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Saccular aortic arch aneurysm

MedGen UID:
1635821
Concept ID:
C4703461
Disease or Syndrome
HPO: HP:0031647

Definition

An eccentric abnormal localized widening (dilatation) of the aortic arch that involves only a portion of the circumference of the vessel wall. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSaccular aortic arch aneurysm

Professional guidelines

PubMed

Silverberg D, Bar-Dayan A, Rimon U, Raskin D, Fefer P, Halak M
Vasc Endovascular Surg 2020 Jul;54(5):423-429. Epub 2020 Apr 23 doi: 10.1177/1538574420921282. PMID: 32323631
Abraham CZ, Lioupis C
J Thorac Cardiovasc Surg 2013 Mar;145(3 Suppl):S110-7. doi: 10.1016/j.jtcvs.2012.11.064. PMID: 23410767
Ueno A, Maruyama Y, Tada Y, Fukushima K
J Cardiovasc Surg (Torino) 1976 Sep-Oct;17(5):408-12. PMID: 9414

Recent clinical studies

Etiology

Dionne PO, Tenorio ER, Cajas Monson LC, Pochettino A, Oderich GS
Ann Thorac Surg 2021 Jul;112(1):e27-e31. Epub 2020 Jun 17 doi: 10.1016/j.athoracsur.2020.04.120. PMID: 32562624
Bayliss CD, Booth KL, Williams R, Dark JH, Gould KF
Ann Thorac Surg 2017 Nov;104(5):e379-e381. doi: 10.1016/j.athoracsur.2017.07.005. PMID: 29054233
Baldwin ZK, Chuter TA, Hiramoto JS, Reilly LM, Schneider DB
J Endovasc Ther 2008 Apr;15(2):161-5. doi: 10.1583/07-2308.1. PMID: 18426274
Lin JS, Chang SC, Chen FJ, Chern MS
Chest 1996 Jan;109(1):127-30. doi: 10.1378/chest.109.1.127. PMID: 8549173

Diagnosis

Tran MT, Nguyen HS, Nguyen HD, Le TQ
Circ Cardiovasc Imaging 2022 Jan;15(1):e013783. Epub 2021 Dec 28 doi: 10.1161/CIRCIMAGING.121.013783. PMID: 34961329
Dionne PO, Tenorio ER, Cajas Monson LC, Pochettino A, Oderich GS
Ann Thorac Surg 2021 Jul;112(1):e27-e31. Epub 2020 Jun 17 doi: 10.1016/j.athoracsur.2020.04.120. PMID: 32562624
Waikittipong S
Asian Cardiovasc Thorac Ann 2012 Oct;20(5):575-7. doi: 10.1177/0218492311436257. PMID: 23087303
Siddiqui MA, Akhtar J, Rizvi SW, Rizvi SA, Ahmad I, Ekramullah M
Tuberk Toraks 2012;60(2):163-6. doi: 10.5578/tt.3649. PMID: 22779938
Lin JS, Chang SC, Chen FJ, Chern MS
Chest 1996 Jan;109(1):127-30. doi: 10.1378/chest.109.1.127. PMID: 8549173

Therapy

Ben Hammamia M, Ziadi J, Miri R, Ben Mrad M, Ghedira F, Denguir R
Ann Vasc Surg 2019 May;57:272.e9-272.e13. Epub 2019 Jan 24 doi: 10.1016/j.avsg.2018.09.040. PMID: 30684627
Bayliss CD, Booth KL, Williams R, Dark JH, Gould KF
Ann Thorac Surg 2017 Nov;104(5):e379-e381. doi: 10.1016/j.athoracsur.2017.07.005. PMID: 29054233
Westaby S, Luthra S, Anthony S, Ormerod O, Wilson N
Circulation 2012 Mar 13;125(10):1318-20. doi: 10.1161/CIRCULATIONAHA.111.048710. PMID: 22412093
Kojima N, Sakano Y, Ohki S, Misawa Y
Interact Cardiovasc Thorac Surg 2011 Mar;12(3):502-4. Epub 2010 Dec 21 doi: 10.1510/icvts.2010.260976. PMID: 21177298

Prognosis

Dionne PO, Tenorio ER, Cajas Monson LC, Pochettino A, Oderich GS
Ann Thorac Surg 2021 Jul;112(1):e27-e31. Epub 2020 Jun 17 doi: 10.1016/j.athoracsur.2020.04.120. PMID: 32562624
Tan TXZ, Balakrishnan T, Lam MHH, Chui YY, Cheng LT
J Radiol Case Rep 2019 Jul;13(7):21-28. Epub 2019 Jul 31 doi: 10.3941/jrcr.v13i7.3580. PMID: 31558964Free PMC Article
Ben Hammamia M, Ziadi J, Miri R, Ben Mrad M, Ghedira F, Denguir R
Ann Vasc Surg 2019 May;57:272.e9-272.e13. Epub 2019 Jan 24 doi: 10.1016/j.avsg.2018.09.040. PMID: 30684627
Siddiqui MA, Akhtar J, Rizvi SW, Rizvi SA, Ahmad I, Ekramullah M
Tuberk Toraks 2012;60(2):163-6. doi: 10.5578/tt.3649. PMID: 22779938
Kojima N, Sakano Y, Ohki S, Misawa Y
Interact Cardiovasc Thorac Surg 2011 Mar;12(3):502-4. Epub 2010 Dec 21 doi: 10.1510/icvts.2010.260976. PMID: 21177298

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