Pseudounicornuate uterus

MedGen UID:: 1657403
•Concept ID:: C4749300
•: Congenital Abnormality

Synonyms:	Incomplete unilateral aplasia of Mullerian ducts; incomplete unilateral aplasia of the Mullerian ducts; Incomplete unilateral aplasia of the Müllerian ducts; incomplete unilateral aplasia of the Müllerian ducts; Incomplete unilateral Mullerian aplasia; incomplete unilateral Mullerian aplasia; Incomplete unilateral Müllerian aplasia; incomplete unilateral Müllerian aplasia; pseudounicornuate uterus; Unicornuate uterus with rudimentary horn; unicornuate uterus with rudimentary horn
SNOMED CT:	Incomplete unilateral aplasia of Mullerian ducts (770591002); Unicornuate uterus with rudimentary horn (770591002); Incomplete unilateral Mullerian aplasia (770591002); Pseudounicornuate uterus (770591002)

Monarch Initiative:	MONDO:0015833
Orphanet:	ORPHA180079

Definition

A rare non-syndromic uterovaginal malformation with characteristics of a crescent-shaped, small-sized uterus containing a single horn and fallopian tube associated with a rudimentary second horn (which can be solid or contain a cavity with functioning endometrium and be communicating or non-communicating). Urinary tract anomalies are frequently associated. [from SNOMEDCT_US]