U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Metastatic Clear Cell Sarcoma of Soft Tissue

MedGen UID:
1695380
Concept ID:
C5205915
Neoplastic Process

Definition

A clear cell sarcoma of soft tissue that has spread from the original site of growth to other anatomic sites. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMetastatic Clear Cell Sarcoma of Soft Tissue

Professional guidelines

PubMed

Datta NK, Das KP, Aish PK, Datta M, Banik SK, Sen SK, Chowdhury RM
Mymensingh Med J 2023 Jan;32(1):135-143. PMID: 36594313
Suárez C, Díaz-Mejía N, Morales-Barrera R, González M, Mateo J, Carles J
Curr Opin Urol 2021 May 1;31(3):242-248. doi: 10.1097/MOU.0000000000000869. PMID: 33742977
Cornillie J, van Cann T, Wozniak A, Hompes D, Schöffski P
Expert Rev Anticancer Ther 2016 Aug;16(8):839-45. Epub 2016 Jun 20 doi: 10.1080/14737140.2016.1197122. PMID: 27253849

Recent clinical studies

Etiology

Datta NK, Das KP, Aish PK, Datta M, Banik SK, Sen SK, Chowdhury RM
Mymensingh Med J 2023 Jan;32(1):135-143. PMID: 36594313
Evangelou Z, Linos K
J Cutan Pathol 2022 Aug;49(8):747-759. Epub 2022 May 20 doi: 10.1111/cup.14232. PMID: 35338512
Suárez C, Díaz-Mejía N, Morales-Barrera R, González M, Mateo J, Carles J
Curr Opin Urol 2021 May 1;31(3):242-248. doi: 10.1097/MOU.0000000000000869. PMID: 33742977
Dirksen U, Brennan B, Le Deley MC, Cozic N, van den Berg H, Bhadri V, Brichard B, Claude L, Craft A, Amler S, Gaspar N, Gelderblom H, Goldsby R, Gorlick R, Grier HE, Guinbretiere JM, Hauser P, Hjorth L, Janeway K, Juergens H, Judson I, Krailo M, Kruseova J, Kuehne T, Ladenstein R, Lervat C, Lessnick SL, Lewis I, Linassier C, Marec-Berard P, Marina N, Morland B, Pacquement H, Paulussen M, Randall RL, Ranft A, Le Teuff G, Wheatley K, Whelan J, Womer R, Oberlin O, Hawkins DS; Euro-E.W.I.N.G. 99 and Ewing 2008 Investigators
J Clin Oncol 2019 Dec 1;37(34):3192-3202. Epub 2019 Sep 25 doi: 10.1200/JCO.19.00915. PMID: 31553693Free PMC Article
de Fijter JW
Transplantation 2017 Jan;101(1):45-55. doi: 10.1097/TP.0000000000001447. PMID: 27547865

Diagnosis

Agaimy A
Semin Diagn Pathol 2023 Jul;40(4):306-312. Epub 2023 Jun 23 doi: 10.1053/j.semdp.2023.06.001. PMID: 37438163
Kaczorowski M, Chłopek M, Kruczak A, Ryś J, Lasota J, Miettinen M
Am J Surg Pathol 2022 Nov 1;46(11):1467-1476. Epub 2022 Aug 16 doi: 10.1097/PAS.0000000000001944. PMID: 35973038Free PMC Article
Dirksen U, Brennan B, Le Deley MC, Cozic N, van den Berg H, Bhadri V, Brichard B, Claude L, Craft A, Amler S, Gaspar N, Gelderblom H, Goldsby R, Gorlick R, Grier HE, Guinbretiere JM, Hauser P, Hjorth L, Janeway K, Juergens H, Judson I, Krailo M, Kruseova J, Kuehne T, Ladenstein R, Lervat C, Lessnick SL, Lewis I, Linassier C, Marec-Berard P, Marina N, Morland B, Pacquement H, Paulussen M, Randall RL, Ranft A, Le Teuff G, Wheatley K, Whelan J, Womer R, Oberlin O, Hawkins DS; Euro-E.W.I.N.G. 99 and Ewing 2008 Investigators
J Clin Oncol 2019 Dec 1;37(34):3192-3202. Epub 2019 Sep 25 doi: 10.1200/JCO.19.00915. PMID: 31553693Free PMC Article
Matias-Guiu X, Stewart CJR
Pathology 2018 Feb;50(2):190-204. Epub 2017 Dec 11 doi: 10.1016/j.pathol.2017.10.006. PMID: 29241974
Mercado-Asis LB, Wolf KI, Jochmanova I, Taïeb D
Endocr Pract 2018 Jan;24(1):78-90. Epub 2017 Nov 16 doi: 10.4158/EP-2017-0057. PMID: 29144820

