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Shawl sign

MedGen UID:
1386202
•Concept ID:
C4476837
•
Finding
HPO: HP:0025535

Definition

Erythematous, poikilodermatous macules distributed in a shawl pattern over the shoulders, arms and upper back. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVShawl sign

Professional guidelines

PubMed

Redefining dermatomyositis: a description of new diagnostic criteria that differentiate pure dermatomyositis from overlap myositis with dermatomyositis features.
Troyanov Y, Targoff IN, Payette MP, Raynauld JP, Chartier S, Goulet JR, Bourré-Tessier J, Rich E, Grodzicky T, Fritzler MJ, Joyal F, Koenig M, Senécal JL
Medicine (Baltimore) 2014 Nov;93(24):318-332. doi: 10.1097/MD.0000000000000222. PMID: 25500701Free PMC Article
Innate immune-response mechanisms in dermatomyositis: an update on pathogenesis, diagnosis and treatment.
Hornung T, Wenzel J
Drugs 2014 Jun;74(9):981-98. doi: 10.1007/s40265-014-0240-6. PMID: 24939511

Recent clinical studies

Etiology

Clinical characteristics and prognostic analysis of idiopathic inflammatory myopathy with positive anti-aminoacyl-tRNA synthetase antibodies: A single center experience.
Zhang D, Wang H, Zhou X, Yang J, Liu Y, Wang W, Jiang P, Fan B
Immun Inflamm Dis 2023 Nov;11(11):e1085. doi: 10.1002/iid3.1085. PMID: 38018600Free PMC Article
Association of anti-TPM4 autoantibodies with vasculopathic cutaneous manifestations in juvenile dermatomyositis.
Karasawa R, Yudoh K, Sato T, Tanaka M, Sabbagh SE, Flegel WA, Mammen AL, Jarvis JN, Rider LG; Childhood Myositis Heterogeneity Study Group
Rheumatology (Oxford) 2023 Nov 2;62(11):3757-3762. doi: 10.1093/rheumatology/kead203. PMID: 37144941Free PMC Article
Machine Learning Algorithms Identify Clinical Subtypes and Cancer in Anti-TIF1γ+ Myositis: A Longitudinal Study of 87 Patients.
Zhao L, Xie S, Zhou B, Shen C, Li L, Pi W, Gong Z, Zhao J, Peng Q, Zhou J, Peng J, Zhou Y, Zou L, Song L, Zhu H, Luo H
Front Immunol 2022;13:802499. Epub 2022 Feb 14 doi: 10.3389/fimmu.2022.802499. PMID: 35237262Free PMC Article
Risk factors for cancer-associated myositis: A large-scale multicenter cohort study.
Li Y, Jia X, Sun X, Shi L, Lin F, Gan Y, Zhang X, Gao X, Miao M, Hong D, Li Y, He J
Int J Rheum Dis 2021 Feb;24(2):268-273. Epub 2020 Dec 26 doi: 10.1111/1756-185X.14046. PMID: 33369084
The myositis autoantibody phenotypes of the juvenile idiopathic inflammatory myopathies.
Rider LG, Shah M, Mamyrova G, Huber AM, Rice MM, Targoff IN, Miller FW; Childhood Myositis Heterogeneity Collaborative Study Group
Medicine (Baltimore) 2013 Jul;92(4):223-243. doi: 10.1097/MD.0b013e31829d08f9. PMID: 23877355Free PMC Article

Diagnosis

Skin Manifestation Associated With Multicentric Reticulohistiocytosis.
Yamamoto T
J Clin Rheumatol 2022 Jan 1;28(1):e234-e239. doi: 10.1097/RHU.0000000000001679. PMID: 33337805
Risk factors for cancer-associated myositis: A large-scale multicenter cohort study.
Li Y, Jia X, Sun X, Shi L, Lin F, Gan Y, Zhang X, Gao X, Miao M, Hong D, Li Y, He J
Int J Rheum Dis 2021 Feb;24(2):268-273. Epub 2020 Dec 26 doi: 10.1111/1756-185X.14046. PMID: 33369084
Cutaneous Manifestations in Dermatomyositis: Key Clinical and Serological Features-a Comprehensive Review.
Muro Y, Sugiura K, Akiyama M
Clin Rev Allergy Immunol 2016 Dec;51(3):293-302. doi: 10.1007/s12016-015-8496-5. PMID: 26100618
Innate immune-response mechanisms in dermatomyositis: an update on pathogenesis, diagnosis and treatment.
Hornung T, Wenzel J
Drugs 2014 Jun;74(9):981-98. doi: 10.1007/s40265-014-0240-6. PMID: 24939511
The myositis autoantibody phenotypes of the juvenile idiopathic inflammatory myopathies.
Rider LG, Shah M, Mamyrova G, Huber AM, Rice MM, Targoff IN, Miller FW; Childhood Myositis Heterogeneity Collaborative Study Group
Medicine (Baltimore) 2013 Jul;92(4):223-243. doi: 10.1097/MD.0b013e31829d08f9. PMID: 23877355Free PMC Article

