F.1. Diagnosis of cystic fibrosis

Figure 1Flow diagram of clinical article selection for when to suspect CF review

F.2. Information and support

Figure 2Flow diagram of clinical article selection for information and support review

F.3. Service delivery

F.3.1. Service configuration

Figure 3Flow diagram of clinical article selection for service delivery - models of care review

F.3.2. Multidisciplinary teams

Figure 4Flow diagram of clinical article selection for service delivery: multi-disciplinary teams review

F.4. Transition

Figure 5Flow diagram of clinical article selection for the transition review

F.5. Complications of CF

Figure 6Flow diagram of clinical article selection for complications of CF review

F.6. Pulmonary monitoring

Figure 7Flow diagram of clinical article selection for pulmonary monitoring review

F.7. Airway clearance

Figure 8Flow diagram of clinical article selection for airway clearance techniques review

F.8. Mucoactive agents

Figure 9Flow diagram of clinical article selection for mucoactive agents review

F.9. Pulmonary infection

Figure 10Flow diagram of clinical article selection for antimicrobial prophylaxis review

F.10. Immunomodulatory agents

Figure 11Flow diagram of clinical article selection for Immunomodulatory agents review

F.11. Nutritional interventions

Figure 12Flow diagram of clinical article selection for nutrition review

F.12. Exocrine pancreatic insufficiency

Figure 13Flow diagram of clinical article selection for PERT review

F.13. Distal intestinal obstruction syndrome

Figure 14Flow diagram of clinical article selection for DIOS review

F.14. Liver disease

Figure 15Flow diagram of clinical article selection for ultrasound review

F.15. Ursodeoxycholic acid

Figure 16Flow diagram of clinical article selection for UDCA review

F.16. Cystic fibrosis related diabetes

Figure 17Flow diagram of clinical article selection for monitoring for the onset of cystic fibrosis related diabetes review

F.17. Bone Mineral density

Figure 18Flow diagram of clinical article selection for monitoring of bone mineral density review

F.18. Exercise

Figure 19Flow diagram of clinical article selection for exercise review

F.19. Psychological assessment

Figure 20Flow diagram of clinical article selection for assessment of psychological and behavioural problems review

F.20. Cross-infection control

Figure 21Flow diagram of clinical article selection for cross-infection control review

F.21. Health economics

Figure 22Flow diagram of selection for economic evaluations

The methods and results for each of those 16 economic evaluations will be presented in the appropriate sections below, whilst data extraction tables and quality assessments can be found in Appendix L and M, respectively.