U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormal tricuspid valve physiology

MedGen UID:
1642206
•Concept ID:
C4703463
•
Disease or Syndrome
HPO: HP:0031651

Definition

Any functional defect of the tricuspid valve. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal tricuspid valve physiology

Professional guidelines

PubMed

The American Association for Thoracic Surgery (AATS) 2024 expert consensus document: Management of neonates and infants with Ebstein anomaly.
Konstantinov IE, Chai P, Bacha E, Caldarone CA, Da Silva JP, Da Fonseca Da Silva L, Dearani J, Hornberger L, Knott-Craig C, Del Nido P, Qureshi M, Sarris G, Starnes V, Tsang V
J Thorac Cardiovasc Surg 2024 Aug;168(2):311-324. Epub 2024 Apr 27 doi: 10.1016/j.jtcvs.2024.04.018. PMID: 38685467
Periprocedural and perioperatory management of patients with tricuspid valve disease.
Monaco F, Di Prima AL, De Luca M, Barucco G, Zangrillo A
Minerva Cardioangiol 2018 Dec;66(6):691-699. Epub 2018 Apr 11 doi: 10.23736/S0026-4725.18.04699-6. PMID: 29642696
Ebstein's Anomaly: Genetics, Clinical Manifestations, and Management.
Yuan SM
Pediatr Neonatol 2017 Jun;58(3):211-215. Epub 2016 Nov 19 doi: 10.1016/j.pedneo.2016.08.004. PMID: 28017577

Recent clinical studies

Etiology

Heart failure in the adult Ebstein patient.
Schultz K, Haeffele CL
Heart Fail Rev 2020 Jul;25(4):623-632. doi: 10.1007/s10741-020-09930-2. PMID: 32472521
Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Anatomy and Physiology of the Tricuspid Valve.
Dahou A, Levin D, Reisman M, Hahn RT
JACC Cardiovasc Imaging 2019 Mar;12(3):458-468. doi: 10.1016/j.jcmg.2018.07.032. PMID: 30846121
Polyamines and microbiota in bicuspid and tricuspid aortic valve aortopathy.
Forte A, Balistreri CR, De Feo M, Della Corte A, Hellstrand P, Persson L, Nilsson BO
J Mol Cell Cardiol 2019 Apr;129:179-187. Epub 2019 Feb 28 doi: 10.1016/j.yjmcc.2019.02.014. PMID: 30825483
Echocardiographic assessment of Ebstein's anomaly.
Booker OJ, Nanda NC
Echocardiography 2015 Jan;32 Suppl 2:S177-88. Epub 2014 May 29 doi: 10.1111/echo.12486. PMID: 24888693

Diagnosis

Transposition physiology in the setting of concordant ventriculo-arterial connections.
Chowdhury UK, Anderson RH, Spicer DE, George N, Sankhyan LK, Pandey NN, Goja S, Chandhirasekar B
J Card Surg 2022 Sep;37(9):2823-2834. Epub 2022 Jun 19 doi: 10.1111/jocs.16688. PMID: 35717625
Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Morphologic Types of Tricuspid Regurgitation: Characteristics and Prognostic Implications.
Prihadi EA, Delgado V, Leon MB, Enriquez-Sarano M, Topilsky Y, Bax JJ
JACC Cardiovasc Imaging 2019 Mar;12(3):491-499. doi: 10.1016/j.jcmg.2018.09.027. PMID: 30846123
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687
Ebstein anomaly: a review.
Galea J, Ellul S, Schembri A, Schembri-Wismayer P, Calleja-Agius J
Neonatal Netw 2014 Sep-Oct;33(5):268-74. doi: 10.1891/0730-0832.33.5.268. PMID: 25161135

Therapy

The American Association for Thoracic Surgery (AATS) 2024 expert consensus document: Management of neonates and infants with Ebstein anomaly.
Konstantinov IE, Chai P, Bacha E, Caldarone CA, Da Silva JP, Da Fonseca Da Silva L, Dearani J, Hornberger L, Knott-Craig C, Del Nido P, Qureshi M, Sarris G, Starnes V, Tsang V
J Thorac Cardiovasc Surg 2024 Aug;168(2):311-324. Epub 2024 Apr 27 doi: 10.1016/j.jtcvs.2024.04.018. PMID: 38685467
Pulmonary hypertension in bronchopulmonary dysplasia.
Hansmann G, Sallmon H, Roehr CC, Kourembanas S, Austin ED, Koestenberger M; European Pediatric Pulmonary Vascular Disease Network (EPPVDN)
Pediatr Res 2021 Feb;89(3):446-455. Epub 2020 Jun 10 doi: 10.1038/s41390-020-0993-4. PMID: 32521539Free PMC Article
Ebstein's Anomaly.
Holst KA, Connolly HM, Dearani JA
Methodist Debakey Cardiovasc J 2019 Apr-Jun;15(2):138-144. doi: 10.14797/mdcj-15-2-138. PMID: 31384377Free PMC Article
Neonatal Ebstein Anomaly.
Kumar TKS, Boston US, Knott-Craig CJ
Semin Thorac Cardiovasc Surg 2017 Autumn;29(3):331-337. Epub 2017 Sep 25 doi: 10.1053/j.semtcvs.2017.09.006. PMID: 28958645
Reexamining remodeling.
Schäfers HJ, Raddatz A, Schmied W, Takahashi H, Miura Y, Kunihara T, Aicher D
J Thorac Cardiovasc Surg 2015 Feb;149(2 Suppl):S30-6. Epub 2014 Sep 18 doi: 10.1016/j.jtcvs.2014.09.048. PMID: 25439784

