U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Recurrent Desmoid Fibromatosis

MedGen UID:
1654474
Concept ID:
C4744430
Neoplastic Process
Synonyms: Recurrent Desmoid Tumor; Recurrent Desmoid-Type Fibromatosis

Definition

Desmoid fibromatosis that has recurred after a period of remission. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRecurrent Desmoid Fibromatosis

Professional guidelines

PubMed

Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Spolverato G, Capelli G, Kasper B, Gounder M
Surg Oncol Clin N Am 2022 Jul;31(3):447-458. Epub 2022 May 31 doi: 10.1016/j.soc.2022.03.008. PMID: 35715144
Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article

Recent clinical studies

Etiology

Gounder M, Ratan R, Alcindor T, Schöffski P, van der Graaf WT, Wilky BA, Riedel RF, Lim A, Smith LM, Moody S, Attia S, Chawla S, D'Amato G, Federman N, Merriam P, Van Tine BA, Vincenzi B, Benson C, Bui NQ, Chugh R, Tinoco G, Charlson J, Dileo P, Hartner L, Lapeire L, Mazzeo F, Palmerini E, Reichardt P, Stacchiotti S, Bailey HH, Burgess MA, Cote GM, Davis LE, Deshpande H, Gelderblom H, Grignani G, Loggers E, Philip T, Pressey JG, Kummar S, Kasper B
N Engl J Med 2023 Mar 9;388(10):898-912. doi: 10.1056/NEJMoa2210140. PMID: 36884323
Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Spolverato G, Capelli G, Kasper B, Gounder M
Surg Oncol Clin N Am 2022 Jul;31(3):447-458. Epub 2022 May 31 doi: 10.1016/j.soc.2022.03.008. PMID: 35715144
Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Gounder MM, Mahoney MR, Van Tine BA, Ravi V, Attia S, Deshpande HA, Gupta AA, Milhem MM, Conry RM, Movva S, Pishvaian MJ, Riedel RF, Sabagh T, Tap WD, Horvat N, Basch E, Schwartz LH, Maki RG, Agaram NP, Lefkowitz RA, Mazaheri Y, Yamashita R, Wright JJ, Dueck AC, Schwartz GK
N Engl J Med 2018 Dec 20;379(25):2417-2428. doi: 10.1056/NEJMoa1805052. PMID: 30575484Free PMC Article

Diagnosis

Okuda M, Yoshida K, Kobayashi S, Gabata T
Skeletal Radiol 2023 Jul;52(7):1293-1303. Epub 2023 Jan 16 doi: 10.1007/s00256-023-04275-x. PMID: 36646850
Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Otero S, Moskovic EC, Strauss DC, Benson C, Miah AB, Thway K, Messiou C
Clin Radiol 2015 Sep;70(9):1038-45. Epub 2015 Jul 7 doi: 10.1016/j.crad.2015.04.015. PMID: 26162574
Fisher C, Thway K
Pathology 2014 Feb;46(2):135-40. doi: 10.1097/PAT.0000000000000045. PMID: 24378386

Therapy

Gounder M, Ratan R, Alcindor T, Schöffski P, van der Graaf WT, Wilky BA, Riedel RF, Lim A, Smith LM, Moody S, Attia S, Chawla S, D'Amato G, Federman N, Merriam P, Van Tine BA, Vincenzi B, Benson C, Bui NQ, Chugh R, Tinoco G, Charlson J, Dileo P, Hartner L, Lapeire L, Mazzeo F, Palmerini E, Reichardt P, Stacchiotti S, Bailey HH, Burgess MA, Cote GM, Davis LE, Deshpande H, Gelderblom H, Grignani G, Loggers E, Philip T, Pressey JG, Kummar S, Kasper B
N Engl J Med 2023 Mar 9;388(10):898-912. doi: 10.1056/NEJMoa2210140. PMID: 36884323
Zhou MY, Bui NQ, Charville GW, Ghanouni P, Ganjoo KN
Cancer Treat Res Commun 2022;31:100562. Epub 2022 Apr 16 doi: 10.1016/j.ctarc.2022.100562. PMID: 35460976
Gounder MM, Mahoney MR, Van Tine BA, Ravi V, Attia S, Deshpande HA, Gupta AA, Milhem MM, Conry RM, Movva S, Pishvaian MJ, Riedel RF, Sabagh T, Tap WD, Horvat N, Basch E, Schwartz LH, Maki RG, Agaram NP, Lefkowitz RA, Mazaheri Y, Yamashita R, Wright JJ, Dueck AC, Schwartz GK
N Engl J Med 2018 Dec 20;379(25):2417-2428. doi: 10.1056/NEJMoa1805052. PMID: 30575484Free PMC Article
Gounder MM, Thomas DM, Tap WD
J Clin Oncol 2018 Jan 10;36(2):202-209. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.8482. PMID: 29220303Free PMC Article
Martínez Trufero J, Pajares Bernad I, Torres Ramón I, Hernando Cubero J, Pazo Cid R
Curr Treat Options Oncol 2017 May;18(5):29. doi: 10.1007/s11864-017-0474-0. PMID: 28439797

