syndrome Type II

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