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Refractory Ewing Sarcoma

MedGen UID:
1631504
Concept ID:
C4684866
Neoplastic Process

Definition

Ewing sarcoma that does not respond to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Ewing Sarcoma

Professional guidelines

Recent clinical studies

Etiology

Xu J, Xie L, Sun X, Liu K, Liang X, Cai Z, Tang X, Guo W
Clin Cancer Res 2023 Mar 14;29(6):1040-1046. doi: 10.1158/1078-0432.CCR-22-3546. PMID: 36622702
Sano H, Mochizuki K, Kobayashi S, Ohara Y, Takahashi N, Kudo S, Ikeda K, Ohto H, Kikuta A
Cancer Rep (Hoboken) 2022 Jul;5(7):e1519. Epub 2021 Jul 22 doi: 10.1002/cnr2.1519. PMID: 34291886Free PMC Article
Podda MG, Luksch R, Puma N, Gandola L, Morosi C, Terenziani M, Ferrari A, Casanova M, Spreafico F, Meazza C, Catania S, Schiavello E, Biassoni V, Chiaravalli S, Massimino M
Tumori 2016 Jan-Feb;102(1):84-8. Epub 2015 Oct 28 doi: 10.5301/tj.5000419. PMID: 26797935
van Maldegem AM, Benson C, Rutkowski P, Blay JY, van den Berg H, Placzke J, Rasper M, Judson I, Juergens H, Dirksen U, Gelderblom H
Pediatr Blood Cancer 2015 Jan;62(1):40-4. Epub 2014 Sep 22 doi: 10.1002/pbc.25230. PMID: 25251256
Raciborska A, Bilska K, Drabko K, Chaber R, Pogorzala M, Wyrobek E, Polczyńska K, Rogowska E, Rodriguez-Galindo C, Wozniak W
Pediatr Blood Cancer 2013 Oct;60(10):1621-5. Epub 2013 Jun 15 doi: 10.1002/pbc.24621. PMID: 23776128

Diagnosis

Mooney B, Negri GL, Shyp T, Delaidelli A, Zhang HF, Spencer Miko SE, Weiner AK, Radaoui AB, Shraim R, Lizardo MM, Hughes CS, Li A, El-Naggar AM, Rouleau M, Li W, Dimitrov DS, Kurmasheva RT, Houghton PJ, Diskin SJ, Maris JM, Morin GB, Sorensen PH
Clin Cancer Res 2024 Mar 1;30(5):1022-1037. doi: 10.1158/1078-0432.CCR-23-2187. PMID: 37812652Free PMC Article
Lacroix J, Kis Z, Josupeit R, Schlund F, Stroh-Dege A, Frank-Stöhr M, Leuchs B, Schlehofer JR, Rommelaere J, Dinsart C
Viruses 2018 Jun 3;10(6) doi: 10.3390/v10060302. PMID: 29865280Free PMC Article
Podda MG, Luksch R, Puma N, Gandola L, Morosi C, Terenziani M, Ferrari A, Casanova M, Spreafico F, Meazza C, Catania S, Schiavello E, Biassoni V, Chiaravalli S, Massimino M
Tumori 2016 Jan-Feb;102(1):84-8. Epub 2015 Oct 28 doi: 10.5301/tj.5000419. PMID: 26797935
van Maldegem AM, Benson C, Rutkowski P, Blay JY, van den Berg H, Placzke J, Rasper M, Judson I, Juergens H, Dirksen U, Gelderblom H
Pediatr Blood Cancer 2015 Jan;62(1):40-4. Epub 2014 Sep 22 doi: 10.1002/pbc.25230. PMID: 25251256
DuBois SG, Krailo MD, Lessnick SL, Smith R, Chen Z, Marina N, Grier HE, Stegmaier K; Children's Oncology Group
Pediatr Blood Cancer 2009 Mar;52(3):324-7. doi: 10.1002/pbc.21822. PMID: 18989890Free PMC Article

