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Advanced Papillary Renal Cell Carcinoma

MedGen UID:
1704723
Concept ID:
C5206804
Neoplastic Process

Definition

A papillary renal cell carcinoma that has spread extensively to other anatomic sites or is no longer responding to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced Papillary Renal Cell Carcinoma

Professional guidelines

PubMed

Staehler M, Goebell PJ, Müller L, Emde TO, Wetzel N, Kruggel L, Jänicke M, Marschner N; RCC-Registry Group (Tumour Registry of Advanced Renal Cell Carcinoma)
Int J Cancer 2020 Mar 1;146(5):1307-1315. Epub 2019 Nov 22 doi: 10.1002/ijc.32671. PMID: 31498894Free PMC Article

Recent clinical studies

Etiology

Sweeney PL, Jang A, Halat SK, Pal SK, Barata PC
Cancer Treat Res Commun 2022;33:100639. Epub 2022 Sep 22 doi: 10.1016/j.ctarc.2022.100639. PMID: 36162322
Pal SK, Tangen C, Thompson IM Jr, Balzer-Haas N, George DJ, Heng DYC, Shuch B, Stein M, Tretiakova M, Humphrey P, Adeniran A, Narayan V, Bjarnason GA, Vaishampayan U, Alva A, Zhang T, Cole S, Plets M, Wright J, Lara PN Jr
Lancet 2021 Feb 20;397(10275):695-703. Epub 2021 Feb 13 doi: 10.1016/S0140-6736(21)00152-5. PMID: 33592176Free PMC Article
Staehler M, Goebell PJ, Müller L, Emde TO, Wetzel N, Kruggel L, Jänicke M, Marschner N; RCC-Registry Group (Tumour Registry of Advanced Renal Cell Carcinoma)
Int J Cancer 2020 Mar 1;146(5):1307-1315. Epub 2019 Nov 22 doi: 10.1002/ijc.32671. PMID: 31498894Free PMC Article
Schöffski P, Wozniak A, Escudier B, Rutkowski P, Anthoney A, Bauer S, Sufliarsky J, van Herpen C, Lindner LH, Grünwald V, Zakotnik B, Lerut E, Debiec-Rychter M, Marréaud S, Lia M, Raveloarivahy T, Collette S, Albiges L
Eur J Cancer 2017 Dec;87:147-163. Epub 2017 Nov 14 doi: 10.1016/j.ejca.2017.10.014. PMID: 29149761

Diagnosis

Angori S, Banaei-Esfahani A, Mühlbauer K, Bolck HA, Kahraman A, Karakulak T, Poyet C, Feodoroff M, Potdar S, Kallioniemi O, Pietiäinen V, Schraml P, Moch H
Eur Urol Focus 2023 Sep;9(5):751-759. Epub 2023 Mar 16 doi: 10.1016/j.euf.2023.03.005. PMID: 36933996
Pal SK, Ali SM, Yakirevich E, Geynisman DM, Karam JA, Elvin JA, Frampton GM, Huang X, Lin DI, Rosenzweig M, Lipson D, Stephens PJ, Ross JS, Miller VA, Agarwal N, Shuch B, Choueiri TK, Chung JH
Eur Urol 2018 Jan;73(1):71-78. Epub 2017 Jun 4 doi: 10.1016/j.eururo.2017.05.033. PMID: 28592388

Therapy

Pahwa R, Dubhashi J, Singh A, Jailwala P, Lobanov A, Thomas CJ, Ceribelli M, Wilson K, Ricketts CJ, Vocke CD, Wells C, Bottaro DP, Linehan WM, Neckers L, Srinivasan R
J Exp Clin Cancer Res 2022 Jun 27;41(1):208. doi: 10.1186/s13046-022-02416-z. PMID: 35754026Free PMC Article
Pal SK, Tangen C, Thompson IM Jr, Balzer-Haas N, George DJ, Heng DYC, Shuch B, Stein M, Tretiakova M, Humphrey P, Adeniran A, Narayan V, Bjarnason GA, Vaishampayan U, Alva A, Zhang T, Cole S, Plets M, Wright J, Lara PN Jr
Lancet 2021 Feb 20;397(10275):695-703. Epub 2021 Feb 13 doi: 10.1016/S0140-6736(21)00152-5. PMID: 33592176Free PMC Article
Staehler M, Goebell PJ, Müller L, Emde TO, Wetzel N, Kruggel L, Jänicke M, Marschner N; RCC-Registry Group (Tumour Registry of Advanced Renal Cell Carcinoma)
Int J Cancer 2020 Mar 1;146(5):1307-1315. Epub 2019 Nov 22 doi: 10.1002/ijc.32671. PMID: 31498894Free PMC Article
Schöffski P, Wozniak A, Escudier B, Rutkowski P, Anthoney A, Bauer S, Sufliarsky J, van Herpen C, Lindner LH, Grünwald V, Zakotnik B, Lerut E, Debiec-Rychter M, Marréaud S, Lia M, Raveloarivahy T, Collette S, Albiges L
Eur J Cancer 2017 Dec;87:147-163. Epub 2017 Nov 14 doi: 10.1016/j.ejca.2017.10.014. PMID: 29149761
Choueiri TK, Plimack E, Arkenau HT, Jonasch E, Heng DYC, Powles T, Frigault MM, Clark EA, Handzel AA, Gardner H, Morgan S, Albiges L, Pal SK
J Clin Oncol 2017 Sep 10;35(26):2993-3001. Epub 2017 Jun 23 doi: 10.1200/JCO.2017.72.2967. PMID: 28644771

