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Central serous chorioretinopathy

MedGen UID:
147591
Concept ID:
C0730328
Disease or Syndrome
Synonym: Central serous chorioretinopathy after bone marrow transplantation
SNOMED CT: CSR - central serous retinopathy (312956001); Central serous choroidopathy (312956001); Central serous retinopathy (312956001); CSC - Central serous choroidopathy (312956001); Central serous chorioretinopathy (312956001)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
HPO: HP:0025567
Monarch Initiative: MONDO:0018616
Orphanet: ORPHA443079

Definition

An anomaly of the retina with serous detachment of the neurosensory retina secondary to one or more focal lesions of the retinal pigment epithelium (RPE), and associated with blurred vision, usually in one eye only and perceived typically by the patient as a dark spot in the center of the visual field with associated micropsia and metamorphopsia. Normal vision often recurs spontaneously within a few months. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral serous chorioretinopathy

Professional guidelines

PubMed

Goté JT, Singh SR, Chhablani J
Graefes Arch Clin Exp Ophthalmol 2023 Aug;261(8):2135-2168. Epub 2023 Mar 2 doi: 10.1007/s00417-023-05996-4. PMID: 36862202
van Rijssen TJ, van Dijk EHC, Yzer S, Ohno-Matsui K, Keunen JEE, Schlingemann RO, Sivaprasad S, Querques G, Downes SM, Fauser S, Hoyng CB, Piccolino FC, Chhablani JK, Lai TYY, Lotery AJ, Larsen M, Holz FG, Freund KB, Yannuzzi LA, Boon CJF
Prog Retin Eye Res 2019 Nov;73:100770. Epub 2019 Jul 15 doi: 10.1016/j.preteyeres.2019.07.003. PMID: 31319157
Hanumunthadu D, Tan ACS, Singh SR, Sahu NK, Chhablani J
Indian J Ophthalmol 2018 Dec;66(12):1704-1714. doi: 10.4103/ijo.IJO_1077_18. PMID: 30451170Free PMC Article

Recent clinical studies

Etiology

Mazzeo TJMM, Leber HM, da Silva AG, Freire RCM, Barbosa GCS, Criado GG, Jacob GAV, Machado CG, Gomes AMV
Graefes Arch Clin Exp Ophthalmol 2022 Mar;260(3):723-735. Epub 2021 Oct 14 doi: 10.1007/s00417-021-05450-3. PMID: 34648069
Kaye R, Chandra S, Sheth J, Boon CJF, Sivaprasad S, Lotery A
Prog Retin Eye Res 2020 Nov;79:100865. Epub 2020 May 11 doi: 10.1016/j.preteyeres.2020.100865. PMID: 32407978
Ge G, Zhang Y, Zhang Y, Xu Z, Zhang M
Graefes Arch Clin Exp Ophthalmol 2020 Jan;258(1):71-77. Epub 2019 Nov 16 doi: 10.1007/s00417-019-04486-w. PMID: 31734720
Daruich A, Matet A, Dirani A, Bousquet E, Zhao M, Farman N, Jaisser F, Behar-Cohen F
Prog Retin Eye Res 2015 Sep;48:82-118. Epub 2015 May 27 doi: 10.1016/j.preteyeres.2015.05.003. PMID: 26026923
Liegl R, Ulbig MW
Ophthalmologica 2014;232(2):65-76. Epub 2014 Apr 26 doi: 10.1159/000360014. PMID: 24776999

Diagnosis

Fung AT, Yang Y, Kam AW
Clin Exp Ophthalmol 2023 Apr;51(3):243-270. Epub 2023 Jan 30 doi: 10.1111/ceo.14201. PMID: 36597282
van Dijk EHC, Boon CJF
Prog Retin Eye Res 2021 Sep;84:100955. Epub 2021 Mar 11 doi: 10.1016/j.preteyeres.2021.100955. PMID: 33716160
Kaye R, Chandra S, Sheth J, Boon CJF, Sivaprasad S, Lotery A
Prog Retin Eye Res 2020 Nov;79:100865. Epub 2020 May 11 doi: 10.1016/j.preteyeres.2020.100865. PMID: 32407978
Daruich A, Matet A, Behar-Cohen F
Dev Ophthalmol 2017;58:27-38. Epub 2017 Mar 28 doi: 10.1159/000455267. PMID: 28351043
Daruich A, Matet A, Dirani A, Bousquet E, Zhao M, Farman N, Jaisser F, Behar-Cohen F
Prog Retin Eye Res 2015 Sep;48:82-118. Epub 2015 May 27 doi: 10.1016/j.preteyeres.2015.05.003. PMID: 26026923

