Table 8.

Recommended Follow Up for Select Genetic Causes of Hearing Loss by Progression Type

Progression TypeGeneRecommended Testing Intervals
Generally stable or very slowly progressive OTOG
STRC
Yearly or biannually
Progressive COCH
GSDME
KCNQ4
MYO7A
MYO15A
SLC26A4
USH2A
WFS1
At least yearly; consider biannually for children
Fluctuating OTOF
SLC26A4

From: Genetic Hearing Loss Overview

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