U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Unresectable Chordoma

MedGen UID:
1664696
Concept ID:
C4727172
Neoplastic Process

Definition

A chordoma which is not amenable to surgical resection. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUnresectable Chordoma

Professional guidelines

PubMed

Locquet MA, Brahmi M, Blay JY, Dutour A
BMC Cancer 2023 Aug 11;23(1):742. doi: 10.1186/s12885-023-11232-3. PMID: 37563551Free PMC Article
Albarrán V, Villamayor ML, Chamorro J, Rosero DI, Pozas J, San Román M, Calvo JC, Pérez de Aguado P, Moreno J, Guerrero P, González C, García de Quevedo C, Álvarez-Ballesteros P, Vaz MÁ
Int J Mol Sci 2022 Nov 9;23(22) doi: 10.3390/ijms232213784. PMID: 36430263Free PMC Article
Hristov B, Shokek O, Frassica DA
J Natl Compr Canc Netw 2007 Apr;5(4):456-66. doi: 10.6004/jnccn.2007.0040. PMID: 17442236

Recent clinical studies

Etiology

Albarrán V, Villamayor ML, Chamorro J, Rosero DI, Pozas J, San Román M, Calvo JC, Pérez de Aguado P, Moreno J, Guerrero P, González C, García de Quevedo C, Álvarez-Ballesteros P, Vaz MÁ
Int J Mol Sci 2022 Nov 9;23(22) doi: 10.3390/ijms232213784. PMID: 36430263Free PMC Article
Aoki S, Koto M, Ikawa H, Imai R, Tokuhiko O, Shinoto M, Takiyama H, Yamada S, Tsuji H
Head Neck 2022 Oct;44(10):2162-2170. Epub 2022 Jun 23 doi: 10.1002/hed.27127. PMID: 35734902Free PMC Article
Liu Z, Gao S, Zhu L, Wang J, Zhang P, Li P, Zhang F, Yao W
Cancer Med 2021 Nov;10(21):7593-7600. Epub 2021 Sep 26 doi: 10.1002/cam4.4286. PMID: 34564939Free PMC Article
Pennington Z, Ehresman J, Elsamadicy AA, Shin JH, Goodwin CR, Schwab JH, Sciubba DM
Neurosurg Focus 2021 May;50(5):E17. doi: 10.3171/2021.2.FOCUS201059. PMID: 33932924
Liu C, Jia Q, Wei H, Yang X, Liu T, Zhao J, Ling Y, Wang C, Yu H, Li Z, Jiao J, Wu Z, Yang C, Xiao J
Lancet Oncol 2020 Sep;21(9):1244-1252. doi: 10.1016/S1470-2045(20)30466-6. PMID: 32888455

Diagnosis

Banfield W, Ioakeim-Ioannidou M, Goldberg S, Ahmed S, Schwab JH, Cote GM, Choy E, Shin JH, Hornicek FJ, Liebsch NJ, Chen YE, MacDonald SM, DeLaney TF
Radiother Oncol 2022 Jun;171:139-145. Epub 2022 Apr 13 doi: 10.1016/j.radonc.2022.04.007. PMID: 35429502
Miyahara H, Nodomi S, Umeda K, Itasaka S, Waki K, Imai T
J Pediatr Hematol Oncol 2020 Jan;42(1):65-68. doi: 10.1097/MPH.0000000000001318. PMID: 30281526
Whelan JS, Davis LE
J Clin Oncol 2018 Jan 10;36(2):188-193. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.1743. PMID: 29220289
Scimeca PG, James-Herry AG, Black KS, Kahn E, Weinblatt ME
J Pediatr Hematol Oncol 1996 May;18(2):237-40. doi: 10.1097/00043426-199605000-00032. PMID: 8846149
Jackson CG
Am J Otol 1981 Oct;3(2):161-71. PMID: 6272580

Therapy

Albarrán V, Villamayor ML, Chamorro J, Rosero DI, Pozas J, San Román M, Calvo JC, Pérez de Aguado P, Moreno J, Guerrero P, González C, García de Quevedo C, Álvarez-Ballesteros P, Vaz MÁ
Int J Mol Sci 2022 Nov 9;23(22) doi: 10.3390/ijms232213784. PMID: 36430263Free PMC Article
Dong M, Liu R, Zhang Q, Luo H, Wang D, Wang Y, Chen J, Ou Y, Wang X
Radiat Oncol 2022 Oct 25;17(1):172. doi: 10.1186/s13014-022-02089-0. PMID: 36284346Free PMC Article
Aoki S, Koto M, Ikawa H, Imai R, Tokuhiko O, Shinoto M, Takiyama H, Yamada S, Tsuji H
Head Neck 2022 Oct;44(10):2162-2170. Epub 2022 Jun 23 doi: 10.1002/hed.27127. PMID: 35734902Free PMC Article
Beddok A, Saint-Martin C, Mammar H, Feuvret L, Helfre S, Bolle S, Froelich S, Goudjil F, Zefkili S, Amessis M, Peurien D, Cornet S, Dendale R, Alapetite C, Calugaru V
Acta Oncol 2021 Feb;60(2):245-251. Epub 2020 Oct 23 doi: 10.1080/0284186X.2020.1834140. PMID: 33095672
Imai R, Kamada T, Araki N; Working Group for Bone and Soft Tissue Sarcomas
Int J Radiat Oncol Biol Phys 2016 May 1;95(1):322-327. Epub 2016 Feb 8 doi: 10.1016/j.ijrobp.2016.02.012. PMID: 27084649

