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Thoracic Spinal Cord Ependymal Tumor

MedGen UID:
1383650
•Concept ID:
C4331407
•
Neoplastic Process

Definition

A finding indicating the presence of an ependymal tumor in the thoracic region of spinal cord. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVThoracic Spinal Cord Ependymal Tumor

Recent clinical studies

Etiology

MYCN amplification drives an aggressive form of spinal ependymoma.
Ghasemi DR, Sill M, Okonechnikov K, Korshunov A, Yip S, Schutz PW, Scheie D, Kruse A, Harter PN, Kastelan M, Wagner M, Hartmann C, Benzel J, Maass KK, Khasraw M, Sträter R, Thomas C, Paulus W, Kratz CP, Witt H, Kawauchi D, Herold-Mende C, Sahm F, Brandner S, Kool M, Jones DTW, von Deimling A, Pfister SM, Reuss DE, Pajtler KW
Acta Neuropathol 2019 Dec;138(6):1075-1089. Epub 2019 Aug 14 doi: 10.1007/s00401-019-02056-2. PMID: 31414211Free PMC Article
Isolated Dorsal Thoracic Neuroenteric Cyst with Spinal Cord Compression: Case Reports in Pediatrics.
El Ahmadieh TY, Sillero R, Kafka B, Aoun SG, Price AV
World Neurosurg 2018 Oct;118:296-300. Epub 2018 Jul 25 doi: 10.1016/j.wneu.2018.07.147. PMID: 30055362
Recurrence rates and functional outcome after resection of intrinsic intramedullary tumors.
Schebesch KM, Mueller S, Wendl C, Brawanski A, Riemenschneider MJ, Proescholdt M
Clin Neurol Neurosurg 2015 Jul;134:60-6. Epub 2015 Apr 24 doi: 10.1016/j.clineuro.2015.04.006. PMID: 25950925
Spectrum of nonterminal myelocystoceles.
Rossi A, Piatelli G, Gandolfo C, Pavanello M, Hoffmann C, Van Goethem JW, Cama A, Tortori-Donati P
Neurosurgery 2006 Mar;58(3):509-15; discussion 509-15. doi: 10.1227/01.NEU.0000197122.92954.82. PMID: 16528191
MRI manifestations of leptomeningeal metastasis.
Chou MS, Tsai TC, Lin MB, Liu GC, Howng SL
Gaoxiong Yi Xue Ke Xue Za Zhi 1994 Apr;10(4):186-93. PMID: 8007048

Diagnosis

MYCN amplification drives an aggressive form of spinal ependymoma.
Ghasemi DR, Sill M, Okonechnikov K, Korshunov A, Yip S, Schutz PW, Scheie D, Kruse A, Harter PN, Kastelan M, Wagner M, Hartmann C, Benzel J, Maass KK, Khasraw M, Sträter R, Thomas C, Paulus W, Kratz CP, Witt H, Kawauchi D, Herold-Mende C, Sahm F, Brandner S, Kool M, Jones DTW, von Deimling A, Pfister SM, Reuss DE, Pajtler KW
Acta Neuropathol 2019 Dec;138(6):1075-1089. Epub 2019 Aug 14 doi: 10.1007/s00401-019-02056-2. PMID: 31414211Free PMC Article
Recurrence rates and functional outcome after resection of intrinsic intramedullary tumors.
Schebesch KM, Mueller S, Wendl C, Brawanski A, Riemenschneider MJ, Proescholdt M
Clin Neurol Neurosurg 2015 Jul;134:60-6. Epub 2015 Apr 24 doi: 10.1016/j.clineuro.2015.04.006. PMID: 25950925
Tanycytic ependymoma in a 76-year-old Puerto Rican male.
Ortiz Ydel M, Pérez Berenguer JL, Mercado Acosta J, Polo M, de Jesús-Garces O, Vega IE
Int J Clin Exp Pathol 2014;7(11):7789-94. Epub 2014 Oct 15 PMID: 25550817Free PMC Article
Spinal intramedullary ependymal cyst: a case report.
Iwahashi H, Kawai S, Watabe Y, Chitoku S, Akita N, Fuji T, Oda T
Surg Neurol 1999 Oct;52(4):357-61. doi: 10.1016/s0090-3019(99)00097-x. PMID: 10555841
MRI manifestations of leptomeningeal metastasis.
Chou MS, Tsai TC, Lin MB, Liu GC, Howng SL
Gaoxiong Yi Xue Ke Xue Za Zhi 1994 Apr;10(4):186-93. PMID: 8007048