Prognosis

Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Morphologic Types of Tricuspid Regurgitation: Characteristics and Prognostic Implications.
Prihadi EA, Delgado V, Leon MB, Enriquez-Sarano M, Topilsky Y, Bax JJ
JACC Cardiovasc Imaging 2019 Mar;12(3):491-499. doi: 10.1016/j.jcmg.2018.09.027. PMID: 30846123
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687
Ebstein anomaly: a review.
Galea J, Ellul S, Schembri A, Schembri-Wismayer P, Calleja-Agius J
Neonatal Netw 2014 Sep-Oct;33(5):268-74. doi: 10.1891/0730-0832.33.5.268. PMID: 25161135
Idiopathic ventricular tachycardia.
Altemose GT, Buxton AE
Annu Rev Med 1999;50:159-77. doi: 10.1146/annurev.med.50.1.159. PMID: 10073270

Clinical prediction guides

Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Ebstein's Anomaly.
Holst KA, Connolly HM, Dearani JA
Methodist Debakey Cardiovasc J 2019 Apr-Jun;15(2):138-144. doi: 10.14797/mdcj-15-2-138. PMID: 31384377Free PMC Article
MicroRNAs fingerprint of bicuspid aortic valve.
Sabatino J, Wicik Z, De Rosa S, Eyileten C, Jakubik D, Spaccarotella C, Mongiardo A, Postula M, Indolfi C
J Mol Cell Cardiol 2019 Sep;134:98-106. Epub 2019 Jul 3 doi: 10.1016/j.yjmcc.2019.07.001. PMID: 31278905
Morphologic Types of Tricuspid Regurgitation: Characteristics and Prognostic Implications.
Prihadi EA, Delgado V, Leon MB, Enriquez-Sarano M, Topilsky Y, Bax JJ
JACC Cardiovasc Imaging 2019 Mar;12(3):491-499. doi: 10.1016/j.jcmg.2018.09.027. PMID: 30846123
Cardiac imaging in Ebstein anomaly.
Qureshi MY, O'Leary PW, Connolly HM
Trends Cardiovasc Med 2018 Aug;28(6):403-409. Epub 2018 Jan 12 doi: 10.1016/j.tcm.2018.01.002. PMID: 29409687

Recent systematic reviews

Family screening for bicuspid aortic valve and aortic dilatation: a meta-analysis.
Bray JJH, Freer R, Pitcher A, Kharbanda R
Eur Heart J 2023 Sep 1;44(33):3152-3164. doi: 10.1093/eurheartj/ehad320. PMID: 37288540Free PMC Article
End-Diastolic Forward Flow and Restrictive Physiology in Repaired Tetralogy of Fallot: A Systematic Review and Meta-Analysis.
Van den Eynde J, Derdeyn E, Schuermans A, Shivaram P, Budts W, Danford DA, Kutty S
J Am Heart Assoc 2022 Apr 5;11(7):e024036. Epub 2022 Mar 18 doi: 10.1161/JAHA.121.024036. PMID: 35301867Free PMC Article
Absent pulmonary valve with tricuspid atresia/stenosis: literature review with new three long-term cases.
Kawasaki Y, Murakami Y, Fujino M, Sasaki T, Nakamura K, Yoshida Y, Suzuki T, Nishigaki K, Ehara E
Heart Vessels 2022 Jan;37(1):142-151. Epub 2021 Jun 5 doi: 10.1007/s00380-021-01887-y. PMID: 34089363
Risk Factors for Coarctation of the Aorta on Prenatal Ultrasound: A Systematic Review and Meta-Analysis.
Familiari A, Morlando M, Khalil A, Sonesson SE, Scala C, Rizzo G, Del Sordo G, Vassallo C, Elena Flacco M, Manzoli L, Lanzone A, Scambia G, Acharya G, D'Antonio F
Circulation 2017 Feb 21;135(8):772-785. Epub 2016 Dec 29 doi: 10.1161/CIRCULATIONAHA.116.024068. PMID: 28034902
Complex Ebstein's malformation: defining preoperative cardiac anatomy and function.
Negoi RI, Ispas AT, Ghiorghiu I, Filipoiu F, Negoi I, Hostiuc M, Hostiuc S, Ginghina C
J Card Surg 2013 Jan;28(1):70-81. doi: 10.1111/jocs.12032. PMID: 23330581

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...