Therapy

Suárez C, Díaz-Mejía N, Morales-Barrera R, González M, Mateo J, Carles J
Curr Opin Urol 2021 May 1;31(3):242-248. doi: 10.1097/MOU.0000000000000869. PMID: 33742977
Dirksen U, Brennan B, Le Deley MC, Cozic N, van den Berg H, Bhadri V, Brichard B, Claude L, Craft A, Amler S, Gaspar N, Gelderblom H, Goldsby R, Gorlick R, Grier HE, Guinbretiere JM, Hauser P, Hjorth L, Janeway K, Juergens H, Judson I, Krailo M, Kruseova J, Kuehne T, Ladenstein R, Lervat C, Lessnick SL, Lewis I, Linassier C, Marec-Berard P, Marina N, Morland B, Pacquement H, Paulussen M, Randall RL, Ranft A, Le Teuff G, Wheatley K, Whelan J, Womer R, Oberlin O, Hawkins DS; Euro-E.W.I.N.G. 99 and Ewing 2008 Investigators
J Clin Oncol 2019 Dec 1;37(34):3192-3202. Epub 2019 Sep 25 doi: 10.1200/JCO.19.00915. PMID: 31553693Free PMC Article
de Fijter JW
Transplantation 2017 Jan;101(1):45-55. doi: 10.1097/TP.0000000000001447. PMID: 27547865
Cornillie J, van Cann T, Wozniak A, Hompes D, Schöffski P
Expert Rev Anticancer Ther 2016 Aug;16(8):839-45. Epub 2016 Jun 20 doi: 10.1080/14737140.2016.1197122. PMID: 27253849
Hyman DM, Puzanov I, Subbiah V, Faris JE, Chau I, Blay JY, Wolf J, Raje NS, Diamond EL, Hollebecque A, Gervais R, Elez-Fernandez ME, Italiano A, Hofheinz RD, Hidalgo M, Chan E, Schuler M, Lasserre SF, Makrutzki M, Sirzen F, Veronese ML, Tabernero J, Baselga J
N Engl J Med 2015 Aug 20;373(8):726-36. doi: 10.1056/NEJMoa1502309. PMID: 26287849Free PMC Article

Prognosis

Huang X, Liao X
N Engl J Med 2020 Jul 23;383(4):379. doi: 10.1056/NEJMicm1913435. PMID: 32706536
Dirksen U, Brennan B, Le Deley MC, Cozic N, van den Berg H, Bhadri V, Brichard B, Claude L, Craft A, Amler S, Gaspar N, Gelderblom H, Goldsby R, Gorlick R, Grier HE, Guinbretiere JM, Hauser P, Hjorth L, Janeway K, Juergens H, Judson I, Krailo M, Kruseova J, Kuehne T, Ladenstein R, Lervat C, Lessnick SL, Lewis I, Linassier C, Marec-Berard P, Marina N, Morland B, Pacquement H, Paulussen M, Randall RL, Ranft A, Le Teuff G, Wheatley K, Whelan J, Womer R, Oberlin O, Hawkins DS; Euro-E.W.I.N.G. 99 and Ewing 2008 Investigators
J Clin Oncol 2019 Dec 1;37(34):3192-3202. Epub 2019 Sep 25 doi: 10.1200/JCO.19.00915. PMID: 31553693Free PMC Article
Matias-Guiu X, Stewart CJR
Pathology 2018 Feb;50(2):190-204. Epub 2017 Dec 11 doi: 10.1016/j.pathol.2017.10.006. PMID: 29241974
Cornillie J, van Cann T, Wozniak A, Hompes D, Schöffski P
Expert Rev Anticancer Ther 2016 Aug;16(8):839-45. Epub 2016 Jun 20 doi: 10.1080/14737140.2016.1197122. PMID: 27253849
Gooskens SL, Furtwängler R, Vujanic GM, Dome JS, Graf N, van den Heuvel-Eibrink MM
Eur J Cancer 2012 Sep;48(14):2219-26. Epub 2012 May 12 doi: 10.1016/j.ejca.2012.04.009. PMID: 22579455

