Progressive familial heart block, type 1A
- Synonyms
- Cardiac conduction defect progressive; HEART BLOCK, PROGRESSIVE FAMILIAL, TYPE I; Heart block progressive familial type 1; Heart block, progressive, type IA; Hereditary bundle branch system defect; PROGRESSIVE FAMILIAL HEART BLOCK, TYPE IA
Summary
Available tests
Check Related conditions for additional relevant tests.
Clinical tests (73 available)
Clinical features
Help- Abnormality of the cardiovascular system
- Complete heart block with broad QRS complexes
Complete heart block with broad QRS complexes
- MedGen UID: 1391206
- Concept ID: C4476543
- Finding: Disease or Syndrome
Abnormality of the cardiovascular system
- Left anterior fascicular block
Left anterior fascicular block
- MedGen UID: 75547
- Concept ID: C0264912
- Finding: Disease or Syndrome
Abnormality of the cardiovascular system
- Left posterior fascicular block
Left posterior fascicular block
- MedGen UID: 78115
- Concept ID: C0264913
- Finding: Disease or Syndrome
Abnormality of the cardiovascular system
- Prolonged PR interval
Prolonged PR interval
- MedGen UID: 154645
- Concept ID: C0600125
- Finding: Finding
Abnormality of the cardiovascular system
- Right bundle branch block
Right bundle branch block
- MedGen UID: 88445
- Concept ID: C0085615
- Finding: Disease or Syndrome
Abnormality of the cardiovascular system
- Syncope
Syncope
- MedGen UID: 21443
- Concept ID: C0039070
- Finding: Sign or Symptom
Abnormality of the cardiovascular system
- Complete heart block with broad QRS complexes
- Abnormality of the respiratory system
- Dyspnea
Dyspnea
- MedGen UID: 3938
- Concept ID: C0013404
- Finding: Sign or Symptom
Abnormality of the respiratory system
- Dyspnea
- Constitutional symptom
- Sudden cardiac death
Sudden cardiac death
- MedGen UID: 38841
- Concept ID: C0085298
- Finding: Pathologic Function
Constitutional symptom
- Sudden death
Sudden death
- MedGen UID: 8257
- Concept ID: C0011071
- Finding: Pathologic Function
Constitutional symptom
- Sudden cardiac death
- HRS/EHRA/APHRS, 2013Executive summary: HRS/EHRA/APHRS expert consensus statement on the diagnosis and management of patients with inherited primary arrhythmia syndromes.
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