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Cutaneous Rosai-Dorfman Disease

MedGen UID:
1712213
•Concept ID:
C5239290
•
Disease or Syndrome
Synonym: Cutaneous Sinus Histiocytosis With Massive Lymphadenopathy

Definition

Rosai-Dorfman disease affecting the skin. It manifests with multiple papules, nodules, or plaques. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCutaneous Rosai-Dorfman Disease

Professional guidelines

PubMed

Treatment of purely cutaneous ​Rosai-Dorfman disease with topical rapamycin.
Balestri R, Magnano M, Pedrolli A, Girardelli CR, Rech G
Clin Exp Dermatol 2023 Apr 27;48(5):545-547. doi: 10.1093/ced/llad018. PMID: 36647561

Recent clinical studies

Etiology

The evaluation of IgG4 and IgG expression in cutaneous Rosai-Dorfman disease.
Zou P, Zhan Y, Xue R, Liu Y, Zhang G
An Bras Dermatol 2023 Sep-Oct;98(5):651-655. Epub 2023 Jun 8 doi: 10.1016/j.abd.2022.07.010. PMID: 37301673Free PMC Article
Rosai-Dorfman disease: an overview.
Bruce-Brand C, Schneider JW, Schubert P
J Clin Pathol 2020 Nov;73(11):697-705. Epub 2020 Jun 26 doi: 10.1136/jclinpath-2020-206733. PMID: 32591351
Cutaneous Rosai-Dorfman disease.
Gaul M, Chang T
Cutis 2019 Mar;103(3):171-173. PMID: 31039225
Cutaneous Rosai-Dorfman Disease of the Face: A Comprehensive Literature Review and Case Report.
Al-Khateeb TH
J Oral Maxillofac Surg 2016 Mar;74(3):528-40. Epub 2015 Sep 25 doi: 10.1016/j.joms.2015.09.017. PMID: 26455470
Cutaneous Rosai-Dorfman disease.
Merola JF, Pulitzer M, Rosenman K, Brownell I
Dermatol Online J 2008 May 15;14(5):8. PMID: 18627744

Diagnosis

A comprehensive assessment of cutaneous Rosai-Dorfman disease.
Ahmed A, Crowson N, Magro CM
Ann Diagn Pathol 2019 Jun;40:166-173. Epub 2019 Feb 25 doi: 10.1016/j.anndiagpath.2019.02.004. PMID: 31108464
Cutaneous Rosai-Dorfman disease.
Gaul M, Chang T
Cutis 2019 Mar;103(3):171-173. PMID: 31039225
Cutaneous Rosai-Dorfman Disease.
Keeling BH, Thelin LL, Gavino AC, Ahmed AM
Skinmed 2017;15(4):301-302. Epub 2017 Aug 1 PMID: 28859745
Cutaneous Rosai-Dorfman disease.
DE Pasquale R, Longo V, Pavone A, Scuderi L
G Ital Dermatol Venereol 2016 Jun;151(3):302-6. Epub 2015 Mar 27 PMID: 25812620
Cutaneous Rosai-Dorfman disease.
Landim FM, Rios Hde O, Costa CO, Feitosa RG, Rocha Filho FD, Costa AA
An Bras Dermatol 2009 Jul;84(3):275-8. doi: 10.1590/s0365-05962009000300010. PMID: 19668942