Therapy

Xu J, Xie L, Sun X, Liu K, Liang X, Cai Z, Tang X, Guo W
Clin Cancer Res 2023 Mar 14;29(6):1040-1046. doi: 10.1158/1078-0432.CCR-22-3546. PMID: 36622702
Aykan MB, Erturk I, Acar R, Yildiran GS, Yildiz B, Karadurmus N
J Coll Physicians Surg Pak 2022 Jan;32(1):51-56. doi: 10.29271/jcpsp.2022.01.51. PMID: 34983148
Sano H, Mochizuki K, Kobayashi S, Ohara Y, Takahashi N, Kudo S, Ikeda K, Ohto H, Kikuta A
Cancer Rep (Hoboken) 2022 Jul;5(7):e1519. Epub 2021 Jul 22 doi: 10.1002/cnr2.1519. PMID: 34291886Free PMC Article
Podda MG, Luksch R, Puma N, Gandola L, Morosi C, Terenziani M, Ferrari A, Casanova M, Spreafico F, Meazza C, Catania S, Schiavello E, Biassoni V, Chiaravalli S, Massimino M
Tumori 2016 Jan-Feb;102(1):84-8. Epub 2015 Oct 28 doi: 10.5301/tj.5000419. PMID: 26797935
Raciborska A, Bilska K, Drabko K, Chaber R, Pogorzala M, Wyrobek E, Polczyńska K, Rogowska E, Rodriguez-Galindo C, Wozniak W
Pediatr Blood Cancer 2013 Oct;60(10):1621-5. Epub 2013 Jun 15 doi: 10.1002/pbc.24621. PMID: 23776128

Prognosis

Sano H, Mochizuki K, Kobayashi S, Ohara Y, Takahashi N, Kudo S, Ikeda K, Ohto H, Kikuta A
Cancer Rep (Hoboken) 2022 Jul;5(7):e1519. Epub 2021 Jul 22 doi: 10.1002/cnr2.1519. PMID: 34291886Free PMC Article
van Maldegem AM, Benson C, Rutkowski P, Blay JY, van den Berg H, Placzke J, Rasper M, Judson I, Juergens H, Dirksen U, Gelderblom H
Pediatr Blood Cancer 2015 Jan;62(1):40-4. Epub 2014 Sep 22 doi: 10.1002/pbc.25230. PMID: 25251256
Yoon JH, Kwon MM, Park HJ, Park SY, Lim KY, Joo J, Park BK
BMC Cancer 2014 Aug 28;14:622. doi: 10.1186/1471-2407-14-622. PMID: 25164234Free PMC Article
Yildiz I, Sen F, Ekenel M, Darendeliler E, Bavbek S, Agaoglu F, Ozger H, Eralp L, Bilgic B, Basaran M
In Vivo 2014 May-Jun;28(3):403-9. PMID: 24815845
Raciborska A, Bilska K, Drabko K, Chaber R, Pogorzala M, Wyrobek E, Polczyńska K, Rogowska E, Rodriguez-Galindo C, Wozniak W
Pediatr Blood Cancer 2013 Oct;60(10):1621-5. Epub 2013 Jun 15 doi: 10.1002/pbc.24621. PMID: 23776128

Clinical prediction guides

Aykan MB, Erturk I, Acar R, Yildiran GS, Yildiz B, Karadurmus N
J Coll Physicians Surg Pak 2022 Jan;32(1):51-56. doi: 10.29271/jcpsp.2022.01.51. PMID: 34983148
Lacroix J, Kis Z, Josupeit R, Schlund F, Stroh-Dege A, Frank-Stöhr M, Leuchs B, Schlehofer JR, Rommelaere J, Dinsart C
Viruses 2018 Jun 3;10(6) doi: 10.3390/v10060302. PMID: 29865280Free PMC Article
Grohar PJ, Glod J, Peer CJ, Sissung TM, Arnaldez FI, Long L, Figg WD, Whitcomb P, Helman LJ, Widemann BC
Cancer Chemother Pharmacol 2017 Sep;80(3):645-652. Epub 2017 Jul 22 doi: 10.1007/s00280-017-3382-x. PMID: 28735378Free PMC Article
Wagner LM, Fouladi M, Ahmed A, Krailo MD, Weigel B, DuBois SG, Doyle LA, Chen H, Blaney SM
Pediatr Blood Cancer 2015 Mar;62(3):440-4. Epub 2014 Nov 28 doi: 10.1002/pbc.25334. PMID: 25446280Free PMC Article
Choy E, Butrynski JE, Harmon DC, Morgan JA, George S, Wagner AJ, D'Adamo D, Cote GM, Flamand Y, Benes CH, Haber DA, Baselga JM, Demetri GD
BMC Cancer 2014 Nov 5;14:813. doi: 10.1186/1471-2407-14-813. PMID: 25374341Free PMC Article

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