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Coronary cameral fistula to right ventricle

MedGen UID:
1627780
•Concept ID:
C4531039
•
Anatomical Abnormality
HPO: HP:0031561

Definition

An abnormal communication between the terminus of a coronary artery, bypassing the myocardial capillary bed and entering the right ventricle. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCoronary cameral fistula to right ventricle

Professional guidelines

PubMed

Unilateral and multilateral congenital coronary-pulmonary fistulas in adults: clinical presentation, diagnostic modalities, and management with a brief review of the literature.
Said SA, Nijhuis RL, Akker JW, Takechi M, Slart RH, Bos JS, Hoorntje CR, Houwelingen KG, Bakker-de Boo M, Braam RL, Vet TM
Clin Cardiol 2014 Sep;37(9):536-45. Epub 2014 Sep 5 doi: 10.1002/clc.22297. PMID: 25196980Free PMC Article

Recent clinical studies

Etiology

Coronary steal phenomenon following right ventricle decompression and revascularization of atretic left coronary ostium: case report.
Pająk J, Karolczak MA, Buczyński M, Mądry W, Grégoire DJ, Weryński P, Król-Jawień W, Godlewski K, Tomkiewicz-Pająk L, Kuźma J
J Cardiothorac Surg 2021 Oct 13;16(1):299. doi: 10.1186/s13019-021-01681-x. PMID: 34645497Free PMC Article
Congenital Aorto-Cardiac Connections (CACC) Revisited: Introduction of a Novel Anatomic-therapeutic Classification.
Rad EM, Hijazi ZM, Pouraliakbar H, Mirzaaghayan MR, Zamani H
Pediatr Cardiol 2021 Oct;42(7):1459-1477. Epub 2021 Jul 29 doi: 10.1007/s00246-021-02671-5. PMID: 34327543
Coronary artery changes in congenital coronary-cameral fistulas evaluated by computed tomographic angiography.
Siripornpitak S, Sriprachyakul A, Promphan W, Mokarapong P, Wanitkun S
Jpn J Radiol 2021 Dec;39(12):1149-1158. Epub 2021 Jun 28 doi: 10.1007/s11604-021-01164-y. PMID: 34181176
Right Ventricle-Dependent Coronary Circulation: Location of Obstruction Is Associated With Survival.
Spigel ZA, Qureshi AM, Morris SA, Mery CM, Sexson-Tejtel SK, Zea-Vera R, Binsalamah ZM, Imamura M, Heinle JS, Adachi I
Ann Thorac Surg 2020 May;109(5):1480-1487. Epub 2019 Sep 30 doi: 10.1016/j.athoracsur.2019.08.066. PMID: 31580859
Pulmonary atresia with intact ventricular septum and coronary cameral fistulae: an unusual finding of a subsystemic right ventricle.
Mohan S, Weinberg PM, Glatz AC
Cardiol Young 2016 Jun;26(5):979-82. Epub 2016 Jan 22 doi: 10.1017/S1047951115002711. PMID: 26796991

Diagnosis

Pediatric coronary cameral fistula in a structurally normal heart: a case report and review of the literature.
Mortezaeian H, Taheri M, Anafje M, Esmaeili Z, Hassanzadeh G, Ebrahimi P
J Med Case Rep 2024 Sep 20;18(1):456. doi: 10.1186/s13256-024-04784-w. PMID: 39300528Free PMC Article
Coronary-Cameral Fistula to Pulmonary Artery: An Innocent Bystander?
Bhasin D, Arora GK, Giridhara P, Gupta A, Isser HS, Bansal S
J Invasive Cardiol 2021 Jan;33(1):E70. doi: 10.25270/jic/20.00108. PMID: 33385992
Coronary-Cameral Fistula.
Boyle S, Jesuthasan LSB, Jenkins C, Challa P, Ranjan S, Dahiya A
Circ Cardiovasc Imaging 2019 May;12(5):e008691. doi: 10.1161/CIRCIMAGING.118.008691. PMID: 31088151
Multiple coronary-cameral fistulae.
Tiryakioglu SK, Gocer H, Tiryakioglu O, Kumbay E
Tex Heart Inst J 2010;37(3):378-9. PMID: 20548831Free PMC Article
Multiple coronary-cameral fistulae causing angina pectoris.
Arslan S, Gurlertop Y, Elbey MA, Karakelleoglu S
Tex Heart Inst J 2009;36(6):622-3. PMID: 20069097Free PMC Article

