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GTR Home > Conditions/Phenotypes > Heparin cofactor II deficiency

Summary

Heparin cofactor II (HCF2; 142360) rapidly inhibits thrombin in plasma in the presence of dermatan sulfate or heparin. Congenital HCF2 deficiency is associated with thromboembolism and is classified into type I (quantitative) or type II (qualitative) deficiency (Kondo et al., 1996). [from OMIM]

Available tests

11 tests are in the database for this condition.

Genes See tests for all associated and related genes

  • Also known as: D22S673, HC2, HCF2, HCII, HLS2, LS2, THPH10, SERPIND1
    Summary: serpin family D member 1

Clinical features

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