Therapy

Papillary tumor of the spinal cord: report of 2 cases.
Mobley B, Kalani MY, Harsh GR 4th, Edwards MS, Vogel H
Am J Surg Pathol 2009 Aug;33(8):1191-7. doi: 10.1097/PAS.0b013e31819c45ca. PMID: 19417584

Prognosis

MYCN amplification drives an aggressive form of spinal ependymoma.
Ghasemi DR, Sill M, Okonechnikov K, Korshunov A, Yip S, Schutz PW, Scheie D, Kruse A, Harter PN, Kastelan M, Wagner M, Hartmann C, Benzel J, Maass KK, Khasraw M, Sträter R, Thomas C, Paulus W, Kratz CP, Witt H, Kawauchi D, Herold-Mende C, Sahm F, Brandner S, Kool M, Jones DTW, von Deimling A, Pfister SM, Reuss DE, Pajtler KW
Acta Neuropathol 2019 Dec;138(6):1075-1089. Epub 2019 Aug 14 doi: 10.1007/s00401-019-02056-2. PMID: 31414211Free PMC Article
Isolated Dorsal Thoracic Neuroenteric Cyst with Spinal Cord Compression: Case Reports in Pediatrics.
El Ahmadieh TY, Sillero R, Kafka B, Aoun SG, Price AV
World Neurosurg 2018 Oct;118:296-300. Epub 2018 Jul 25 doi: 10.1016/j.wneu.2018.07.147. PMID: 30055362
Recurrence rates and functional outcome after resection of intrinsic intramedullary tumors.
Schebesch KM, Mueller S, Wendl C, Brawanski A, Riemenschneider MJ, Proescholdt M
Clin Neurol Neurosurg 2015 Jul;134:60-6. Epub 2015 Apr 24 doi: 10.1016/j.clineuro.2015.04.006. PMID: 25950925
Spectrum of nonterminal myelocystoceles.
Rossi A, Piatelli G, Gandolfo C, Pavanello M, Hoffmann C, Van Goethem JW, Cama A, Tortori-Donati P
Neurosurgery 2006 Mar;58(3):509-15; discussion 509-15. doi: 10.1227/01.NEU.0000197122.92954.82. PMID: 16528191
Primary intradural extramedullary ependymoma: case report and review of the literature.
Duffau H, Gazzaz M, Kujas M, Fohanno D
Spine (Phila Pa 1976) 2000 Aug 1;25(15):1993-5. doi: 10.1097/00007632-200008010-00021. PMID: 10908946

Clinical prediction guides

MYCN amplification drives an aggressive form of spinal ependymoma.
Ghasemi DR, Sill M, Okonechnikov K, Korshunov A, Yip S, Schutz PW, Scheie D, Kruse A, Harter PN, Kastelan M, Wagner M, Hartmann C, Benzel J, Maass KK, Khasraw M, Sträter R, Thomas C, Paulus W, Kratz CP, Witt H, Kawauchi D, Herold-Mende C, Sahm F, Brandner S, Kool M, Jones DTW, von Deimling A, Pfister SM, Reuss DE, Pajtler KW
Acta Neuropathol 2019 Dec;138(6):1075-1089. Epub 2019 Aug 14 doi: 10.1007/s00401-019-02056-2. PMID: 31414211Free PMC Article
Recurrence rates and functional outcome after resection of intrinsic intramedullary tumors.
Schebesch KM, Mueller S, Wendl C, Brawanski A, Riemenschneider MJ, Proescholdt M
Clin Neurol Neurosurg 2015 Jul;134:60-6. Epub 2015 Apr 24 doi: 10.1016/j.clineuro.2015.04.006. PMID: 25950925
Spectrum of nonterminal myelocystoceles.
Rossi A, Piatelli G, Gandolfo C, Pavanello M, Hoffmann C, Van Goethem JW, Cama A, Tortori-Donati P
Neurosurgery 2006 Mar;58(3):509-15; discussion 509-15. doi: 10.1227/01.NEU.0000197122.92954.82. PMID: 16528191
Myxopapillary ependymoma with anaplastic features.
Awaya H, Kaneko M, Amatya VJ, Takeshima Y, Oka S, Inai K
Pathol Int 2003 Oct;53(10):700-3. doi: 10.1046/j.1440-1827.2003.01546.x. PMID: 14516321
MRI manifestations of leptomeningeal metastasis.
Chou MS, Tsai TC, Lin MB, Liu GC, Howng SL
Gaoxiong Yi Xue Ke Xue Za Zhi 1994 Apr;10(4):186-93. PMID: 8007048

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