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Abnormal pulmonary valve cusp morphology

MedGen UID:
1623853
•Concept ID:
C4531035
•
Anatomical Abnormality
HPO: HP:0031566

Definition

Any structural anomaly of the pulmonary valve leaflets. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal pulmonary valve cusp morphology

Recent clinical studies

Etiology

Quadricuspid Pulmonary Valve: Case Report and the Comparison with Quadricuspid Aortic Valve.
Miyake T, Inoue T, Mushiake S
Curr Cardiol Rev 2023;19(2):e220322202505. doi: 10.2174/1573403X18666220322092706. PMID: 35319379Free PMC Article
Long-term outcomes of truncus arteriosus repair: A modulated renewal competing risks analysis.
Guariento A, Doulamis IP, Staffa SJ, Gellis L, Oh NA, Kido T, Mayer JE, Baird CW, Emani SM, Zurakowski D, Del Nido PJ, Nathan M
J Thorac Cardiovasc Surg 2022 Jan;163(1):224-236.e6. Epub 2021 Feb 12 doi: 10.1016/j.jtcvs.2021.01.136. PMID: 33726908
Almost All Incompetent BAV Should Be Repaired.
David TE
Semin Thorac Cardiovasc Surg 2019 Winter;31(4):661-663. Epub 2019 Apr 10 doi: 10.1053/j.semtcvs.2019.03.009. PMID: 30980931
Fused aortic valve without an elliptical-shaped systolic orifice in patients with severe aortic stenosis: cardiac computed tomography is useful for differentiation between bicuspid aortic valve with raphe and tricuspid aortic valve with commissural fusion.
Bak SH, Ko SM, Song MG, Shin JK, Chee HK, Kim JS
Eur Radiol 2015 Apr;25(4):1208-17. Epub 2014 Nov 26 doi: 10.1007/s00330-014-3494-1. PMID: 25424562
Intermediate-term results of repair for aortic, neoaortic, and truncal valve insufficiency in children.
Hawkins JA, Kouretas PC, Holubkov R, Williams RV, Tani LY, Su JT, Lambert LM, Mart CR, Puchalski MD, Minich LL
J Thorac Cardiovasc Surg 2007 May;133(5):1311-7. Epub 2007 Mar 29 doi: 10.1016/j.jtcvs.2006.11.051. PMID: 17467448

Diagnosis

Quadricuspid Pulmonary Valve: Case Report and the Comparison with Quadricuspid Aortic Valve.
Miyake T, Inoue T, Mushiake S
Curr Cardiol Rev 2023;19(2):e220322202505. doi: 10.2174/1573403X18666220322092706. PMID: 35319379Free PMC Article
Long-term outcomes of truncus arteriosus repair: A modulated renewal competing risks analysis.
Guariento A, Doulamis IP, Staffa SJ, Gellis L, Oh NA, Kido T, Mayer JE, Baird CW, Emani SM, Zurakowski D, Del Nido PJ, Nathan M
J Thorac Cardiovasc Surg 2022 Jan;163(1):224-236.e6. Epub 2021 Feb 12 doi: 10.1016/j.jtcvs.2021.01.136. PMID: 33726908
Transthoracic Echocardiographic Evaluation of Pulmonary Valve Anomalies in Pediatric Patients.
Wang SS, Xu MG, Zhuang J, Li WB, Zhang ZW, Xu G
J Ultrasound Med 2019 Apr;38(4):1091-1096. Epub 2018 Oct 7 doi: 10.1002/jum.14780. PMID: 30294866
Fused aortic valve without an elliptical-shaped systolic orifice in patients with severe aortic stenosis: cardiac computed tomography is useful for differentiation between bicuspid aortic valve with raphe and tricuspid aortic valve with commissural fusion.
Bak SH, Ko SM, Song MG, Shin JK, Chee HK, Kim JS
Eur Radiol 2015 Apr;25(4):1208-17. Epub 2014 Nov 26 doi: 10.1007/s00330-014-3494-1. PMID: 25424562
Valve-sparing options in tetralogy of Fallot surgery.
Bacha E
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2012;15(1):24-6. doi: 10.1053/j.pcsu.2012.01.006. PMID: 22424504