Therapy

Machine Learning Algorithms Identify Clinical Subtypes and Cancer in Anti-TIF1γ+ Myositis: A Longitudinal Study of 87 Patients.
Zhao L, Xie S, Zhou B, Shen C, Li L, Pi W, Gong Z, Zhao J, Peng Q, Zhou J, Peng J, Zhou Y, Zou L, Song L, Zhu H, Luo H
Front Immunol 2022;13:802499. Epub 2022 Feb 14 doi: 10.3389/fimmu.2022.802499. PMID: 35237262Free PMC Article
Erythroderma and extensive poikiloderma - a rare initial presentation of dermatomyositis: a case report.
Herath HMMTB, Keragala BSDP, Pahalagamage SP, Janappriya GHCC, Kulatunga A, Gunasekera CN
J Med Case Rep 2018 Mar 24;12(1):83. doi: 10.1186/s13256-018-1618-y. PMID: 29571300Free PMC Article
Advanced Lung Adenocarcinoma with Nivolumab-associated Dermatomyositis.
Kudo F, Watanabe Y, Iwai Y, Miwa C, Nagai Y, Ota H, Yabe H, Demitsu T, Hagiwara K, Koyama N, Koyama S
Intern Med 2018 Aug 1;57(15):2217-2221. Epub 2018 Mar 9 doi: 10.2169/internalmedicine.9381-17. PMID: 29526968Free PMC Article
Innate immune-response mechanisms in dermatomyositis: an update on pathogenesis, diagnosis and treatment.
Hornung T, Wenzel J
Drugs 2014 Jun;74(9):981-98. doi: 10.1007/s40265-014-0240-6. PMID: 24939511
The myositis autoantibody phenotypes of the juvenile idiopathic inflammatory myopathies.
Rider LG, Shah M, Mamyrova G, Huber AM, Rice MM, Targoff IN, Miller FW; Childhood Myositis Heterogeneity Collaborative Study Group
Medicine (Baltimore) 2013 Jul;92(4):223-243. doi: 10.1097/MD.0b013e31829d08f9. PMID: 23877355Free PMC Article

Prognosis

Clinical characteristics and prognostic analysis of idiopathic inflammatory myopathy with positive anti-aminoacyl-tRNA synthetase antibodies: A single center experience.
Zhang D, Wang H, Zhou X, Yang J, Liu Y, Wang W, Jiang P, Fan B
Immun Inflamm Dis 2023 Nov;11(11):e1085. doi: 10.1002/iid3.1085. PMID: 38018600Free PMC Article
Clinical Heterogeneity of Patients With Antinuclear Matrix Protein 2 Antibody-Positive Myositis: A Retrospective Cohort Study in China.
Li S, Sun C, Zhang L, Han J, Yang H, Gao S, He L, Zhang P, Lu X, Shu X, Wang G
J Rheumatol 2022 Aug;49(8):922-928. Epub 2022 Jun 15 doi: 10.3899/jrheum.211234. PMID: 35705242
Machine Learning Algorithms Identify Clinical Subtypes and Cancer in Anti-TIF1γ+ Myositis: A Longitudinal Study of 87 Patients.
Zhao L, Xie S, Zhou B, Shen C, Li L, Pi W, Gong Z, Zhao J, Peng Q, Zhou J, Peng J, Zhou Y, Zou L, Song L, Zhu H, Luo H
Front Immunol 2022;13:802499. Epub 2022 Feb 14 doi: 10.3389/fimmu.2022.802499. PMID: 35237262Free PMC Article
Risk factors for cancer-associated myositis: A large-scale multicenter cohort study.
Li Y, Jia X, Sun X, Shi L, Lin F, Gan Y, Zhang X, Gao X, Miao M, Hong D, Li Y, He J
Int J Rheum Dis 2021 Feb;24(2):268-273. Epub 2020 Dec 26 doi: 10.1111/1756-185X.14046. PMID: 33369084
The myositis autoantibody phenotypes of the juvenile idiopathic inflammatory myopathies.
Rider LG, Shah M, Mamyrova G, Huber AM, Rice MM, Targoff IN, Miller FW; Childhood Myositis Heterogeneity Collaborative Study Group
Medicine (Baltimore) 2013 Jul;92(4):223-243. doi: 10.1097/MD.0b013e31829d08f9. PMID: 23877355Free PMC Article

Clinical prediction guides

Clinical characteristics and prognostic analysis of idiopathic inflammatory myopathy with positive anti-aminoacyl-tRNA synthetase antibodies: A single center experience.
Zhang D, Wang H, Zhou X, Yang J, Liu Y, Wang W, Jiang P, Fan B
Immun Inflamm Dis 2023 Nov;11(11):e1085. doi: 10.1002/iid3.1085. PMID: 38018600Free PMC Article
Characteristics of anti-transcriptional intermediary factor 1 gamma autoantibody-positive dermatomyositis patients in Singapore.
Chua CG, Low JZ, Lim WY, Manghani M
Ann Acad Med Singap 2022 Dec;51(12):755-765. doi: 10.47102/annals-acadmedsg.2022278. PMID: 36592144
Machine Learning Algorithms Identify Clinical Subtypes and Cancer in Anti-TIF1γ+ Myositis: A Longitudinal Study of 87 Patients.
Zhao L, Xie S, Zhou B, Shen C, Li L, Pi W, Gong Z, Zhao J, Peng Q, Zhou J, Peng J, Zhou Y, Zou L, Song L, Zhu H, Luo H
Front Immunol 2022;13:802499. Epub 2022 Feb 14 doi: 10.3389/fimmu.2022.802499. PMID: 35237262Free PMC Article
Risk factors for cancer-associated myositis: A large-scale multicenter cohort study.
Li Y, Jia X, Sun X, Shi L, Lin F, Gan Y, Zhang X, Gao X, Miao M, Hong D, Li Y, He J
Int J Rheum Dis 2021 Feb;24(2):268-273. Epub 2020 Dec 26 doi: 10.1111/1756-185X.14046. PMID: 33369084
The red face revisited: connective tissue disorders.
Kazandjieva J, Tsankov N, Pramatarov K
Clin Dermatol 2014 Jan-Feb;32(1):153-8. doi: 10.1016/j.clindermatol.2013.05.037. PMID: 24314389

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