Table 6.

Treatment of Manifestations in Individuals with Usher Syndrome Type II

Hearing loss Hearing aidsYoung children benefit from early fitting of hearing aids & speech training.
Cochlear implantationChildren w/incomplete speech & sentence rehabilitation w/hearing aids & older persons w/severe-to-profound hearing loss: consider for cochlear implantation.
  • See Retinitis Pigmentosa Overview, Management.
  • Argus II prosthesis 1
Tunnel vision & night blindness can ↑ likelihood of accidental injury.
Imbalance Vestibular rehabNeurologically active medications or sedatives can aggravate mild vestibular dysfunction.

Nadal & Iglesias [2018] describe the visual outcomes and rehabilitation of a one individual with USH2 that underwent Argus II prosthesis surgery.

From: Usher Syndrome Type II

Cover of GeneReviews®
GeneReviews® [Internet].
Adam MP, Mirzaa GM, Pagon RA, et al., editors.
Seattle (WA): University of Washington, Seattle; 1993-2023.
Copyright © 1993-2023, University of Washington, Seattle. GeneReviews is a registered trademark of the University of Washington, Seattle. All rights reserved.

GeneReviews® chapters are owned by the University of Washington. Permission is hereby granted to reproduce, distribute, and translate copies of content materials for noncommercial research purposes only, provided that (i) credit for source ( and copyright (© 1993-2023 University of Washington) are included with each copy; (ii) a link to the original material is provided whenever the material is published elsewhere on the Web; and (iii) reproducers, distributors, and/or translators comply with the GeneReviews® Copyright Notice and Usage Disclaimer. No further modifications are allowed. For clarity, excerpts of GeneReviews chapters for use in lab reports and clinic notes are a permitted use.

For more information, see the GeneReviews® Copyright Notice and Usage Disclaimer.

For questions regarding permissions or whether a specified use is allowed, contact: ude.wu@tssamda.

NCBI Bookshelf. A service of the National Library of Medicine, National Institutes of Health.