Prognosis

Okuda M, Yoshida K, Kobayashi S, Gabata T
Skeletal Radiol 2023 Jul;52(7):1293-1303. Epub 2023 Jan 16 doi: 10.1007/s00256-023-04275-x. PMID: 36646850
Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Gounder MM, Mahoney MR, Van Tine BA, Ravi V, Attia S, Deshpande HA, Gupta AA, Milhem MM, Conry RM, Movva S, Pishvaian MJ, Riedel RF, Sabagh T, Tap WD, Horvat N, Basch E, Schwartz LH, Maki RG, Agaram NP, Lefkowitz RA, Mazaheri Y, Yamashita R, Wright JJ, Dueck AC, Schwartz GK
N Engl J Med 2018 Dec 20;379(25):2417-2428. doi: 10.1056/NEJMoa1805052. PMID: 30575484Free PMC Article
Martínez Trufero J, Pajares Bernad I, Torres Ramón I, Hernando Cubero J, Pazo Cid R
Curr Treat Options Oncol 2017 May;18(5):29. doi: 10.1007/s11864-017-0474-0. PMID: 28439797
Fiore M, MacNeill A, Gronchi A, Colombo C
Surg Oncol Clin N Am 2016 Oct;25(4):803-26. Epub 2016 Aug 5 doi: 10.1016/j.soc.2016.05.010. PMID: 27591500

Clinical prediction guides

Gounder M, Ratan R, Alcindor T, Schöffski P, van der Graaf WT, Wilky BA, Riedel RF, Lim A, Smith LM, Moody S, Attia S, Chawla S, D'Amato G, Federman N, Merriam P, Van Tine BA, Vincenzi B, Benson C, Bui NQ, Chugh R, Tinoco G, Charlson J, Dileo P, Hartner L, Lapeire L, Mazzeo F, Palmerini E, Reichardt P, Stacchiotti S, Bailey HH, Burgess MA, Cote GM, Davis LE, Deshpande H, Gelderblom H, Grignani G, Loggers E, Philip T, Pressey JG, Kummar S, Kasper B
N Engl J Med 2023 Mar 9;388(10):898-912. doi: 10.1056/NEJMoa2210140. PMID: 36884323
Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Gounder MM, Thomas DM, Tap WD
J Clin Oncol 2018 Jan 10;36(2):202-209. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.8482. PMID: 29220303Free PMC Article
Grignol VP, Pollock R, Howard JH
Surg Clin North Am 2016 Oct;96(5):1015-30. doi: 10.1016/j.suc.2016.05.008. PMID: 27542640
Sakorafas GH, Nissotakis C, Peros G
Surg Oncol 2007 Aug;16(2):131-42. Epub 2007 Aug 24 doi: 10.1016/j.suronc.2007.07.009. PMID: 17719772

Recent systematic reviews

Meade A, Wisecarver I, Cho MJ, Davis JJ, Duque S, Farewell JT, Zhang AY
Ann Plast Surg 2023 May 1;90(5S Suppl 2):S195-S202. Epub 2022 Dec 21 doi: 10.1097/SAP.0000000000003381. PMID: 36729103
Moore D, Burns L, Creavin B, Ryan E, Conlon K, Kelly ME, Kavanagh D
Ir J Med Sci 2023 Apr;192(2):549-560. Epub 2022 Apr 21 doi: 10.1007/s11845-022-03008-8. PMID: 35445926Free PMC Article
Kito M, Ogose A, Yoshida M, Nishida Y
Jpn J Clin Oncol 2020 May 5;50(5):574-580. doi: 10.1093/jjco/hyaa009. PMID: 32115631
Toh JW, Morgan M
Colorectal Dis 2016 Apr;18(4):337-50. doi: 10.1111/codi.13232. PMID: 26663419
Ver Halen JP, Soto-Miranda MA, Sandoval JA
Ann Plast Surg 2015 Oct;75(4):480-6. doi: 10.1097/SAP.0000000000000129. PMID: 26360656

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...