Therapy

Cutaneous Rosai-Dorfman disease: a challenging diagnosis.
Sampaio R, Silva L, Catorze G, Viana I
BMJ Case Rep 2021 Feb 4;14(2) doi: 10.1136/bcr-2020-239244. PMID: 33541998Free PMC Article
Cutaneous Rosai - Dorfman disease in a patient with late syphilis and cervical cancer - case report and a review of literature.
Bielach-Bazyluk A, Serwin AB, Pilaszewicz-Puza A, Flisiak I
BMC Dermatol 2020 Dec 7;20(1):19. doi: 10.1186/s12895-020-00115-w. PMID: 33287799Free PMC Article
Primary cutaneous Rosai-Dorfman disease; a case-based review of a diagnostically and therapeutically challenging rare variant.
Fayne R, Rengifo SS, Gonzalez I, Solorzano JL, Gonzalez D, Vega F, Cho-Vega JH
Ann Diagn Pathol 2020 Apr;45:151446. Epub 2019 Dec 17 doi: 10.1016/j.anndiagpath.2019.151446. PMID: 31978810
Cutaneous Rosai-Dorfman disease.
Gaul M, Chang T
Cutis 2019 Mar;103(3):171-173. PMID: 31039225
Facial Cutaneous Rosai-Dorfman Disease.
Flores-Terry MÁ, Romero-Aguilera G, González-López L, García-Arpa M
Actas Dermosifiliogr 2017 Jun;108(5):480-482. Epub 2017 Jan 18 doi: 10.1016/j.ad.2016.10.018. PMID: 28109522

Prognosis

A comprehensive assessment of cutaneous Rosai-Dorfman disease.
Ahmed A, Crowson N, Magro CM
Ann Diagn Pathol 2019 Jun;40:166-173. Epub 2019 Feb 25 doi: 10.1016/j.anndiagpath.2019.02.004. PMID: 31108464
Cutaneous Rosai-Dorfman Disease of the Face: A Comprehensive Literature Review and Case Report.
Al-Khateeb TH
J Oral Maxillofac Surg 2016 Mar;74(3):528-40. Epub 2015 Sep 25 doi: 10.1016/j.joms.2015.09.017. PMID: 26455470
Cutaneous Rosai-Dorfman disease.
Merola JF, Pulitzer M, Rosenman K, Brownell I
Dermatol Online J 2008 May 15;14(5):8. PMID: 18627744
Cutaneous rosai-dorfman disease: a clinical and histopathologic study of 25 cases in China.
Kong YY, Kong JC, Shi DR, Lu HF, Zhu XZ, Wang J, Chen ZW
Am J Surg Pathol 2007 Mar;31(3):341-50. doi: 10.1097/01.pas.0000213387.70783.b6. PMID: 17325475
Cutaneous Rosai-Dorfman disease.
Rubenstein MA, Farnsworth NN, Pielop JA, Orengo IF, Curry JL, Drucker CR, Hsu S
Dermatol Online J 2006 Jan 27;12(1):8. PMID: 16638376

Clinical prediction guides

Dermoscopy combined with reflectance confocal microscopy as a noninvasive involvement for monitoring Cutaneous Rosai-Dorfman: A case report.
Xu H, Wen L, Hu C, Li J, Wang P, Wang X
Photodiagnosis Photodyn Ther 2023 Dec;44:103874. Epub 2023 Nov 7 doi: 10.1016/j.pdpdt.2023.103874. PMID: 37939892
Possible association of cutaneous Rosai-Dorfman disease and chronic Crohn disease: a case series report.
Salva KA, Stenstrom M, Breadon JY, Odland PB, Bennett D, Longley J, Wood GS
JAMA Dermatol 2014 Feb;150(2):177-81. doi: 10.1001/jamadermatol.2013.7609. PMID: 24305684Free PMC Article
Cutaneous Rosai-Dorfman disease with increased number of eosinophils: coincidence or histologic variant?
Cangelosi JJ, Prieto VG, Ivan D
Arch Pathol Lab Med 2011 Dec;135(12):1597-600. doi: 10.5858/arpa.2010-0554-CR. PMID: 22129191
Cutaneous rosai-dorfman disease: a clinical and histopathologic study of 25 cases in China.
Kong YY, Kong JC, Shi DR, Lu HF, Zhu XZ, Wang J, Chen ZW
Am J Surg Pathol 2007 Mar;31(3):341-50. doi: 10.1097/01.pas.0000213387.70783.b6. PMID: 17325475
Purely cutaneous Rosai--Dorfman disease.
Annessi G, Giannetti A
Br J Dermatol 1996 Apr;134(4):749-53. PMID: 8733385

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