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Recurrent Rhabdoid Tumor of the Kidney

MedGen UID:
1692137
Concept ID:
C5206778
Neoplastic Process

Definition

The reemergence of a rhabdoid tumor of the kidney after a period of remission. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRecurrent Rhabdoid Tumor of the Kidney

Recent clinical studies

Etiology

Koh KN, Han JW, Choi HS, Kang HJ, Lee JW, Yoo KH, Sung KW, Koo HH, Hong KT, Choi JY, Kang SH, Kim H, Im HJ, Hahn SM, Lyu CJ, Baek HJ, Kook H, Park KM, Yang EJ, Lim YT, Kim S, Lee JW, Chung NG, Cho B, Park M, Park HJ, Park BK, Lee JA, Park JE, Kim SK, Kim JY, Kim HS, Ma Y, Park KD, Park SK, Park ES, Shim YJ, Yoo ES, Ryu KH, Yoo JW, Lim YJ, Yoon HS, Lee MJ, Lee JM, Jeon IS, Jung HL, Chueh HW, Won S; Korean Pediatric Hematology and Oncology Group (KPHOG)
Cancer Res Treat 2023 Jan;55(1):279-290. Epub 2022 Aug 11 doi: 10.4143/crt.2022.073. PMID: 35952715Free PMC Article
Gavens E, Arul GS, Pachl M
Surg Oncol 2020 Dec;35:498-503. Epub 2020 Oct 24 doi: 10.1016/j.suronc.2020.10.009. PMID: 33130442
Melchior P, Dzierma Y, Rübe C, Graf N, Kager L, Dieckmann K, Kroiss S, Hubertus J, Warmann S, Schenk JP, Leuschner I, Nemes K, Meier CM, Vokuhl C, Frühwald M, Furtwängler R
Int J Radiat Oncol Biol Phys 2020 Nov 1;108(3):667-675. Epub 2020 May 11 doi: 10.1016/j.ijrobp.2020.04.046. PMID: 32407933
Cheng H, Yang S, Cai S, Ma X, Qin H, Zhang W, Fu L, Zeng Q, Wen M, Peng X, Wang H
Oncologist 2019 Jul;24(7):e551-e558. Epub 2019 Mar 26 doi: 10.1634/theoncologist.2018-0416. PMID: 30914466Free PMC Article
Sugito K, Uekusa S, Kawashima H, Furuya T, Ohashi K, Inoue M, Ikeda T, Koshinaga T, Tomita R, Mugishima H, Maebayashi T
Int J Clin Oncol 2011 Oct;16(5):482-7. Epub 2011 Apr 1 doi: 10.1007/s10147-011-0210-x. PMID: 21455626

Diagnosis

Vejmelkova K, Pokorna P, Noskova K, Faustmannova A, Drabova K, Pavelka Z, Bajciova V, Broz M, Tinka P, Jezova M, Palova H, Kren L, Valik D, Slaby O, Sterba J
Sci Rep 2023 Dec 7;13(1):21623. doi: 10.1038/s41598-023-48774-2. PMID: 38062114Free PMC Article
Cheng H, Yang S, Cai S, Ma X, Qin H, Zhang W, Fu L, Zeng Q, Wen M, Peng X, Wang H
Oncologist 2019 Jul;24(7):e551-e558. Epub 2019 Mar 26 doi: 10.1634/theoncologist.2018-0416. PMID: 30914466Free PMC Article
Wegert J, Vokuhl C, Collord G, Del Castillo Velasco-Herrera M, Farndon SJ, Guzzo C, Jorgensen M, Anderson J, Slater O, Duncan C, Bausenwein S, Streitenberger H, Ziegler B, Furtwängler R, Graf N, Stratton MR, Campbell PJ, Jones DT, Koelsche C, Pfister SM, Mifsud W, Sebire N, Sparber-Sauer M, Koscielniak E, Rosenwald A, Gessler M, Behjati S
Nat Commun 2018 Jun 18;9(1):2378. doi: 10.1038/s41467-018-04650-6. PMID: 29915264Free PMC Article
Uwineza A, Gill H, Buckley P, Owens C, Capra M, O'Sullivan C, McDermott M, Brett F, Farrell M, Pears J, O'Sullivan MJ
Cancer Genet 2014 Sep;207(9):398-402. Epub 2014 Jun 11 doi: 10.1016/j.cancergen.2014.05.015. PMID: 25085603
Shamberger RC
Semin Surg Oncol 1999 Mar;16(2):105-20. doi: 10.1002/(sici)1098-2388(199903)16:2<105::aid-ssu4>3.0.co;2-t. PMID: 9988867

