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Neurenteric cyst

MedGen UID:
14343
Concept ID:
C0027806
Congenital Abnormality
Synonyms: Cyst, Neurenteric; Cyst, Neuroenteric; Cysts, Neurenteric; Cysts, Neuroenteric; Neurenteric Cyst; Neurenteric Cysts; Neuroenteric Cyst; Neuroenteric Cysts
SNOMED CT: Neurenteric cyst (789120001); Neurenteric cyst (41353005)
 
HPO: HP:0030725
Monarch Initiative: MONDO:0017087
Orphanet: ORPHA268865

Definition

The neurenteric cyst is a rare lesion composed of heterotopic endodermal tissue. During the third week of human embryogenesis, the neurenteric canal unites the yolk sac and the amniotic cavity as it traverses the primitive notochordal plate. Persistence of the normally transient neurenteric canal prevents appropriate separation of endoderm and notochord. This results in a variable degree of communication between neural and enteric epithelium. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeurenteric cyst
Follow this link to review classifications for Neurenteric cyst in Orphanet.

Professional guidelines

PubMed

Meller C, Covini D, Aiello H, Izbizky G, Portillo Medina S, Otaño L
Arch Argent Pediatr 2021 Jun;119(3):e215-e228. doi: 10.5546/aap.2021.eng.e215. PMID: 34033426
Phillips LA, Burton JM, Evans SH
Curr Probl Pediatr Adolesc Health Care 2017 Jul;47(7):173-177. Epub 2017 Jul 19 doi: 10.1016/j.cppeds.2017.06.007. PMID: 28734746
Levin BL, Varga E
J Genet Couns 2016 Oct;25(5):901-11. Epub 2016 Apr 30 doi: 10.1007/s10897-016-9956-7. PMID: 27130656

Recent clinical studies

Etiology

Kozak J, Bizik I, Surkala J, Steno J, Steno A
Bratisl Lek Listy 2019;120(9):680-685. doi: 10.4149/BLL_2019_114. PMID: 31475554
Çay A, Aydoğdu İ, Mirapoglu SL, Toprak H
J Med Ultrason (2001) 2018 Oct;45(4):633-639. Epub 2018 Feb 21 doi: 10.1007/s10396-018-0869-y. PMID: 29468491
Chen CT, Lai HY, Jung SM, Lee CY, Wu CT, Lee ST
World Neurosurg 2016 Dec;96:85-90. Epub 2016 Aug 29 doi: 10.1016/j.wneu.2016.08.089. PMID: 27586176
Visvanathan V, Crowther J, Taylor W
Scott Med J 2015 Feb;60(1):e4-7. Epub 2014 Dec 3 doi: 10.1177/0036933014563239. PMID: 25471489
Colović R, Micev M, Jovanović M, Matić S, Grubor N, Atkinson HD
World J Gastroenterol 2008 Jun 21;14(23):3759-62. doi: 10.3748/wjg.14.3759. PMID: 18595146Free PMC Article

Diagnosis

Poyuran R, Kalaparti VSVG, Thomas B, Kesavapisharady K, Narasimhaiah D
Neuropathology 2023 Jun;43(3):221-232. Epub 2022 Oct 10 doi: 10.1111/neup.12867. PMID: 36210745
Diyora B, Bhende B, Kukreja S
World Neurosurg 2018 Oct;118:126-131. Epub 2018 Aug 4 doi: 10.1016/j.wneu.2018.07.027. PMID: 30010074
Çay A, Aydoğdu İ, Mirapoglu SL, Toprak H
J Med Ultrason (2001) 2018 Oct;45(4):633-639. Epub 2018 Feb 21 doi: 10.1007/s10396-018-0869-y. PMID: 29468491
Chen CT, Lai HY, Jung SM, Lee CY, Wu CT, Lee ST
World Neurosurg 2016 Dec;96:85-90. Epub 2016 Aug 29 doi: 10.1016/j.wneu.2016.08.089. PMID: 27586176
Visvanathan V, Crowther J, Taylor W
Scott Med J 2015 Feb;60(1):e4-7. Epub 2014 Dec 3 doi: 10.1177/0036933014563239. PMID: 25471489

