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Adrenal Gland Sarcoma

MedGen UID:
1656574
•Concept ID:
C4745189
•
Neoplastic Process

Definition

A rare sarcoma that arises from the adrenal gland. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdrenal Gland Sarcoma

Professional guidelines

PubMed

Sunitinib for the treatment of patients with advanced pheochromocytomas or paragangliomas: The phase 2 non-randomized SUTNET clinical trial.
Nasca V, Prinzi N, Coppa J, Prisciandaro M, Oldani S, Ghelardi F, Conca E, Capone I, Busico A, Perrone F, Tamborini E, Sabella G, Greco G, Greco FG, Tafuto S, Procopio G, Morano F, Niger M, Maccauro M, Milione M, de Braud F, Pietrantonio F, Pusceddu S
Eur J Cancer 2024 Sep;209:114276. Epub 2024 Aug 9 doi: 10.1016/j.ejca.2024.114276. PMID: 39128186
Role of repeated F-18 fluorodeoxyglucose imaging in management of patients with bone and soft tissue sarcoma.
el-Zeftawy H, Heiba SI, Jana S, Rosen G, Salem S, Santiago JF, Abdel-Dayem HM
Cancer Biother Radiopharm 2001 Feb;16(1):37-46. doi: 10.1089/108497801750096005. PMID: 11279796
Significance and management of local recurrences and limited metastatic disease in the abdomen.
Windham TC, Pearson AS, Skibber JM, Mansfield PF, Lee JE, Pisters PW, Evans DB
Surg Clin North Am 2000 Apr;80(2):761-74, xii. doi: 10.1016/s0039-6109(05)70211-5. PMID: 10836016

Recent clinical studies

Therapy

Ewing sarcoma of the adrenal gland: a case report and review of the literature.
Eddaoualline H, Mazouz K, Rafiq B, El Mghari Tabib G, El Ansari N, Belbaraka R, El Omrani A, Khouchani M
J Med Case Rep 2018 Mar 16;12(1):69. doi: 10.1186/s13256-018-1601-7. PMID: 29544549Free PMC Article
A vinyl chloride-exposed worker with an adrenal gland angiosarcoma: a case report.
Criscuolo M, Valerio J, Gianicolo ME, Gianicolo EA, Portaluri M
Ind Health 2014;52(1):66-70. Epub 2013 Dec 2 doi: 10.2486/indhealth.2013-0044. PMID: 24292955Free PMC Article
Ewing's sarcoma/primitive neuroectodermal tumor arising from the adrenal gland: a case report and literature review.
Sasaki T, Onishi T, Yabana T, Hoshina A
Tumori 2013 May-Jun;99(3):e104-6. doi: 10.1177/030089161309900326. PMID: 24158076
Unusual presentation of Ewing sarcoma in the adrenal gland: a secondary malignancy from a survivor of Burkitt lymphoma.
Lim SH, Lee JY, Lee JY, Kim JH, Choi KH, Hyun JY, Ko YH, Lee J, Kim SJ, Kim WS
Jpn J Clin Oncol 2013 Jun;43(6):676-80. Epub 2013 Apr 5 doi: 10.1093/jjco/hyt047. PMID: 23564674
Second primary malignancy risk in thyroid cancer survivors: a systematic review and meta-analysis.
Subramanian S, Goldstein DP, Parlea L, Thabane L, Ezzat S, Ibrahim-Zada I, Straus S, Brierley JD, Tsang RW, Gafni A, Rotstein L, Sawka AM
Thyroid 2007 Dec;17(12):1277-88. doi: 10.1089/thy.2007.0171. PMID: 18020916

