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Pancreaticobiliary Maljunction

MedGen UID:
1684095
Concept ID:
C5197719
Congenital Abnormality
Synonyms: Anomalous Pancreaticobiliary Ductal Union; Anomalous Pancreaticobiliary Junction; Anomalous Pancreaticobiliary Junctions; Junction, Anomalous Pancreaticobiliary; Maljunction, Pancreaticobiliary; Pancreaticobiliary Junction, Anomalous; Pancreaticobiliary Maljunctions

Definition

A group of anatomical variations in which the COMMON BILE DUCT and MAIN PANCREATIC DUCT are joined outside the duodenal wall often with abnormally long common channel rather than at the SPHINCTER OF ODDI. [from MeSH]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPancreaticobiliary Maljunction

Professional guidelines

PubMed

Kamisawa T, Ando H, Shimada M, Hamada Y, Itoi T, Takayashiki T, Miyazaki M
J Hepatobiliary Pancreat Sci 2014 Feb;21(2):87-92. Epub 2013 Jun 20 doi: 10.1002/jhbp.8. PMID: 23798483
Kamisawa T, Ando H, Suyama M, Shimada M, Morine Y, Shimada H; Working Committee of Clinical Practice Guidelines for Pancreaticobiliary Maljunction; Japanese Study Group on Pancreaticobiliary Maljunction
J Gastroenterol 2012 Jul;47(7):731-59. Epub 2012 Jun 22 doi: 10.1007/s00535-012-0611-2. PMID: 22722902
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929

Recent clinical studies

Etiology

Cazares J, Koga H, Yamataka A
Pediatr Surg Int 2023 Jun 1;39(1):209. doi: 10.1007/s00383-023-05483-1. PMID: 37261604
Ono A, Arizono S, Isoda H, Togashi K
Radiographics 2020 Mar-Apr;40(2):378-392. Epub 2020 Jan 17 doi: 10.1148/rg.2020190108. PMID: 31951513
Kamisawa T, Kuruma S, Chiba K, Tabata T, Koizumi S, Kikuyama M
J Gastroenterol 2017 Feb;52(2):158-163. Epub 2016 Oct 4 doi: 10.1007/s00535-016-1268-z. PMID: 27704265
Le Roy B, Gagnière J, Filaire L, Fontarensky M, Hordonneau C, Buc E
Surg Radiol Anat 2016 Nov;38(9):1053-1060. Epub 2016 Mar 22 doi: 10.1007/s00276-016-1669-y. PMID: 27003810
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929

Diagnosis

Cazares J, Koga H, Yamataka A
Pediatr Surg Int 2023 Jun 1;39(1):209. doi: 10.1007/s00383-023-05483-1. PMID: 37261604
Ono A, Arizono S, Isoda H, Togashi K
Radiographics 2020 Mar-Apr;40(2):378-392. Epub 2020 Jan 17 doi: 10.1148/rg.2020190108. PMID: 31951513
Kamisawa T, Kaneko K, Itoi T, Ando H
Lancet Gastroenterol Hepatol 2017 Aug;2(8):610-618. doi: 10.1016/S2468-1253(17)30002-X. PMID: 28691687
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105

Therapy

Du L, Liu C, Wang X, Mu J, Yang Y
Clin Rheumatol 2023 Mar;42(3):839-847. Epub 2022 Oct 5 doi: 10.1007/s10067-022-06398-3. PMID: 36197648
Han X, Geng J, Zhang XX, Zhao L, Wang J, Guo WL
Surg Today 2023 Mar;53(3):316-321. Epub 2022 Aug 9 doi: 10.1007/s00595-022-02571-y. PMID: 35943628
Jin Z, Bie LK, Tang YP, Ge L, Shen SS, Xu B, Li T, Gong B
Oncotarget 2017 Jul 4;8(27):44860-44869. doi: 10.18632/oncotarget.16228. PMID: 28415772Free PMC Article
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105
Tashiro S, Imaizumi T, Ohkawa H, Okada A, Katoh T, Kawaharada Y, Shimada H, Takamatsu H, Miyake H, Todani T; Committee for Registration of the Japanese Study Group on Pancreaticobiliary Maljunction
J Hepatobiliary Pancreat Surg 2003;10(5):345-51. doi: 10.1007/s00534-002-0741-7. PMID: 14598134

Prognosis

Miyoshi H, Inui K, Katano Y, Tachi Y, Yamamoto S
J Med Ultrason (2001) 2021 Apr;48(2):175-186. Epub 2020 Apr 24 doi: 10.1007/s10396-020-01018-6. PMID: 32333131
Kamisawa T, Ando H, Suyama M, Shimada M, Morine Y, Shimada H; Working Committee of Clinical Practice Guidelines for Pancreaticobiliary Maljunction; Japanese Study Group on Pancreaticobiliary Maljunction
J Gastroenterol 2012 Jul;47(7):731-59. Epub 2012 Jun 22 doi: 10.1007/s00535-012-0611-2. PMID: 22722902
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929
Funabiki T, Matsubara T, Miyakawa S, Ishihara S
Langenbecks Arch Surg 2009 Jan;394(1):159-69. Epub 2008 May 24 doi: 10.1007/s00423-008-0336-0. PMID: 18500533
Kamisawa T, Okamoto A
Digestion 2006;73(4):228-36. Epub 2006 Aug 28 doi: 10.1159/000095424. PMID: 16940726

Clinical prediction guides

Cai TN, Huang SG, Yang Y, Mao HM, Guo WL
Pediatr Surg Int 2023 Mar 24;39(1):158. doi: 10.1007/s00383-023-05441-x. PMID: 36959375
Zhang JY, Deng ZH, Gong B
J Dig Dis 2022 Nov;23(11):651-659. doi: 10.1111/1751-2980.13152. PMID: 36630003
Wang CL, Ding HY, Dai Y, Xie TT, Li YB, Cheng L, Wang B, Tang RH, Nie WX
World J Gastroenterol 2014 Jun 14;20(22):7005-10. doi: 10.3748/wjg.v20.i22.7005. PMID: 24944495Free PMC Article
Deng YL, Cheng NS, Lin YX, Zhou RX, Yang C, Jin YW, Xiong XZ
Hepatobiliary Pancreat Dis Int 2011 Dec;10(6):570-80. doi: 10.1016/s1499-3872(11)60098-2. PMID: 22146619
Funabiki T, Matsubara T, Miyakawa S, Ishihara S
Langenbecks Arch Surg 2009 Jan;394(1):159-69. Epub 2008 May 24 doi: 10.1007/s00423-008-0336-0. PMID: 18500533

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