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Status epilepticus with prominent motor symptoms

MedGen UID:
1720011
Concept ID:
C5397675
Disease or Syndrome
HPO: HP:0032658

Definition

Status epilepticus with prominent motor signs during the prolonged seizure. [from HPO]

Professional guidelines

PubMed

Gardella E, Møller RS
Epilepsia 2019 Dec;60 Suppl 3:S77-S85. doi: 10.1111/epi.16319. PMID: 31904124

Recent clinical studies

Etiology

Orav K, Bosque Varela P, Prüwasser T, Machegger L, Leitinger M, Trinka E, Kuchukhidze G
Epileptic Disord 2023 Dec;25(6):823-832. Epub 2023 Oct 10 doi: 10.1002/epd2.20164. PMID: 37776308Free PMC Article
Perez DQ, Espiritu AI, Jamora RDG
Epilepsy Behav 2022 Mar;128:108583. Epub 2022 Feb 9 doi: 10.1016/j.yebeh.2022.108583. PMID: 35151187
Othman AS, El-Tamawy MS, Amer H, Kishk NA, Nawito AM, Shaker E, Basheer MA, Alieldin N, Magdy R
Acta Neurol Scand 2021 Oct;144(4):375-382. Epub 2021 May 27 doi: 10.1111/ane.13478. PMID: 34042176
Bergin PS, Brockington A, Jayabal J, Scott S, Litchfield R, Roberts L, Timog J, Beilharz E, Dalziel SR, Jones P, Yates K, Thornton V, Walker EB, Davis S, Te Ao B, Parmar P, Beghi E, Rossetti AO, Feigin V
Epilepsia 2019 Aug;60(8):1552-1564. Epub 2019 Jul 1 doi: 10.1111/epi.16277. PMID: 31260104
Trinka E, Cock H, Hesdorffer D, Rossetti AO, Scheffer IE, Shinnar S, Shorvon S, Lowenstein DH
Epilepsia 2015 Oct;56(10):1515-23. Epub 2015 Sep 4 doi: 10.1111/epi.13121. PMID: 26336950

Diagnosis

Orav K, Bosque Varela P, Prüwasser T, Machegger L, Leitinger M, Trinka E, Kuchukhidze G
Epileptic Disord 2023 Dec;25(6):823-832. Epub 2023 Oct 10 doi: 10.1002/epd2.20164. PMID: 37776308Free PMC Article
Perez DQ, Espiritu AI, Jamora RDG
Epilepsy Behav 2022 Mar;128:108583. Epub 2022 Feb 9 doi: 10.1016/j.yebeh.2022.108583. PMID: 35151187
Volle DC, Marder KG, McKeon A, Brooks JO, Kruse JL
Gen Hosp Psychiatry 2021 Jan-Feb;68:25-34. Epub 2020 Nov 13 doi: 10.1016/j.genhosppsych.2020.11.008. PMID: 33276270Free PMC Article
Trinka E, Cock H, Hesdorffer D, Rossetti AO, Scheffer IE, Shinnar S, Shorvon S, Lowenstein DH
Epilepsia 2015 Oct;56(10):1515-23. Epub 2015 Sep 4 doi: 10.1111/epi.13121. PMID: 26336950
Inoue Y, Fujiwara T, Matsuda K, Kubota H, Tanaka M, Yagi K, Yamamori K, Takahashi Y
Brain 1997 Jun;120 ( Pt 6):939-53. doi: 10.1093/brain/120.6.939. PMID: 9217679

Therapy

Perez DQ, Espiritu AI, Jamora RDG
Epilepsy Behav 2022 Mar;128:108583. Epub 2022 Feb 9 doi: 10.1016/j.yebeh.2022.108583. PMID: 35151187
Llauradó A, Quintana M, Ballvé A, Campos D, Fonseca E, Abraira L, Toledo M, Santamarina E
J Neurol Sci 2021 Apr 15;423:117368. Epub 2021 Feb 23 doi: 10.1016/j.jns.2021.117368. PMID: 33652289
Orlandi N, Bartolini E, Audenino D, Coletti Moja M, Urso L, d'Orsi G, Pauletto G, Nilo A, Zinno L, Cappellani R, Zummo L, Giordano A, Dainese F, Nazerian P, Pescini F, Beretta S, Dono F, Gaudio LD, Ferlisi M, Marino D, Piccioli M, Renna R, Rosati E, Rum A, Strigaro G, Giovannini G, Meletti S; Collaborators, Cavalli SM, Contento M, Cottone S, Di Claudio MT, Florindo I, Guadagni M, Kiferle L, Lazzaretti D, Lazzari M, Coco DL, Pradella S, Rikani K, Rodorigo D, Sabetta A, Sicurella L, Tontini V, Turchi G, Vaudano AE, Zanoni T
Seizure 2021 Mar;86:70-76. Epub 2021 Jan 30 doi: 10.1016/j.seizure.2021.01.014. PMID: 33561784
Santamarina E, Parejo Carbonell B, Sala J, Gutiérrez-Viedma Á, Miró J, Asensio M, Abraira L, Falip M, Ojeda J, López-González FJ, Rodríguez-Osorio X, Mauri JÁ, Aiguabella M, García Morales I, Toledo M
Epilepsia 2019 Aug;60(8):1593-1601. Epub 2019 Jul 1 doi: 10.1111/epi.16094. PMID: 31260101
Kobayashi K, Murakami N, Yoshinaga H, Enoki H, Ohtsuka Y, Ohtahara S
Jpn J Psychiatry Neurol 1988 Sep;42(3):509-14. doi: 10.1111/j.1440-1819.1988.tb01344.x. PMID: 3241476

