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GTR Home > Conditions/Phenotypes > Autosomal dominant nonsyndromic hearing loss 21


Autosomal dominant deafness-21 (DFNA21) is characterized by nonsyndromic progressive sensorineural hearing loss. The mean age at onset is 30.6 years, with a range from infancy to late adulthood. There is a high prevalence of this genetic form of deafness in the Dutch population (summary by de Bruijn et al., 2021). [from OMIM]

Available tests

2 tests are in the database for this condition.

Check Related conditions for additional relevant tests.

Genes See tests for all associated and related genes

  • Also known as: C6orf32, DFNA21, DFNB104, DIFF40, DIFF48, FAM65B, MYONAP, PL48, RIPOR2
    Summary: RHO family interacting cell polarization regulator 2

Clinical features


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