Prognosis

Single-cell transcriptomic analyses provide insights into the developmental origins of neuroblastoma.
Jansky S, Sharma AK, Körber V, Quintero A, Toprak UH, Wecht EM, Gartlgruber M, Greco A, Chomsky E, Grünewald TGP, Henrich KO, Tanay A, Herrmann C, Höfer T, Westermann F
Nat Genet 2021 May;53(5):683-693. Epub 2021 Mar 25 doi: 10.1038/s41588-021-00806-1. PMID: 33767450
Metastatic Pheochromocytomas and Abdominal Paragangliomas.
Granberg D, Juhlin CC, Falhammar H
J Clin Endocrinol Metab 2021 Apr 23;106(5):e1937-e1952. doi: 10.1210/clinem/dgaa982. PMID: 33462603Free PMC Article
Adrenalectomy for Secondary Malignancy: Patients, Outcomes, and Indications.
Wachtel H, Roses RE, Kuo LE, Lindeman BM, Nehs MA, Tavakkoli A, Parangi S, Hodin RA, Fraker DL, James BC, Carr AA, Wang TS, Solórzano CC, Lubitz CC
Ann Surg 2021 Dec 1;274(6):1073-1080. doi: 10.1097/SLA.0000000000003876. PMID: 32427760
Rare adrenal gland incidentaloma: an unusual Ewing's sarcoma family of tumor presentation and literature review.
Guo H, Chen S, Liu S, Wang K, Liu E, Li F, Hou Y
BMC Urol 2017 Apr 4;17(1):24. doi: 10.1186/s12894-017-0217-3. PMID: 28376845Free PMC Article
New genes and/or molecular pathways associated with adrenal hyperplasias and related adrenocortical tumors.
Stratakis CA
Mol Cell Endocrinol 2009 Mar 5;300(1-2):152-7. Epub 2008 Nov 21 doi: 10.1016/j.mce.2008.11.010. PMID: 19063937Free PMC Article

Clinical prediction guides

Second Primary Cancer Among Patients With Papillary Thyroid Carcinoma Following the Chernobyl Disaster.
Taha A, Taha-Mehlitz S, Nadyrov EA, Zinovkin D, Veyalkin I, Levin L, Pranjol MZI, Melling N, Honaker MD, Cattin PC, Schmid RA
JAMA Netw Open 2023 Aug 1;6(8):e2329559. doi: 10.1001/jamanetworkopen.2023.29559. PMID: 37589974Free PMC Article
Metastatic Pheochromocytomas and Abdominal Paragangliomas.
Granberg D, Juhlin CC, Falhammar H
J Clin Endocrinol Metab 2021 Apr 23;106(5):e1937-e1952. doi: 10.1210/clinem/dgaa982. PMID: 33462603Free PMC Article
Adrenalectomy for Secondary Malignancy: Patients, Outcomes, and Indications.
Wachtel H, Roses RE, Kuo LE, Lindeman BM, Nehs MA, Tavakkoli A, Parangi S, Hodin RA, Fraker DL, James BC, Carr AA, Wang TS, Solórzano CC, Lubitz CC
Ann Surg 2021 Dec 1;274(6):1073-1080. doi: 10.1097/SLA.0000000000003876. PMID: 32427760
MYO5B mutations in pheochromocytoma/paraganglioma promote cancer progression.
Tomić TT, Olausson J, Rehammar A, Deland L, Muth A, Ejeskär K, Nilsson S, Kristiansson E, Wassén ON, Abel F
PLoS Genet 2020 Jun;16(6):e1008803. Epub 2020 Jun 8 doi: 10.1371/journal.pgen.1008803. PMID: 32511227Free PMC Article
Rare adrenal gland incidentaloma: an unusual Ewing's sarcoma family of tumor presentation and literature review.
Guo H, Chen S, Liu S, Wang K, Liu E, Li F, Hou Y
BMC Urol 2017 Apr 4;17(1):24. doi: 10.1186/s12894-017-0217-3. PMID: 28376845Free PMC Article

Recent systematic reviews

Bilateral adrenal metastases and metastatic subcutaneous deposit in the chest wall from osteosarcoma of the mandible: utility of 18F-FDG-PET.
Basu S, Shet T, Awasare S
Hell J Nucl Med 2009 Jan-Apr;12(1):51-4. PMID: 19330184
Second primary malignancy risk in thyroid cancer survivors: a systematic review and meta-analysis.
Subramanian S, Goldstein DP, Parlea L, Thabane L, Ezzat S, Ibrahim-Zada I, Straus S, Brierley JD, Tsang RW, Gafni A, Rotstein L, Sawka AM
Thyroid 2007 Dec;17(12):1277-88. doi: 10.1089/thy.2007.0171. PMID: 18020916

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