Therapy

Palmieri D, Champagne PO, Valappil B, McDowell MM, Gardner PA, Snyderman CH
Am J Rhinol Allergy 2023 Jan;37(1):13-18. Epub 2022 Sep 1 doi: 10.1177/19458924221123113. PMID: 36050937
Stopa BM, Cuoco JA, Stump MS, Rogers CM
World Neurosurg 2022 Aug;164:8-24. Epub 2022 Apr 20 doi: 10.1016/j.wneu.2022.04.057. PMID: 35460907
Esfahani DR, Burokas L, Brown HG, Hahn YS, Nikas D
Childs Nerv Syst 2017 Sep;33(9):1603-1607. Epub 2017 Jun 22 doi: 10.1007/s00381-017-3487-x. PMID: 28643040
Wait SD, Choi LS, Teo C
Childs Nerv Syst 2011 Apr;27(4):639-41. Epub 2010 Nov 25 doi: 10.1007/s00381-010-1332-6. PMID: 21107583
Menezes AH
Childs Nerv Syst 2008 Oct;24(10):1203-7. Epub 2008 Mar 26 doi: 10.1007/s00381-008-0597-5. PMID: 18365213

Prognosis

Kozak J, Bizik I, Surkala J, Steno J, Steno A
Bratisl Lek Listy 2019;120(9):680-685. doi: 10.4149/BLL_2019_114. PMID: 31475554
Çay A, Aydoğdu İ, Mirapoglu SL, Toprak H
J Med Ultrason (2001) 2018 Oct;45(4):633-639. Epub 2018 Feb 21 doi: 10.1007/s10396-018-0869-y. PMID: 29468491
Chakraborty S, Priamo F, Loven T, Li J, Insinga S, Schulder M
World Neurosurg 2016 Jan;85:143-52. Epub 2015 Sep 1 doi: 10.1016/j.wneu.2015.08.057. PMID: 26341448
Visvanathan V, Crowther J, Taylor W
Scott Med J 2015 Feb;60(1):e4-7. Epub 2014 Dec 3 doi: 10.1177/0036933014563239. PMID: 25471489
Kumar R, Prakash M
Childs Nerv Syst 2007 Feb;23(2):243-7. Epub 2006 Sep 21 doi: 10.1007/s00381-006-0211-7. PMID: 17021726

Clinical prediction guides

Diyora B, Bhende B, Kukreja S
World Neurosurg 2018 Oct;118:126-131. Epub 2018 Aug 4 doi: 10.1016/j.wneu.2018.07.027. PMID: 30010074
Yang T, Wu L, Fang J, Yang C, Deng X, Xu Y
J Neurosurg Spine 2015 Jul;23(1):99-110. Epub 2015 Apr 24 doi: 10.3171/2014.11.SPINE14352. PMID: 25909275
Uschold T, Xu DS, Wilson DA, Abla AA, Nakaji P, Spetzler RF, Chang SW
World Neurosurg 2014 Sep-Oct;82(3-4):480-4. Epub 2013 Oct 16 doi: 10.1016/j.wneu.2013.10.037. PMID: 24141002
Rossi A, Piatelli G, Gandolfo C, Pavanello M, Hoffmann C, Van Goethem JW, Cama A, Tortori-Donati P
Neurosurgery 2006 Mar;58(3):509-15; discussion 509-15. doi: 10.1227/01.NEU.0000197122.92954.82. PMID: 16528191
Chung HD, DeMello DE, D'Souza N, Estrada J
Neurology 1982 Apr;32(4):441-4. doi: 10.1212/wnl.32.4.441. PMID: 7038532

Recent systematic reviews

Stopa BM, Cuoco JA, Stump MS, Rogers CM
World Neurosurg 2022 Aug;164:8-24. Epub 2022 Apr 20 doi: 10.1016/j.wneu.2022.04.057. PMID: 35460907

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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