Therapy

Long-term outcomes of truncus arteriosus repair: A modulated renewal competing risks analysis.
Guariento A, Doulamis IP, Staffa SJ, Gellis L, Oh NA, Kido T, Mayer JE, Baird CW, Emani SM, Zurakowski D, Del Nido PJ, Nathan M
J Thorac Cardiovasc Surg 2022 Jan;163(1):224-236.e6. Epub 2021 Feb 12 doi: 10.1016/j.jtcvs.2021.01.136. PMID: 33726908
Almost All Incompetent BAV Should Be Repaired.
David TE
Semin Thorac Cardiovasc Surg 2019 Winter;31(4):661-663. Epub 2019 Apr 10 doi: 10.1053/j.semtcvs.2019.03.009. PMID: 30980931
Prosthetic reconstruction of bicuspid pulmonary valve in tetralogy of Fallot.
Sasikumar N, Ramanan S, Rema KM, Kumar RS, Subramanyan R, Cherian KM
Asian Cardiovasc Thorac Ann 2014 May;22(4):436-41. Epub 2013 Nov 13 doi: 10.1177/0218492313496416. PMID: 24771732
Pulmonary valve-in-valve implants: how long do they prolong reintervention and what causes them to fail?
Law KB, Phillips KR, Butany J
Cardiovasc Pathol 2012 Nov-Dec;21(6):519-21. Epub 2012 Mar 16 doi: 10.1016/j.carpath.2012.02.010. PMID: 22425628
Morphologic effects of percutaneous balloon pulmonary valvuloplasty.
Walls JT, Lababidi Z, Curtis JJ
South Med J 1987 Apr;80(4):475-8. doi: 10.1097/00007611-198704000-00017. PMID: 3563581

Prognosis

Quadricuspid Pulmonary Valve: Case Report and the Comparison with Quadricuspid Aortic Valve.
Miyake T, Inoue T, Mushiake S
Curr Cardiol Rev 2023;19(2):e220322202505. doi: 10.2174/1573403X18666220322092706. PMID: 35319379Free PMC Article
Long-term outcomes of truncus arteriosus repair: A modulated renewal competing risks analysis.
Guariento A, Doulamis IP, Staffa SJ, Gellis L, Oh NA, Kido T, Mayer JE, Baird CW, Emani SM, Zurakowski D, Del Nido PJ, Nathan M
J Thorac Cardiovasc Surg 2022 Jan;163(1):224-236.e6. Epub 2021 Feb 12 doi: 10.1016/j.jtcvs.2021.01.136. PMID: 33726908
Prosthetic reconstruction of bicuspid pulmonary valve in tetralogy of Fallot.
Sasikumar N, Ramanan S, Rema KM, Kumar RS, Subramanyan R, Cherian KM
Asian Cardiovasc Thorac Ann 2014 May;22(4):436-41. Epub 2013 Nov 13 doi: 10.1177/0218492313496416. PMID: 24771732
Surgical strategy for the bicuspid aortic valve: tricuspidization with cusp extension versus pulmonary autograft.
McMullan DM, Oppido G, Davies B, Kawahira Y, Cochrane AD, d'Udekem d'Acoz Y, Penny DJ, Brizard CP
J Thorac Cardiovasc Surg 2007 Jul;134(1):90-8. doi: 10.1016/j.jtcvs.2007.01.054. PMID: 17599491
Pulmonary valve reconstruction in absent pulmonary valve syndrome: a new technique.
Shatapathy P, Aggarwal BK, Kamath SG, Sai S
J Card Surg 1997 May-Jun;12(3):180-4. doi: 10.1111/j.1540-8191.1997.tb00120.x. PMID: 9395947

Clinical prediction guides

Three-dimensional transthoracic echocardiographic identification of individual cusps of the pulmonary valve: Potential misidentification by the two-dimensional technique.
Elsayed M, Hsiung MC, Nanda NC, Alratroot A, Turaga NSS
Echocardiography 2018 Jun;35(6):855-859. Epub 2018 Jun 2 doi: 10.1111/echo.14032. PMID: 29858885
Fused aortic valve without an elliptical-shaped systolic orifice in patients with severe aortic stenosis: cardiac computed tomography is useful for differentiation between bicuspid aortic valve with raphe and tricuspid aortic valve with commissural fusion.
Bak SH, Ko SM, Song MG, Shin JK, Chee HK, Kim JS
Eur Radiol 2015 Apr;25(4):1208-17. Epub 2014 Nov 26 doi: 10.1007/s00330-014-3494-1. PMID: 25424562
Morphologic determinants favoring surgical aortic valvuloplasty versus pulmonary autograft aortic valve replacement in children.
van Son JA, Reddy VM, Black MD, Rajasinghe H, Haas GS, Hanley FL
J Thorac Cardiovasc Surg 1996 Jun;111(6):1149-56; discussion 1156-7. doi: 10.1016/s0022-5223(96)70216-7. PMID: 8642815
Pulmonary valve eccentricity in d-transposition of the great arteries and implications for the arterial switch operation.
Kovalchin JP, Allen HD, Cassidy SC, Lev M, Bharati S
Am J Cardiol 1994 Jan 15;73(2):186-90. doi: 10.1016/0002-9149(94)90212-7. PMID: 8296741
Morphologic features of an intact ventricular septum susceptible to subpulmonary obstruction in complete transposition.
Chiu IS, Anderson RH, Macartney FJ, de Leval MR, Stark J
Am J Cardiol 1984 Jun 1;53(11):1633-8. doi: 10.1016/0002-9149(84)90592-7. PMID: 6731308

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