U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Adrenal Cortical Sarcomatoid Carcinoma

MedGen UID:
1612498
Concept ID:
C0279579
Neoplastic Process
Synonyms: Adrenal Cortex Anaplastic Carcinoma; Adrenal Cortex Sarcomatoid Carcinoma

Definition

A carcinoma that arises from the adrenal cortex and is characterized by the partial or complete loss of adrenal cortical differentiation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdrenal Cortical Sarcomatoid Carcinoma

Professional guidelines

PubMed

Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Fassnacht M, Dekkers OM, Else T, Baudin E, Berruti A, de Krijger R, Haak HR, Mihai R, Assie G, Terzolo M
Eur J Endocrinol 2018 Oct 1;179(4):G1-G46. doi: 10.1530/EJE-18-0608. PMID: 30299884
Spain L, Diem S, Larkin J
Cancer Treat Rev 2016 Mar;44:51-60. Epub 2016 Feb 6 doi: 10.1016/j.ctrv.2016.02.001. PMID: 26874776

Recent clinical studies

Etiology

Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Gaujoux S, Weinandt M, Bonnet S, Reslinger V, Bertherat J, Dousset B
J Visc Surg 2017 Oct;154(5):335-343. Epub 2017 Jul 25 doi: 10.1016/j.jviscsurg.2017.06.010. PMID: 28754418
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Diagnosis

Chung R, Garratt J, Remer EM, Navin P, Blake MA, Taffel MT, Hackett CE, Sharbidre KG, Tu W, Low G, Bara M, Carney BW, Corwin MT, Campbell MJ, Lee JT, Lee CY, Dueber JC, Shehata MA, Caoili EM, Schieda N, Elsayes KM
Radiographics 2023 Jul;43(7):e220191. doi: 10.1148/rg.220191. PMID: 37347698
Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Sherlock M, Scarsbrook A, Abbas A, Fraser S, Limumpornpetch P, Dineen R, Stewart PM
Endocr Rev 2020 Dec 1;41(6):775-820. doi: 10.1210/endrev/bnaa008. PMID: 32266384Free PMC Article
Dackiw AP, Lee JE, Gagel RF, Evans DB
World J Surg 2001 Jul;25(7):914-26. doi: 10.1007/s00268-001-0030-7. PMID: 11572033

Therapy

Ilanchezhian M, Varghese DG, Glod JW, Reilly KM, Widemann BC, Pommier Y, Kaplan RN, Del Rivero J
Front Endocrinol (Lausanne) 2022;13:961650. Epub 2022 Oct 31 doi: 10.3389/fendo.2022.961650. PMID: 36387865Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Long SE, Miller BS
Surg Clin North Am 2019 Aug;99(4):759-771. Epub 2019 May 27 doi: 10.1016/j.suc.2019.04.012. PMID: 31255205
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Prognosis

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Mete O, Asa SL, Giordano TJ, Papotti M, Sasano H, Volante M
Endocr Pathol 2018 Jun;29(2):137-149. doi: 10.1007/s12022-018-9525-8. PMID: 29542002
Else T, Kim AC, Sabolch A, Raymond VM, Kandathil A, Caoili EM, Jolly S, Miller BS, Giordano TJ, Hammer GD
Endocr Rev 2014 Apr;35(2):282-326. Epub 2013 Dec 20 doi: 10.1210/er.2013-1029. PMID: 24423978Free PMC Article
Dackiw AP, Lee JE, Gagel RF, Evans DB
World J Surg 2001 Jul;25(7):914-26. doi: 10.1007/s00268-001-0030-7. PMID: 11572033

Clinical prediction guides

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Igaz P
Curr Opin Endocrinol Diabetes Obes 2019 Jun;26(3):155-159. doi: 10.1097/MED.0000000000000472. PMID: 30801265
Mete O, Asa SL, Giordano TJ, Papotti M, Sasano H, Volante M
Endocr Pathol 2018 Jun;29(2):137-149. doi: 10.1007/s12022-018-9525-8. PMID: 29542002
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Recent systematic reviews

Padua TC, Marandino L, Raggi D, Hallanger-Johnson J, Kutikov A, Spiess PE, Necchi A
Clin Genitourin Cancer 2023 Feb;21(1):1-7. Epub 2022 Oct 23 doi: 10.1016/j.clgc.2022.10.011. PMID: 36376169
Nakanishi H, Miangul S, Wang R, El Haddad J, El Ghazal N, Abdulsalam FA, Matar RH, Than CA, Johnson BE, Chen H
Ann Surg Oncol 2023 Feb;30(2):994-1005. Epub 2022 Nov 7 doi: 10.1245/s10434-022-12711-w. PMID: 36344710
Yeoh P, Czuber-Dochan W, Aylwin S, Sturt J
Endocrinol Diabetes Metab 2022 Jul;5(4):e341. Epub 2022 Jun 6 doi: 10.1002/edm2.341. PMID: 35670031Free PMC Article
Xu X, Sergi C
Contemp Clin Trials 2016 Sep;50:37-44. Epub 2016 Jul 14 doi: 10.1016/j.cct.2016.07.011. PMID: 27424218
Mearini L, Del Sordo R, Costantini E, Nunzi E, Porena M
Urol Int 2013;91(2):125-33. Epub 2012 Nov 8 doi: 10.1159/000345141. PMID: 23147196

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...