Therapy

A simple, ingenious approach for intra-operative detection of coronary cameral fistula.
Darbari A, Jhalani I, Kumar A, Kumar B
Asian Cardiovasc Thorac Ann 2024 Jun;32(5):321-323. Epub 2024 Jun 5 doi: 10.1177/02184923241260447. PMID: 38840480
A Bleeding Heart: Coronary-Cameral Fistula After Septal Myomectomy.
Walters D, Reeves R, Ang L, Pourdjabbar A, Mahmud E
J Invasive Cardiol 2017 Dec;29(12):E199-E200. PMID: 29207370
Coronary-Cameral Fistula Caused by Guidewire Trauma and Resolved by Coil Embolization.
Banerjee S, Patra S
Tex Heart Inst J 2016 Aug;43(4):338-40. Epub 2016 Aug 1 doi: 10.14503/THIJ-15-5177. PMID: 27547147Free PMC Article
Multiple coronary-cameral fistulae causing angina pectoris.
Arslan S, Gurlertop Y, Elbey MA, Karakelleoglu S
Tex Heart Inst J 2009;36(6):622-3. PMID: 20069097Free PMC Article
Acquired coronary-cameral fistula.
Jacob S, Feigenbaum H
Clin Cardiol 2009 Aug;32(8):E70. doi: 10.1002/clc.20507. PMID: 19610122Free PMC Article

Prognosis

Congenital Aorto-Cardiac Connections (CACC) Revisited: Introduction of a Novel Anatomic-therapeutic Classification.
Rad EM, Hijazi ZM, Pouraliakbar H, Mirzaaghayan MR, Zamani H
Pediatr Cardiol 2021 Oct;42(7):1459-1477. Epub 2021 Jul 29 doi: 10.1007/s00246-021-02671-5. PMID: 34327543
Innovative method to diagnose coronary Cameral fistula by contrast echocardiography.
Eldeib M, Qaddoura F, Sadek M, Abuelatta R, Nagib A
Echocardiography 2021 Feb;38(2):343-346. Epub 2021 Jan 9 doi: 10.1111/echo.14963. PMID: 33421182
Right Ventricle-Dependent Coronary Circulation: Location of Obstruction Is Associated With Survival.
Spigel ZA, Qureshi AM, Morris SA, Mery CM, Sexson-Tejtel SK, Zea-Vera R, Binsalamah ZM, Imamura M, Heinle JS, Adachi I
Ann Thorac Surg 2020 May;109(5):1480-1487. Epub 2019 Sep 30 doi: 10.1016/j.athoracsur.2019.08.066. PMID: 31580859
Coronary-Cameral Fistula.
Boyle S, Jesuthasan LSB, Jenkins C, Challa P, Ranjan S, Dahiya A
Circ Cardiovasc Imaging 2019 May;12(5):e008691. doi: 10.1161/CIRCIMAGING.118.008691. PMID: 31088151
Unilateral and multilateral congenital coronary-pulmonary fistulas in adults: clinical presentation, diagnostic modalities, and management with a brief review of the literature.
Said SA, Nijhuis RL, Akker JW, Takechi M, Slart RH, Bos JS, Hoorntje CR, Houwelingen KG, Bakker-de Boo M, Braam RL, Vet TM
Clin Cardiol 2014 Sep;37(9):536-45. Epub 2014 Sep 5 doi: 10.1002/clc.22297. PMID: 25196980Free PMC Article

Clinical prediction guides

A simple, ingenious approach for intra-operative detection of coronary cameral fistula.
Darbari A, Jhalani I, Kumar A, Kumar B
Asian Cardiovasc Thorac Ann 2024 Jun;32(5):321-323. Epub 2024 Jun 5 doi: 10.1177/02184923241260447. PMID: 38840480
Coronary artery changes in congenital coronary-cameral fistulas evaluated by computed tomographic angiography.
Siripornpitak S, Sriprachyakul A, Promphan W, Mokarapong P, Wanitkun S
Jpn J Radiol 2021 Dec;39(12):1149-1158. Epub 2021 Jun 28 doi: 10.1007/s11604-021-01164-y. PMID: 34181176
Right Ventricle-Dependent Coronary Circulation: Location of Obstruction Is Associated With Survival.
Spigel ZA, Qureshi AM, Morris SA, Mery CM, Sexson-Tejtel SK, Zea-Vera R, Binsalamah ZM, Imamura M, Heinle JS, Adachi I
Ann Thorac Surg 2020 May;109(5):1480-1487. Epub 2019 Sep 30 doi: 10.1016/j.athoracsur.2019.08.066. PMID: 31580859
Coronary-Cameral Fistula.
Boyle S, Jesuthasan LSB, Jenkins C, Challa P, Ranjan S, Dahiya A
Circ Cardiovasc Imaging 2019 May;12(5):e008691. doi: 10.1161/CIRCIMAGING.118.008691. PMID: 31088151
Unilateral and multilateral congenital coronary-pulmonary fistulas in adults: clinical presentation, diagnostic modalities, and management with a brief review of the literature.
Said SA, Nijhuis RL, Akker JW, Takechi M, Slart RH, Bos JS, Hoorntje CR, Houwelingen KG, Bakker-de Boo M, Braam RL, Vet TM
Clin Cardiol 2014 Sep;37(9):536-45. Epub 2014 Sep 5 doi: 10.1002/clc.22297. PMID: 25196980Free PMC Article

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