Prognosis

Orav K, Bosque Varela P, Prüwasser T, Machegger L, Leitinger M, Trinka E, Kuchukhidze G
Epileptic Disord 2023 Dec;25(6):823-832. Epub 2023 Oct 10 doi: 10.1002/epd2.20164. PMID: 37776308Free PMC Article
Llauradó A, Quintana M, Ballvé A, Campos D, Fonseca E, Abraira L, Toledo M, Santamarina E
J Neurol Sci 2021 Apr 15;423:117368. Epub 2021 Feb 23 doi: 10.1016/j.jns.2021.117368. PMID: 33652289
Bergin PS, Brockington A, Jayabal J, Scott S, Litchfield R, Roberts L, Timog J, Beilharz E, Dalziel SR, Jones P, Yates K, Thornton V, Walker EB, Davis S, Te Ao B, Parmar P, Beghi E, Rossetti AO, Feigin V
Epilepsia 2019 Aug;60(8):1552-1564. Epub 2019 Jul 1 doi: 10.1111/epi.16277. PMID: 31260104
Leitinger M, Trinka E, Giovannini G, Zimmermann G, Florea C, Rohracher A, Kalss G, Neuray C, Kreidenhuber R, Höfler J, Kuchukhidze G, Granbichler C, Dobesberger J, Novak HF, Pilz G, Meletti S, Siebert U
Epilepsia 2019 Jan;60(1):53-62. Epub 2018 Nov 26 doi: 10.1111/epi.14607. PMID: 30478910Free PMC Article
Santamarina E, Abraira L, Toledo M, González-Cuevas M, Quintana M, Maisterra O, Sueiras M, Guzman L, Salas-Puig J, Sabín JÁ
Seizure 2018 Aug;60:172-177. Epub 2018 Jul 9 doi: 10.1016/j.seizure.2018.07.006. PMID: 30015150

Clinical prediction guides

Orav K, Bosque Varela P, Prüwasser T, Machegger L, Leitinger M, Trinka E, Kuchukhidze G
Epileptic Disord 2023 Dec;25(6):823-832. Epub 2023 Oct 10 doi: 10.1002/epd2.20164. PMID: 37776308Free PMC Article
Aslan-Kara K, Demir T, Satılmış Ü, Peköz T, Bıçakcı Ş, Bozdemir H
Acta Neurol Belg 2023 Aug;123(4):1257-1266. Epub 2022 Jun 3 doi: 10.1007/s13760-022-01981-6. PMID: 35657480
Jiao X, Xue Y, Yang S, Gong P, Niu Y, Wang Q, Yang H, Xiong H, Zhang Y, Yang Z
Dev Med Child Neurol 2022 Jan;64(1):125-134. Epub 2021 Jul 18 doi: 10.1111/dmcn.14976. PMID: 34275143
Othman AS, El-Tamawy MS, Amer H, Kishk NA, Nawito AM, Shaker E, Basheer MA, Alieldin N, Magdy R
Acta Neurol Scand 2021 Oct;144(4):375-382. Epub 2021 May 27 doi: 10.1111/ane.13478. PMID: 34042176
Llauradó A, Quintana M, Ballvé A, Campos D, Fonseca E, Abraira L, Toledo M, Santamarina E
J Neurol Sci 2021 Apr 15;423:117368. Epub 2021 Feb 23 doi: 10.1016/j.jns.2021.117368. PMID: 33652289

Recent systematic reviews

Licchetta L, Ferri L, Morsillo F, Faustini-Fustini M, Toni F, Pondrelli F, Nonino F, Bisulli F, Tinuper P
Seizure 2023 Mar;106:50-57. Epub 2023 Jan 27 doi: 10.1016/j.seizure.2023.01.018. PMID: 36773573
Perez DQ, Espiritu AI, Jamora RDG
Epilepsy Behav 2022 Mar;128:108583. Epub 2022 Feb 9 doi: 10.1016/j.yebeh.2022.108583. PMID: 35151187
Volle DC, Marder KG, McKeon A, Brooks JO, Kruse JL
Gen Hosp Psychiatry 2021 Jan-Feb;68:25-34. Epub 2020 Nov 13 doi: 10.1016/j.genhosppsych.2020.11.008. PMID: 33276270Free PMC Article

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