Prognosis

Sweeney PL, Jang A, Halat SK, Pal SK, Barata PC
Cancer Treat Res Commun 2022;33:100639. Epub 2022 Sep 22 doi: 10.1016/j.ctarc.2022.100639. PMID: 36162322
Pahwa R, Dubhashi J, Singh A, Jailwala P, Lobanov A, Thomas CJ, Ceribelli M, Wilson K, Ricketts CJ, Vocke CD, Wells C, Bottaro DP, Linehan WM, Neckers L, Srinivasan R
J Exp Clin Cancer Res 2022 Jun 27;41(1):208. doi: 10.1186/s13046-022-02416-z. PMID: 35754026Free PMC Article
Staehler M, Goebell PJ, Müller L, Emde TO, Wetzel N, Kruggel L, Jänicke M, Marschner N; RCC-Registry Group (Tumour Registry of Advanced Renal Cell Carcinoma)
Int J Cancer 2020 Mar 1;146(5):1307-1315. Epub 2019 Nov 22 doi: 10.1002/ijc.32671. PMID: 31498894Free PMC Article
Pal SK, Ali SM, Yakirevich E, Geynisman DM, Karam JA, Elvin JA, Frampton GM, Huang X, Lin DI, Rosenzweig M, Lipson D, Stephens PJ, Ross JS, Miller VA, Agarwal N, Shuch B, Choueiri TK, Chung JH
Eur Urol 2018 Jan;73(1):71-78. Epub 2017 Jun 4 doi: 10.1016/j.eururo.2017.05.033. PMID: 28592388
Choueiri TK, Plimack E, Arkenau HT, Jonasch E, Heng DYC, Powles T, Frigault MM, Clark EA, Handzel AA, Gardner H, Morgan S, Albiges L, Pal SK
J Clin Oncol 2017 Sep 10;35(26):2993-3001. Epub 2017 Jun 23 doi: 10.1200/JCO.2017.72.2967. PMID: 28644771

Clinical prediction guides

Angori S, Banaei-Esfahani A, Mühlbauer K, Bolck HA, Kahraman A, Karakulak T, Poyet C, Feodoroff M, Potdar S, Kallioniemi O, Pietiäinen V, Schraml P, Moch H
Eur Urol Focus 2023 Sep;9(5):751-759. Epub 2023 Mar 16 doi: 10.1016/j.euf.2023.03.005. PMID: 36933996
Staehler M, Goebell PJ, Müller L, Emde TO, Wetzel N, Kruggel L, Jänicke M, Marschner N; RCC-Registry Group (Tumour Registry of Advanced Renal Cell Carcinoma)
Int J Cancer 2020 Mar 1;146(5):1307-1315. Epub 2019 Nov 22 doi: 10.1002/ijc.32671. PMID: 31498894Free PMC Article
Pal SK, Ali SM, Yakirevich E, Geynisman DM, Karam JA, Elvin JA, Frampton GM, Huang X, Lin DI, Rosenzweig M, Lipson D, Stephens PJ, Ross JS, Miller VA, Agarwal N, Shuch B, Choueiri TK, Chung JH
Eur Urol 2018 Jan;73(1):71-78. Epub 2017 Jun 4 doi: 10.1016/j.eururo.2017.05.033. PMID: 28592388
Choueiri TK, Plimack E, Arkenau HT, Jonasch E, Heng DYC, Powles T, Frigault MM, Clark EA, Handzel AA, Gardner H, Morgan S, Albiges L, Pal SK
J Clin Oncol 2017 Sep 10;35(26):2993-3001. Epub 2017 Jun 23 doi: 10.1200/JCO.2017.72.2967. PMID: 28644771

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