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Coarctation in the transverse aortic arch

MedGen UID:
1385566
•Concept ID:
C4476934
•
Congenital Abnormality
HPO: HP:0031053

Definition

Narrowing or constriction of the aorta localized to the region of the transverse aortic arch. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCoarctation in the transverse aortic arch

Professional guidelines

PubMed

Validation of Prenatal Aortic Arch Angle Measurements in the Diagnosis of Neonatal Coarctation of the Aorta.
Freeman K, Kronmal R, Clouse M, Conwell J, Bhat A, Young L, Lewin M, Arya B
Pediatr Cardiol 2021 Aug;42(6):1365-1371. Epub 2021 Apr 26 doi: 10.1007/s00246-021-02620-2. PMID: 33903942
Improving Prenatal Diagnosis of Coarctation of the Aorta.
Morgan CT, Mueller B, Thakur V, Guerra V, Jull C, Mertens L, Friedberg M, Golding F, Seed M, Miner SES, Jaeggi ET, Manlhiot C, Nield LE
Can J Cardiol 2019 Apr;35(4):453-461. Epub 2018 Dec 17 doi: 10.1016/j.cjca.2018.12.019. PMID: 30935636
Diagnosing Neonatal Aortic Coarctation in the Setting of Patent Ductus Arteriosus.
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138

Recent clinical studies

Etiology

Echocardiographic score to predict neonatal surgery for aortic coarctation in newborns with prenatal suspicion and patent ductus arteriosus.
Bartolacelli Y, Palleri D, Balducci A, Ragni L, Hasan T, Bonetti S, Egidy Assenza G, Mariucci ME, Fabi M, Angeli E, Gargiulo GD, Donti A
J Matern Fetal Neonatal Med 2023 Dec;36(1):2201654. doi: 10.1080/14767058.2023.2201654. PMID: 37073133
A clinical prediction model to estimate the risk for coarctation of the aorta: From fetal to newborn life.
Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Preoperative Aortic Arch Size and Late Outcome After Coarctation Repair by Lateral Thoracotomy.
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Aortic arch repair in children with PHACE syndrome.
Caragher SP, Scott JP, Siegel DH, Mitchell ME, Frommelt PC, Drolet BA
J Thorac Cardiovasc Surg 2016 Sep;152(3):709-17. Epub 2016 Apr 14 doi: 10.1016/j.jtcvs.2016.03.082. PMID: 27160940
The neonatal hypoplastic aortic arch: decisions and more decisions.
Langley SM, Sunstrom RE, Reed RD, Rekito AJ, Gerrah R
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):43-51. doi: 10.1053/j.pcsu.2013.01.008. PMID: 23561817

Diagnosis

Echocardiographic score to predict neonatal surgery for aortic coarctation in newborns with prenatal suspicion and patent ductus arteriosus.
Bartolacelli Y, Palleri D, Balducci A, Ragni L, Hasan T, Bonetti S, Egidy Assenza G, Mariucci ME, Fabi M, Angeli E, Gargiulo GD, Donti A
J Matern Fetal Neonatal Med 2023 Dec;36(1):2201654. doi: 10.1080/14767058.2023.2201654. PMID: 37073133
A clinical prediction model to estimate the risk for coarctation of the aorta: From fetal to newborn life.
Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Improving Prenatal Diagnosis of Coarctation of the Aorta.
Morgan CT, Mueller B, Thakur V, Guerra V, Jull C, Mertens L, Friedberg M, Golding F, Seed M, Miner SES, Jaeggi ET, Manlhiot C, Nield LE
Can J Cardiol 2019 Apr;35(4):453-461. Epub 2018 Dec 17 doi: 10.1016/j.cjca.2018.12.019. PMID: 30935636
Preoperative Aortic Arch Size and Late Outcome After Coarctation Repair by Lateral Thoracotomy.
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Diagnosing Neonatal Aortic Coarctation in the Setting of Patent Ductus Arteriosus.
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138

