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Abnormal pulmonary vein physiology

MedGen UID:
1382214
•Concept ID:
C4476884
•
Finding
HPO: HP:0030969

Definition

An abnormality of the function of the pulmonary veins. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal pulmonary vein physiology

Professional guidelines

PubMed

Vein of Galen aneurysmal malformation: rationalizing medical management of neonatal heart failure.
Cory MJ, Durand P, Sillero R, Morin L, Savani R, Chalak L, Angelis D
Pediatr Res 2023 Jan;93(1):39-48. Epub 2022 Apr 14 doi: 10.1038/s41390-022-02064-1. PMID: 35422084
The frequency and efficacy of genetic testing in individuals with scimitar syndrome.
Fick TA, Scott DA, Lupo PJ, Weigand J, Morris SA
Cardiol Young 2022 Apr;32(4):550-557. Epub 2021 Jul 2 doi: 10.1017/S1047951121002535. PMID: 34210367Free PMC Article
Pulmonary vein stenosis: Treatment and challenges.
Vanderlaan RD, Rome J, Hirsch R, Ivy D, Caldarone CA
J Thorac Cardiovasc Surg 2021 Jun;161(6):2169-2176. Epub 2020 Jun 27 doi: 10.1016/j.jtcvs.2020.05.117. PMID: 32763037

Recent clinical studies

Etiology

Outcomes and Risk Factors of Interventions for Pediatric Post-operative Pulmonary Vein Stenosis.
Fujita KT, DiLorenzo MP, Krishnan US, Turner ME, Barry OM, Torres AJ, Bacha EA, Kalfa D, Crystal MA
Pediatr Cardiol 2023 Dec;44(8):1778-1787. Epub 2023 Jul 9 doi: 10.1007/s00246-023-03214-w. PMID: 37422845
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Cardiomyopathy With Restrictive Physiology in Sickle Cell Disease.
Niss O, Quinn CT, Lane A, Daily J, Khoury PR, Bakeer N, Kimball TR, Towbin JA, Malik P, Taylor MD
JACC Cardiovasc Imaging 2016 Mar;9(3):243-52. Epub 2016 Feb 17 doi: 10.1016/j.jcmg.2015.05.013. PMID: 26897687Free PMC Article
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Pulmonary hypertension in CKD.
Bolignano D, Rastelli S, Agarwal R, Fliser D, Massy Z, Ortiz A, Wiecek A, Martinez-Castelao A, Covic A, Goldsmith D, Suleymanlar G, Lindholm B, Parati G, Sicari R, Gargani L, Mallamaci F, London G, Zoccali C
Am J Kidney Dis 2013 Apr;61(4):612-22. Epub 2012 Nov 17 doi: 10.1053/j.ajkd.2012.07.029. PMID: 23164943

Diagnosis

Update on pulmonary arteriovenous malformations.
Salibe-Filho W, Oliveira FR, Terra-Filho M
J Bras Pneumol 2023;49(2):e20220359. Epub 2023 May 1 doi: 10.36416/1806-3756/e20220359. PMID: 37132738Free PMC Article
Pulmonary vein stenosis: Treatment and challenges.
Vanderlaan RD, Rome J, Hirsch R, Ivy D, Caldarone CA
J Thorac Cardiovasc Surg 2021 Jun;161(6):2169-2176. Epub 2020 Jun 27 doi: 10.1016/j.jtcvs.2020.05.117. PMID: 32763037
Congenital diaphragmatic hernia-associated pulmonary hypertension.
Gupta VS, Harting MT
Semin Perinatol 2020 Feb;44(1):151167. Epub 2019 Jul 30 doi: 10.1053/j.semperi.2019.07.006. PMID: 31519366
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954

Therapy

Menopausal hormone therapy and women's health: An umbrella review.
Zhang GQ, Chen JL, Luo Y, Mathur MB, Anagnostis P, Nurmatov U, Talibov M, Zhang J, Hawrylowicz CM, Lumsden MA, Critchley H, Sheikh A, Lundbäck B, Lässer C, Kankaanranta H, Lee SH, Nwaru BI
PLoS Med 2021 Aug;18(8):e1003731. Epub 2021 Aug 2 doi: 10.1371/journal.pmed.1003731. PMID: 34339416Free PMC Article
Somatic Mutations in UBA1 Define a Distinct Subset of Relapsing Polychondritis Patients With VEXAS.
Ferrada MA, Sikora KA, Luo Y, Wells KV, Patel B, Groarke EM, Ospina Cardona D, Rominger E, Hoffmann P, Le MT, Deng Z, Quinn KA, Rose E, Tsai WL, Wigerblad G, Goodspeed W, Jones A, Wilson L, Schnappauf O, Laird RS, Kim J, Allen C, Sirajuddin A, Chen M, Gadina M, Calvo KR, Kaplan MJ, Colbert RA, Aksentijevich I, Young NS, Savic S, Kastner DL, Ombrello AK, Beck DB, Grayson PC
Arthritis Rheumatol 2021 Oct;73(10):1886-1895. Epub 2021 Aug 31 doi: 10.1002/art.41743. PMID: 33779074
COVID-19 versus HIT hypercoagulability.
Warkentin TE, Kaatz S
Thromb Res 2020 Dec;196:38-51. Epub 2020 Aug 10 doi: 10.1016/j.thromres.2020.08.017. PMID: 32841919Free PMC Article
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Thromboprophylaxis for trauma patients.
Barrera LM, Perel P, Ker K, Cirocchi R, Farinella E, Morales Uribe CH
Cochrane Database Syst Rev 2013 Mar 28;(3):CD008303. doi: 10.1002/14651858.CD008303.pub2. PMID: 23543562

