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Cerebellar Ependymal Tumor

MedGen UID:
1373926
Concept ID:
C4329642
Neoplastic Process

Definition

A finding indicating the presence of an ependymal tumor in the cerebellum. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCerebellar Ependymal Tumor

Recent clinical studies

Etiology

Sorajja N, Moore KJ, Sample JM, Hubbard AK, Williams LA
Cancer Epidemiol 2022 Jun;78:102151. Epub 2022 Apr 5 doi: 10.1016/j.canep.2022.102151. PMID: 35395483
Park KB, Chapman T, Aldinger KA, Mirzaa GM, Zeiger J, Beck A, Glass IA, Hevner RF, Jansen AC, Marshall DA, Oegema R, Parrini E, Saneto RP, Curry CJ, Hall JG, Guerrini R, Leventer RJ, Dobyns WB
Am J Med Genet A 2021 Sep;185(9):2690-2718. Epub 2020 Nov 18 doi: 10.1002/ajmg.a.61972. PMID: 33205886Free PMC Article
Debnam JM, Mayer RR, Chi TL, Ketonen L, Weinberg JS, Wei W, Groves MD, Guha-Thakurta N
J Clin Neurosci 2017 Nov;45:252-256. Epub 2017 Aug 9 doi: 10.1016/j.jocn.2017.07.020. PMID: 28802798
de Vries LS, Verboon-Maciolek MA, Cowan FM, Groenendaal F
Early Hum Dev 2006 Dec;82(12):819-25. Epub 2006 Oct 23 doi: 10.1016/j.earlhumdev.2006.09.006. PMID: 17059873
McComb RD, Burger PC
Neurol Clin 1985 Nov;3(4):711-28. PMID: 3001488

Diagnosis

Sorajja N, Moore KJ, Sample JM, Hubbard AK, Williams LA
Cancer Epidemiol 2022 Jun;78:102151. Epub 2022 Apr 5 doi: 10.1016/j.canep.2022.102151. PMID: 35395483
Zhang XP, Liu Y, Zhang D, Zheng Q, Wang C, Wang L, Li QC, Qiu XS, Wang EH
Diagn Pathol 2017 Mar 20;12(1):28. doi: 10.1186/s13000-017-0619-2. PMID: 28320419Free PMC Article
Khanlou N, Shintaku P, Yi J, Moatamed NA
Appl Immunohistochem Mol Morphol 2016 Mar;24(3):207-9. doi: 10.1097/PAI.0000000000000192. PMID: 26371431
de Vries LS, Verboon-Maciolek MA, Cowan FM, Groenendaal F
Early Hum Dev 2006 Dec;82(12):819-25. Epub 2006 Oct 23 doi: 10.1016/j.earlhumdev.2006.09.006. PMID: 17059873
McComb RD, Burger PC
Neurol Clin 1985 Nov;3(4):711-28. PMID: 3001488

Therapy

Johnston DL, Keene D, Bartels U, Carret AS, Crooks B, Eisenstat D, Fryer C, Lafay-Cousin L, Larouche V, Moghrabi A, Wilson B, Zelcer S, Silva M, Brossard J, Bouffet E
J Neurooncol 2010 Sep;99(2):243-9. Epub 2010 Feb 5 doi: 10.1007/s11060-010-0123-y. PMID: 20135195
Mobley B, Kalani MY, Harsh GR 4th, Edwards MS, Vogel H
Am J Surg Pathol 2009 Aug;33(8):1191-7. doi: 10.1097/PAS.0b013e31819c45ca. PMID: 19417584
Maruyama K, Morita A, Shibahara J, Nakazato Y, Kirino T
Neurol Med Chir (Tokyo) 2005 Aug;45(8):411-4. doi: 10.2176/nmc.45.411. PMID: 16127260

Prognosis

Sorajja N, Moore KJ, Sample JM, Hubbard AK, Williams LA
Cancer Epidemiol 2022 Jun;78:102151. Epub 2022 Apr 5 doi: 10.1016/j.canep.2022.102151. PMID: 35395483
Mata-Mbemba D, Zapotocky M, Laughlin S, Taylor MD, Ramaswamy V, Raybaud C
AJNR Am J Neuroradiol 2018 May;39(5):949-955. Epub 2018 Mar 15 doi: 10.3174/ajnr.A5578. PMID: 29545246Free PMC Article
Zhang XP, Liu Y, Zhang D, Zheng Q, Wang C, Wang L, Li QC, Qiu XS, Wang EH
Diagn Pathol 2017 Mar 20;12(1):28. doi: 10.1186/s13000-017-0619-2. PMID: 28320419Free PMC Article
Giuffrè R
Childs Nerv Syst 1989 Apr;5(2):55-9. doi: 10.1007/BF00571110. PMID: 2660986
McComb RD, Burger PC
Neurol Clin 1985 Nov;3(4):711-28. PMID: 3001488

Clinical prediction guides

Marsecano C, Bruno F, Michelini G, Perri M, Calvisi G, Di Cesare E, Splendiani A
Neuroradiol J 2017 Jun;30(3):274-280. Epub 2017 Jan 1 doi: 10.1177/1971400916689371. PMID: 28627990Free PMC Article
Zhang XP, Liu Y, Zhang D, Zheng Q, Wang C, Wang L, Li QC, Qiu XS, Wang EH
Diagn Pathol 2017 Mar 20;12(1):28. doi: 10.1186/s13000-017-0619-2. PMID: 28320419Free PMC Article
Hirano A, Hirano M
Neuropathology 2004 Mar;24(1):1-7. doi: 10.1111/j.1440-1789.2003.00526.x. PMID: 15068166
Akutsu H, Shibata Y, Okazaki M, Hyodo A, Matsumura A
Neurosurgery 2000 Dec;47(6):1434-7; discussion 1437-8. PMID: 11126915
Yates AJ, Franklin TK, McKinney P, Collins R, Comas T, Boesel CP, Pearl DK
J Mol Neurosci 1999 Apr;12(2):111-21. doi: 10.1007/BF02736925. PMID: 10527455

Supplemental Content

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