Therapy

Gavens E, Arul GS, Pachl M
Surg Oncol 2020 Dec;35:498-503. Epub 2020 Oct 24 doi: 10.1016/j.suronc.2020.10.009. PMID: 33130442
Kato M, Koh K, Oshima K, Oguma E, Uchida H, Kishimoto H, Kikuchi A, Hanada R
Pediatr Int 2013 Apr;55(2):245-8. doi: 10.1111/j.1442-200X.2012.03663.x. PMID: 23679167
Sugito K, Uekusa S, Kawashima H, Furuya T, Ohashi K, Inoue M, Ikeda T, Koshinaga T, Tomita R, Mugishima H, Maebayashi T
Int J Clin Oncol 2011 Oct;16(5):482-7. Epub 2011 Apr 1 doi: 10.1007/s10147-011-0210-x. PMID: 21455626
Bourdeaut F, Fréneaux P, Thuille B, Bergeron C, Laurence V, Brugières L, Vérité C, Michon J, Delattre O, Orbach D
Pediatr Blood Cancer 2008 Sep;51(3):363-8. doi: 10.1002/pbc.21632. PMID: 18506766
Boyer MW, Moertel CL, Priest JR, Woods WG
J Clin Oncol 1995 Mar;13(3):631-6. doi: 10.1200/JCO.1995.13.3.631. PMID: 7884424

Prognosis

Vejmelkova K, Pokorna P, Noskova K, Faustmannova A, Drabova K, Pavelka Z, Bajciova V, Broz M, Tinka P, Jezova M, Palova H, Kren L, Valik D, Slaby O, Sterba J
Sci Rep 2023 Dec 7;13(1):21623. doi: 10.1038/s41598-023-48774-2. PMID: 38062114Free PMC Article
Cheng H, Yang S, Cai S, Ma X, Qin H, Zhang W, Fu L, Zeng Q, Wen M, Peng X, Wang H
Oncologist 2019 Jul;24(7):e551-e558. Epub 2019 Mar 26 doi: 10.1634/theoncologist.2018-0416. PMID: 30914466Free PMC Article
Uwineza A, Gill H, Buckley P, Owens C, Capra M, O'Sullivan C, McDermott M, Brett F, Farrell M, Pears J, O'Sullivan MJ
Cancer Genet 2014 Sep;207(9):398-402. Epub 2014 Jun 11 doi: 10.1016/j.cancergen.2014.05.015. PMID: 25085603
Cobb AR, Sebire NJ, Anderson J, Dunaway D
J Craniomaxillofac Surg 2012 Dec;40(8):e258-60. Epub 2011 Nov 12 doi: 10.1016/j.jcms.2011.10.031. PMID: 22079123
Shamberger RC
Semin Surg Oncol 1999 Mar;16(2):105-20. doi: 10.1002/(sici)1098-2388(199903)16:2<105::aid-ssu4>3.0.co;2-t. PMID: 9988867

Clinical prediction guides

Grundy PE, Breslow NE, Li S, Perlman E, Beckwith JB, Ritchey ML, Shamberger RC, Haase GM, D'Angio GJ, Donaldson M, Coppes MJ, Malogolowkin M, Shearer P, Thomas PR, Macklis R, Tomlinson G, Huff V, Green DM; National Wilms Tumor Study Group
J Clin Oncol 2005 Oct 10;23(29):7312-21. Epub 2005 Aug 29 doi: 10.1200/JCO.2005.01.2799. PMID: 16129848
Takamizawa S, Scott D, Wen J, Grundy P, Bishop W, Kimura K, Sandler A
J Pediatr Surg 2001 Jan;36(1):37-42. doi: 10.1053/jpsu.2001.20000. PMID: 11150435
Versteege I, Sévenet N, Lange J, Rousseau-Merck MF, Ambros P, Handgretinger R, Aurias A, Delattre O
Nature 1998 Jul 9;394(6689):203-6. doi: 10.1038/28212. PMID: 9671307

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