U.S. flag

An official website of the United States government

GTR Home > Conditions/Phenotypes > Idiopathic pulmonary arterial hypertension

Idiopathic pulmonary arterial hypertension

Summary

Idiopathic pulmonary arterial hypertension (IPAH) is a sporadic form of pulmonary arterial hypertension (PAH, see this term) characterized by elevated pulmonary arterial resistance leading to right heart failure. IPAH is progressive and potentially fatal and not associated with an underlying condition or family history of PAH. [from ORDO]

Genes See tests for all associated and related genes

  • Related genesHelp

IMPORTANT NOTE: NIH does not independently verify information submitted to the GTR; it relies on submitters to provide information that is accurate and not misleading. NIH makes no endorsements of tests or laboratories listed in the GTR. GTR is not a substitute for medical advice. Patients and consumers with specific questions about a genetic test should contact a health care provider or a genetics professional.