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Coarctation in the transverse aortic arch

MedGen UID:
1385566
Concept ID:
C4476934
Congenital Abnormality
HPO: HP:0031053

Definition

Narrowing or constriction of the aorta localized to the region of the transverse aortic arch. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCoarctation in the transverse aortic arch

Professional guidelines

PubMed

Morgan CT, Mueller B, Thakur V, Guerra V, Jull C, Mertens L, Friedberg M, Golding F, Seed M, Miner SES, Jaeggi ET, Manlhiot C, Nield LE
Can J Cardiol 2019 Apr;35(4):453-461. Epub 2018 Dec 17 doi: 10.1016/j.cjca.2018.12.019. PMID: 30935636
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138
Ford PF, Farber MA
Perspect Vasc Surg Endovasc Ther 2007 Jun;19(2):134-43. doi: 10.1177/1531003507303740. PMID: 17704482

Recent clinical studies

Etiology

Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138
Eckhauser A, South ST, Meyers L, Bleyl SB, Botto LD
J Pediatr 2015 Nov;167(5):1062-6. Epub 2015 Aug 29 doi: 10.1016/j.jpeds.2015.08.002. PMID: 26323199
Langley SM, Sunstrom RE, Reed RD, Rekito AJ, Gerrah R
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):43-51. doi: 10.1053/j.pcsu.2013.01.008. PMID: 23561817

Diagnosis

Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Morgan CT, Mueller B, Thakur V, Guerra V, Jull C, Mertens L, Friedberg M, Golding F, Seed M, Miner SES, Jaeggi ET, Manlhiot C, Nield LE
Can J Cardiol 2019 Apr;35(4):453-461. Epub 2018 Dec 17 doi: 10.1016/j.cjca.2018.12.019. PMID: 30935636
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138
Li M, Langlois N, Byard RW
J Forensic Leg Med 2013 Jul;20(5):395-8. Epub 2012 Aug 22 doi: 10.1016/j.jflm.2012.07.008. PMID: 23756504

Therapy

Quail MA, Segers P, Steeden JA, Muthurangu V
J Cardiovasc Magn Reson 2019 Apr 11;21(1):22. doi: 10.1186/s12968-019-0534-7. PMID: 30975162Free PMC Article
Gray WH, Wells WJ, Starnes VA, Kumar SR
Ann Thorac Surg 2018 Oct;106(4):1214-1219. Epub 2018 May 16 doi: 10.1016/j.athoracsur.2018.04.025. PMID: 29753817
Li M, Langlois N, Byard RW
J Forensic Leg Med 2013 Jul;20(5):395-8. Epub 2012 Aug 22 doi: 10.1016/j.jflm.2012.07.008. PMID: 23756504
Ayabakan C, Binnetoğlu K, Sarisoy Ö, Tokel K
Congenit Heart Dis 2013 Jul-Aug;8(4):316-21. Epub 2013 Mar 1 doi: 10.1111/chd.12044. PMID: 23448395
Zheng JH, Liu JF, Xu ZW, Su ZK, Ding WX
Asian Cardiovasc Thorac Ann 2007 Dec;15(6):482-5. doi: 10.1177/021849230701500607. PMID: 18042772

Prognosis

Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138
Langley SM, Sunstrom RE, Reed RD, Rekito AJ, Gerrah R
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):43-51. doi: 10.1053/j.pcsu.2013.01.008. PMID: 23561817
Hornung TS, Benson LN, McLaughlin PR
Cardiol Rev 2002 May-Jun;10(3):139-48. doi: 10.1097/00045415-200205000-00002. PMID: 12047792

Clinical prediction guides

Wang HH, Wang XM, Zhu M, Liang H, Feng J, Zhang N, Wang YM, Yu YH, Wang AB
J Obstet Gynaecol Res 2022 Sep;48(9):2304-2313. Epub 2022 Jun 26 doi: 10.1111/jog.15341. PMID: 35754096Free PMC Article
Contro E, Cattani L, Balducci A, Prandstraller D, Perolo A, Larcher L, Reggiani MLB, Farina A, Donti A, Gargiulo GD, Pilu G
J Matern Fetal Neonatal Med 2022 Nov;35(22):4299-4305. Epub 2020 Nov 17 doi: 10.1080/14767058.2020.1849109. PMID: 33203263
Ramachandran P, Khoury PR, Beekman RH, Michelfelder EC, Manning PB, Tweddell JS, Cnota JF
Ann Thorac Surg 2018 Aug;106(2):575-580. Epub 2018 May 5 doi: 10.1016/j.athoracsur.2018.03.084. PMID: 29733824
Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138
Hornung TS, Benson LN, McLaughlin PR
Cardiol Rev 2002 May-Jun;10(3):139-48. doi: 10.1097/00045415-200205000-00002. PMID: 12047792

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