Prognosis

Diastology with Cardiac MRI: A Practical Guide.
Rajiah PS, Moore A, Broncano J, Anand V, Kolluri N, Shah DJ, Flamm SD, François CJ
Radiographics 2023 Aug;43(9):e220144. doi: 10.1148/rg.220144. PMID: 37535462
Update on pulmonary arteriovenous malformations.
Salibe-Filho W, Oliveira FR, Terra-Filho M
J Bras Pneumol 2023;49(2):e20220359. Epub 2023 May 1 doi: 10.36416/1806-3756/e20220359. PMID: 37132738Free PMC Article
COVID-19 versus HIT hypercoagulability.
Warkentin TE, Kaatz S
Thromb Res 2020 Dec;196:38-51. Epub 2020 Aug 10 doi: 10.1016/j.thromres.2020.08.017. PMID: 32841919Free PMC Article
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Cerebral vein thrombosis.
Martinelli I
Thromb Res 2013 Jan;131 Suppl 1:S51-4. doi: 10.1016/S0049-3848(13)70022-7. PMID: 23452743

Clinical prediction guides

Somatic Mutations in UBA1 Define a Distinct Subset of Relapsing Polychondritis Patients With VEXAS.
Ferrada MA, Sikora KA, Luo Y, Wells KV, Patel B, Groarke EM, Ospina Cardona D, Rominger E, Hoffmann P, Le MT, Deng Z, Quinn KA, Rose E, Tsai WL, Wigerblad G, Goodspeed W, Jones A, Wilson L, Schnappauf O, Laird RS, Kim J, Allen C, Sirajuddin A, Chen M, Gadina M, Calvo KR, Kaplan MJ, Colbert RA, Aksentijevich I, Young NS, Savic S, Kastner DL, Ombrello AK, Beck DB, Grayson PC
Arthritis Rheumatol 2021 Oct;73(10):1886-1895. Epub 2021 Aug 31 doi: 10.1002/art.41743. PMID: 33779074
COVID-19 versus HIT hypercoagulability.
Warkentin TE, Kaatz S
Thromb Res 2020 Dec;196:38-51. Epub 2020 Aug 10 doi: 10.1016/j.thromres.2020.08.017. PMID: 32841919Free PMC Article
Uncertain thrombophilia markers.
Franchini M, Martinelli I, Mannucci PM
Thromb Haemost 2016 Jan;115(1):25-30. Epub 2015 Aug 13 doi: 10.1160/TH15-06-0478. PMID: 26271270
The left atrial appendage: anatomy, function, and noninvasive evaluation.
Beigel R, Wunderlich NC, Ho SY, Arsanjani R, Siegel RJ
JACC Cardiovasc Imaging 2014 Dec;7(12):1251-65. doi: 10.1016/j.jcmg.2014.08.009. PMID: 25496544
Thromboprophylaxis for trauma patients.
Barrera LM, Perel P, Ker K, Cirocchi R, Farinella E, Morales Uribe CH
Cochrane Database Syst Rev 2013 Mar 28;(3):CD008303. doi: 10.1002/14651858.CD008303.pub2. PMID: 23543562

Recent systematic reviews

Tissue factor in COVID-19-associated coagulopathy.
Subramaniam S, Kothari H, Bosmann M
Thromb Res 2022 Dec;220:35-47. Epub 2022 Oct 1 doi: 10.1016/j.thromres.2022.09.025. PMID: 36265412Free PMC Article
A Systematic Review of Infective Endocarditis in Patients With Bovine Jugular Vein Valves Compared With Other Valve Types.
Sharma A, Cote AT, Hosking MCK, Harris KC
JACC Cardiovasc Interv 2017 Jul 24;10(14):1449-1458. doi: 10.1016/j.jcin.2017.04.025. PMID: 28728659
Sleep apnea and venous thromboembolism. A systematic review.
Lippi G, Mattiuzzi C, Franchini M
Thromb Haemost 2015 Nov;114(5):958-63. Epub 2015 May 21 doi: 10.1160/TH15-03-0188. PMID: 25994924
Thromboprophylaxis for trauma patients.
Barrera LM, Perel P, Ker K, Cirocchi R, Farinella E, Morales Uribe CH
Cochrane Database Syst Rev 2013 Mar 28;(3):CD008303. doi: 10.1002/14651858.CD008303.pub2. PMID: 23543562
Congenital portosystemic shunt: characterization of a multisystem disease.
Sokollik C, Bandsma RH, Gana JC, van den Heuvel M, Ling SC
J Pediatr Gastroenterol Nutr 2013 Jun;56(6):675-81. doi: 10.1097/MPG.0b013e31828b3750. PMID: 23412540

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