U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Adrenal Cortical Sarcomatoid Carcinoma

MedGen UID:
1612498
Concept ID:
C0279579
Neoplastic Process
Synonyms: Adrenal Cortex Anaplastic Carcinoma; Adrenal Cortex Sarcomatoid Carcinoma

Definition

A carcinoma that arises from the adrenal cortex and is characterized by the partial or complete loss of adrenal cortical differentiation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdrenal Cortical Sarcomatoid Carcinoma

Professional guidelines

PubMed

Fassnacht M, Dekkers OM, Else T, Baudin E, Berruti A, de Krijger R, Haak HR, Mihai R, Assie G, Terzolo M
Eur J Endocrinol 2018 Oct 1;179(4):G1-G46. doi: 10.1530/EJE-18-0608. PMID: 30299884
Singh S, Osna NA, Kharbanda KK
World J Gastroenterol 2017 Sep 28;23(36):6549-6570. doi: 10.3748/wjg.v23.i36.6549. PMID: 29085205Free PMC Article
Spain L, Diem S, Larkin J
Cancer Treat Rev 2016 Mar;44:51-60. Epub 2016 Feb 6 doi: 10.1016/j.ctrv.2016.02.001. PMID: 26874776

Recent clinical studies

Etiology

Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Fassnacht M, Assie G, Baudin E, Eisenhofer G, de la Fouchardiere C, Haak HR, de Krijger R, Porpiglia F, Terzolo M, Berruti A; ESMO Guidelines Committee. Electronic address: clinicalguidelines@esmo.org
Ann Oncol 2020 Nov;31(11):1476-1490. Epub 2020 Aug 27 doi: 10.1016/j.annonc.2020.08.2099. PMID: 32861807
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Diagnosis

Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Kastenberg ZJ, Scaife ER
Semin Pediatr Surg 2020 Jun;29(3):150927. Epub 2020 May 17 doi: 10.1016/j.sempedsurg.2020.150927. PMID: 32571512
Sherlock M, Scarsbrook A, Abbas A, Fraser S, Limumpornpetch P, Dineen R, Stewart PM
Endocr Rev 2020 Dec 1;41(6):775-820. doi: 10.1210/endrev/bnaa008. PMID: 32266384Free PMC Article
Longui CA
Rev Paul Pediatr 2019 Jan-Mar;37(1):2-3. doi: 10.1590/1984-0462/;2019;37;1;00021. PMID: 30726455Free PMC Article
Mete O, Asa SL, Giordano TJ, Papotti M, Sasano H, Volante M
Endocr Pathol 2018 Jun;29(2):137-149. doi: 10.1007/s12022-018-9525-8. PMID: 29542002

Therapy

Ilanchezhian M, Varghese DG, Glod JW, Reilly KM, Widemann BC, Pommier Y, Kaplan RN, Del Rivero J
Front Endocrinol (Lausanne) 2022;13:961650. Epub 2022 Oct 31 doi: 10.3389/fendo.2022.961650. PMID: 36387865Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Long SE, Miller BS
Surg Clin North Am 2019 Aug;99(4):759-771. Epub 2019 May 27 doi: 10.1016/j.suc.2019.04.012. PMID: 31255205
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Prognosis

Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Longui CA
Rev Paul Pediatr 2019 Jan-Mar;37(1):2-3. doi: 10.1590/1984-0462/;2019;37;1;00021. PMID: 30726455Free PMC Article
Mete O, Asa SL, Giordano TJ, Papotti M, Sasano H, Volante M
Endocr Pathol 2018 Jun;29(2):137-149. doi: 10.1007/s12022-018-9525-8. PMID: 29542002
Else T, Kim AC, Sabolch A, Raymond VM, Kandathil A, Caoili EM, Jolly S, Miller BS, Giordano TJ, Hammer GD
Endocr Rev 2014 Apr;35(2):282-326. Epub 2013 Dec 20 doi: 10.1210/er.2013-1029. PMID: 24423978Free PMC Article
Dackiw AP, Lee JE, Gagel RF, Evans DB
World J Surg 2001 Jul;25(7):914-26. doi: 10.1007/s00268-001-0030-7. PMID: 11572033

Clinical prediction guides

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Igaz P
Curr Opin Endocrinol Diabetes Obes 2019 Jun;26(3):155-159. doi: 10.1097/MED.0000000000000472. PMID: 30801265
Mete O, Asa SL, Giordano TJ, Papotti M, Sasano H, Volante M
Endocr Pathol 2018 Jun;29(2):137-149. doi: 10.1007/s12022-018-9525-8. PMID: 29542002
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Recent systematic reviews

Yeoh P, Czuber-Dochan W, Aylwin S, Sturt J
Endocrinol Diabetes Metab 2022 Jul;5(4):e341. Epub 2022 Jun 6 doi: 10.1002/edm2.341. PMID: 35670031Free PMC Article
Xu X, Sergi C
Contemp Clin Trials 2016 Sep;50:37-44. Epub 2016 Jul 14 doi: 10.1016/j.cct.2016.07.011. PMID: 27424218
Wong KK, Miller BS, Viglianti BL, Dwamena BA, Gauger PG, Cook GJ, Colletti PM, Rubello D, Gross MD
Clin Nucl Med 2016 Aug;41(8):e368-82. doi: 10.1097/RLU.0000000000001112. PMID: 26825212
Machado NO, Al Qadhi H, Al Wahaibi K, Rizvi SG
JSLS 2015 Jul-Sep;19(3) doi: 10.4293/JSLS.2015.00036. PMID: 26175553Free PMC Article
Mearini L, Del Sordo R, Costantini E, Nunzi E, Porena M
Urol Int 2013;91(2):125-33. Epub 2012 Nov 8 doi: 10.1159/000345141. PMID: 23147196

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...