Clinical prediction guides

Adane B, Alexe G, Seong BKA, Lu D, Hwang EE, Hnisz D, Lareau CA, Ross L, Lin S, Dela Cruz FS, Richardson M, Weintraub AS, Wang S, Iniguez AB, Dharia NV, Conway AS, Robichaud AL, Tanenbaum B, Krill-Burger JM, Vazquez F, Schenone M, Berman JN, Kung AL, Carr SA, Aryee MJ, Young RA, Crompton BD, Stegmaier K
Cancer Cell 2021 Jun 14;39(6):827-844.e10. doi: 10.1016/j.ccell.2021.05.007. PMID: 34129824Free PMC Article
Dirksen U, Brennan B, Le Deley MC, Cozic N, van den Berg H, Bhadri V, Brichard B, Claude L, Craft A, Amler S, Gaspar N, Gelderblom H, Goldsby R, Gorlick R, Grier HE, Guinbretiere JM, Hauser P, Hjorth L, Janeway K, Juergens H, Judson I, Krailo M, Kruseova J, Kuehne T, Ladenstein R, Lervat C, Lessnick SL, Lewis I, Linassier C, Marec-Berard P, Marina N, Morland B, Pacquement H, Paulussen M, Randall RL, Ranft A, Le Teuff G, Wheatley K, Whelan J, Womer R, Oberlin O, Hawkins DS; Euro-E.W.I.N.G. 99 and Ewing 2008 Investigators
J Clin Oncol 2019 Dec 1;37(34):3192-3202. Epub 2019 Sep 25 doi: 10.1200/JCO.19.00915. PMID: 31553693Free PMC Article
Matias-Guiu X, Stewart CJR
Pathology 2018 Feb;50(2):190-204. Epub 2017 Dec 11 doi: 10.1016/j.pathol.2017.10.006. PMID: 29241974
Hyman DM, Puzanov I, Subbiah V, Faris JE, Chau I, Blay JY, Wolf J, Raje NS, Diamond EL, Hollebecque A, Gervais R, Elez-Fernandez ME, Italiano A, Hofheinz RD, Hidalgo M, Chan E, Schuler M, Lasserre SF, Makrutzki M, Sirzen F, Veronese ML, Tabernero J, Baselga J
N Engl J Med 2015 Aug 20;373(8):726-36. doi: 10.1056/NEJMoa1502309. PMID: 26287849Free PMC Article
Gooskens SL, Furtwängler R, Vujanic GM, Dome JS, Graf N, van den Heuvel-Eibrink MM
Eur J Cancer 2012 Sep;48(14):2219-26. Epub 2012 May 12 doi: 10.1016/j.ejca.2012.04.009. PMID: 22579455

Recent systematic reviews

Chan DLH, Segelov E, Wong RS, Smith A, Herbertson RA, Li BT, Tebbutt N, Price T, Pavlakis N
Cochrane Database Syst Rev 2017 Jun 27;6(6):CD007047. doi: 10.1002/14651858.CD007047.pub2. PMID: 28654140Free PMC Article
Peinemann F, Labeit AM
BMJ Open 2014 Jul 29;4(7):e005033. doi: 10.1136/bmjopen-2014-005033. PMID: 25079925Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...