Prognosis

Aoki S, Koto M, Ikawa H, Imai R, Tokuhiko O, Shinoto M, Takiyama H, Yamada S, Tsuji H
Head Neck 2022 Oct;44(10):2162-2170. Epub 2022 Jun 23 doi: 10.1002/hed.27127. PMID: 35734902Free PMC Article
Shah SR, Kim J, Schiapparelli P, Vazquez-Ramos CA, Martinez-Gutierrez JC, Ruiz-Valls A, Inman K, Shamul JG, Green JJ, Quinones-Hinojosa A
Mol Pharm 2019 Apr 1;16(4):1433-1443. Epub 2019 Mar 11 doi: 10.1021/acs.molpharmaceut.8b00959. PMID: 30803231Free PMC Article
Kabolizadeh P, Chen YL, Liebsch N, Hornicek FJ, Schwab JH, Choy E, Rosenthal DI, Niemierko A, DeLaney TF
Int J Radiat Oncol Biol Phys 2017 Feb 1;97(2):254-262. Epub 2016 Oct 13 doi: 10.1016/j.ijrobp.2016.10.006. PMID: 27986348
Imai R, Kamada T, Araki N; Working Group for Bone and Soft Tissue Sarcomas
Int J Radiat Oncol Biol Phys 2016 May 1;95(1):322-327. Epub 2016 Feb 8 doi: 10.1016/j.ijrobp.2016.02.012. PMID: 27084649
Imai R, Kamada T, Sugahara S, Tsuji H, Tsujii H
Br J Radiol 2011 Dec;84 Spec No 1(Spec Iss 1):S48-54. Epub 2011 Mar 22 doi: 10.1259/bjr/13783281. PMID: 21427182Free PMC Article

Clinical prediction guides

Gordon K, Gulidov I, Koryakin S, Smyk D, Makeenkova T, Gogolin D, Lepilina O, Golovanova O, Semenov A, Dujenko S, Medvedeva K, Mardynsky Y
Radiat Oncol 2021 Dec 20;16(1):238. doi: 10.1186/s13014-021-01961-9. PMID: 34930352Free PMC Article
DeMaria PJ, Bilusic M, Park DM, Heery CR, Donahue RN, Madan RA, Bagheri MH, Strauss J, Shen V, Marté JL, Steinberg SM, Schlom J, Gilbert MR, Gulley JL
Oncologist 2021 May;26(5):e847-e858. Epub 2021 Mar 9 doi: 10.1002/onco.13720. PMID: 33594772Free PMC Article
Beddok A, Saint-Martin C, Mammar H, Feuvret L, Helfre S, Bolle S, Froelich S, Goudjil F, Zefkili S, Amessis M, Peurien D, Cornet S, Dendale R, Alapetite C, Calugaru V
Acta Oncol 2021 Feb;60(2):245-251. Epub 2020 Oct 23 doi: 10.1080/0284186X.2020.1834140. PMID: 33095672
Liu C, Jia Q, Wei H, Yang X, Liu T, Zhao J, Ling Y, Wang C, Yu H, Li Z, Jiao J, Wu Z, Yang C, Xiao J
Lancet Oncol 2020 Sep;21(9):1244-1252. doi: 10.1016/S1470-2045(20)30466-6. PMID: 32888455
Demizu Y, Jin D, Sulaiman NS, Nagano F, Terashima K, Tokumaru S, Akagi T, Fujii O, Daimon T, Sasaki R, Fuwa N, Okimoto T
Int J Radiat Oncol Biol Phys 2017 Jun 1;98(2):367-374. Epub 2017 Feb 22 doi: 10.1016/j.ijrobp.2017.02.030. PMID: 28463156

Recent systematic reviews

Dong M, Liu R, Zhang Q, Luo H, Wang D, Wang Y, Chen J, Ou Y, Wang X
Radiat Oncol 2022 Oct 25;17(1):172. doi: 10.1186/s13014-022-02089-0. PMID: 36284346Free PMC Article
Pennington Z, Ehresman J, Elsamadicy AA, Shin JH, Goodwin CR, Schwab JH, Sciubba DM
Neurosurg Focus 2021 May;50(5):E17. doi: 10.3171/2021.2.FOCUS201059. PMID: 33932924

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...