Therapy

You EL, Hébert M, Jin TS, Bourgault S, Caissie M, Tourville É, Chen J, Ordóñez-Mena J, Dirani A
Surv Ophthalmol 2023 Jul-Aug;68(4):601-614. Epub 2023 Mar 16 doi: 10.1016/j.survophthal.2023.03.001. PMID: 36931437
Ge G, Zhang Y, Zhang Y, Xu Z, Zhang M
Graefes Arch Clin Exp Ophthalmol 2020 Jan;258(1):71-77. Epub 2019 Nov 16 doi: 10.1007/s00417-019-04486-w. PMID: 31734720
van Rijssen TJ, van Dijk EHC, Yzer S, Ohno-Matsui K, Keunen JEE, Schlingemann RO, Sivaprasad S, Querques G, Downes SM, Fauser S, Hoyng CB, Piccolino FC, Chhablani JK, Lai TYY, Lotery AJ, Larsen M, Holz FG, Freund KB, Yannuzzi LA, Boon CJF
Prog Retin Eye Res 2019 Nov;73:100770. Epub 2019 Jul 15 doi: 10.1016/j.preteyeres.2019.07.003. PMID: 31319157
Nicholson BP, Atchison E, Idris AA, Bakri SJ
Surv Ophthalmol 2018 Jan-Feb;63(1):1-8. Epub 2017 Jun 30 doi: 10.1016/j.survophthal.2017.06.008. PMID: 28673727
Daruich A, Matet A, Dirani A, Bousquet E, Zhao M, Farman N, Jaisser F, Behar-Cohen F
Prog Retin Eye Res 2015 Sep;48:82-118. Epub 2015 May 27 doi: 10.1016/j.preteyeres.2015.05.003. PMID: 26026923

Prognosis

Myslík M, Kateřina
Cesk Slov Oftalmol 2024;80(2):59-75. doi: 10.31348/2023/27. PMID: 38531681
van Dijk EHC, Boon CJF
Prog Retin Eye Res 2021 Sep;84:100955. Epub 2021 Mar 11 doi: 10.1016/j.preteyeres.2021.100955. PMID: 33716160
Gülkaş S, Şahin Ö
Turk J Ophthalmol 2019 Feb 28;49(1):30-39. doi: 10.4274/tjo.galenos.2018.49035. PMID: 30829023Free PMC Article
Sahoo NK, Singh SR, Rajendran A, Shukla D, Chhablani J
Surv Ophthalmol 2019 Jan-Feb;64(1):30-44. Epub 2018 Sep 20 doi: 10.1016/j.survophthal.2018.09.001. PMID: 30243734
Liegl R, Ulbig MW
Ophthalmologica 2014;232(2):65-76. Epub 2014 Apr 26 doi: 10.1159/000360014. PMID: 24776999

Clinical prediction guides

Rämö JT, Abner E, van Dijk EHC, Wang X, Brinks J, Nikopensius T, Nõukas M, Marjonen H, Silander K, Jukarainen S, Kiiskinen T, Choi SH, Kajanne R, Mehtonen J, Palta P, Lubitz SA, Kaarniranta K, Sobrin L, Kurki M, Yzer S, Ellinor PT, Esko T, Daly MJ, den Hollander AI, Palotie A, Turunen JA, Boon CJF, Rossin EJ; FinnGen Study; Estonian Biobank Research Team
JAMA Ophthalmol 2023 May 1;141(5):449-457. doi: 10.1001/jamaophthalmol.2023.0706. PMID: 37079300Free PMC Article
Arora S, Surakiatchanukul T, Arora T, Cagini C, Lupidi M, Chhablani J
Surv Ophthalmol 2022 Mar-Apr;67(2):463-487. Epub 2021 Jun 25 doi: 10.1016/j.survophthal.2021.06.004. PMID: 34175342
van Rijssen TJ, van Dijk EHC, Yzer S, Ohno-Matsui K, Keunen JEE, Schlingemann RO, Sivaprasad S, Querques G, Downes SM, Fauser S, Hoyng CB, Piccolino FC, Chhablani JK, Lai TYY, Lotery AJ, Larsen M, Holz FG, Freund KB, Yannuzzi LA, Boon CJF
Prog Retin Eye Res 2019 Nov;73:100770. Epub 2019 Jul 15 doi: 10.1016/j.preteyeres.2019.07.003. PMID: 31319157
Wong KH, Lau KP, Chhablani J, Tao Y, Li Q, Wong IY
Acta Ophthalmol 2016 Jun;94(4):321-5. Epub 2015 Jul 1 doi: 10.1111/aos.12779. PMID: 26132864
Daruich A, Matet A, Dirani A, Bousquet E, Zhao M, Farman N, Jaisser F, Behar-Cohen F
Prog Retin Eye Res 2015 Sep;48:82-118. Epub 2015 May 27 doi: 10.1016/j.preteyeres.2015.05.003. PMID: 26026923

Recent systematic reviews

van Dijk EHC, Feenstra HMA, Bjerager J, Grauslund J, Boon CJF, Subhi Y
Acta Ophthalmol 2023 Mar;101(2):140-159. Epub 2022 Sep 30 doi: 10.1111/aos.15263. PMID: 36178171
Chen ZJ, Lu SY, Rong SS, Ho M, Ng DS, Chen H, Gong B, Yam JC, Young AL, Brelen M, Tham CC, Pang CP, Chen LJ
Br J Ophthalmol 2022 Nov;106(11):1542-1548. Epub 2021 May 26 doi: 10.1136/bjophthalmol-2021-318953. PMID: 34039561
Genovese G, Meduri A, Muscatello MRA, Gangemi S, Cedro C, Bruno A, Aragona P, Pandolfo G
Medicina (Kaunas) 2021 Jun 16;57(6) doi: 10.3390/medicina57060628. PMID: 34208694Free PMC Article
Akkaya S
Int Ophthalmol 2018 Oct;38(5):2239-2246. Epub 2017 Aug 1 doi: 10.1007/s10792-017-0666-4. PMID: 28766279
Liu B, Deng T, Zhang J
Retina 2016 Jan;36(1):9-19. doi: 10.1097/IAE.0000000000000837. PMID: 26710181

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