Therapy

The aorta after coarctation repair - effects of calibre and curvature on arterial haemodynamics.
Quail MA, Segers P, Steeden JA, Muthurangu V
J Cardiovasc Magn Reson 2019 Apr 11;21(1):22. doi: 10.1186/s12968-019-0534-7. PMID: 30975162Free PMC Article
Arch Augmentation via Median Sternotomy for Coarctation of Aorta With Proximal Arch Hypoplasia.
Gray WH, Wells WJ, Starnes VA, Kumar SR
Ann Thorac Surg 2018 Oct;106(4):1214-1219. Epub 2018 May 16 doi: 10.1016/j.athoracsur.2018.04.025. PMID: 29753817
Persistent Aortic Arch Hypoplasia After Coarctation Treatment Is Associated With Late Systemic Hypertension.
Quennelle S, Powell AJ, Geva T, Prakash A
J Am Heart Assoc 2015 Jun 25;4(7) doi: 10.1161/JAHA.115.001978. PMID: 26112642Free PMC Article
Fatal aortobronchial fistula.
Li M, Langlois N, Byard RW
J Forensic Leg Med 2013 Jul;20(5):395-8. Epub 2012 Aug 22 doi: 10.1016/j.jflm.2012.07.008. PMID: 23756504
Aortic complications after pediatric cardiac transplantation in patients with a previous Norwood reconstruction.
Kanter KR, Mahle WT, Vincent RN, Berg AM
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2011;14(1):24-8. doi: 10.1053/j.pcsu.2011.01.011. PMID: 21444045

Prognosis

Echocardiographic score to predict neonatal surgery for aortic coarctation in newborns with prenatal suspicion and patent ductus arteriosus.
Bartolacelli Y, Palleri D, Balducci A, Ragni L, Hasan T, Bonetti S, Egidy Assenza G, Mariucci ME, Fabi M, Angeli E, Gargiulo GD, Donti A
J Matern Fetal Neonatal Med 2023 Dec;36(1):2201654. doi: 10.1080/14767058.2023.2201654. PMID: 37073133
A clinical prediction model to estimate the risk for coarctation of the aorta: From fetal to newborn life.
Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Preoperative Aortic Arch Size and Late Outcome After Coarctation Repair by Lateral Thoracotomy.
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
The neonatal hypoplastic aortic arch: decisions and more decisions.
Langley SM, Sunstrom RE, Reed RD, Rekito AJ, Gerrah R
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):43-51. doi: 10.1053/j.pcsu.2013.01.008. PMID: 23561817
The fetal three-vessel and tracheal view revisited.
Gardiner H, Chaoui R
Semin Fetal Neonatal Med 2013 Oct;18(5):261-8. Epub 2013 Mar 5 doi: 10.1016/j.siny.2013.01.007. PMID: 23466189

Clinical prediction guides

Echocardiographic score to predict neonatal surgery for aortic coarctation in newborns with prenatal suspicion and patent ductus arteriosus.
Bartolacelli Y, Palleri D, Balducci A, Ragni L, Hasan T, Bonetti S, Egidy Assenza G, Mariucci ME, Fabi M, Angeli E, Gargiulo GD, Donti A
J Matern Fetal Neonatal Med 2023 Dec;36(1):2201654. doi: 10.1080/14767058.2023.2201654. PMID: 37073133
A clinical prediction model to estimate the risk for coarctation of the aorta: From fetal to newborn life.
Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Prediction of neonatal coarctation of the aorta at fetal echocardiography: a scoring system.
Contro E, Cattani L, Balducci A, Prandstraller D, Perolo A, Larcher L, Reggiani MLB, Farina A, Donti A, Gargiulo GD, Pilu G
J Matern Fetal Neonatal Med 2022 Nov;35(22):4299-4305. Epub 2020 Nov 17 doi: 10.1080/14767058.2020.1849109. PMID: 33203263
Preoperative Aortic Arch Size and Late Outcome After Coarctation Repair by Lateral Thoracotomy.
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Diagnosing Neonatal Aortic Coarctation in the Setting of Patent Ductus Arteriosus.
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138

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