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Epithelioid Malignant Peripheral Nerve Sheath Tumor of the Skin

MedGen UID:
1727912
Concept ID:
C5419748
Neoplastic Process
Synonyms: Cutaneous Epithelioid Malignant Peripheral Nerve Sheath Tumor; Dermal Epithelioid Malignant Peripheral Nerve Sheath Tumor; Skin Epithelioid Malignant Peripheral Nerve Sheath Tumor

Definition

An epithelioid malignant peripheral nerve sheath tumor that arises from the skin. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEpithelioid Malignant Peripheral Nerve Sheath Tumor of the Skin

Professional guidelines

PubMed

Hart J, Mandavilli S
Arch Pathol Lab Med 2011 Feb;135(2):268-72. doi: 10.5858/135.2.268. PMID: 21284449

Recent clinical studies

Etiology

Czaja R, Layng KV, Barrett A, Hooper P, Alomari A, Warren S
J Cutan Pathol 2023 Apr;50(4):343-348. Epub 2022 Nov 23 doi: 10.1111/cup.14355. PMID: 36335562
Röhrich M, Koelsche C, Schrimpf D, Capper D, Sahm F, Kratz A, Reuss J, Hovestadt V, Jones DT, Bewerunge-Hudler M, Becker A, Weis J, Mawrin C, Mittelbronn M, Perry A, Mautner VF, Mechtersheimer G, Hartmann C, Okuducu AF, Arp M, Seiz-Rosenhagen M, Hänggi D, Heim S, Paulus W, Schittenhelm J, Ahmadi R, Herold-Mende C, Unterberg A, Pfister SM, von Deimling A, Reuss DE
Acta Neuropathol 2016 Jun;131(6):877-87. Epub 2016 Feb 8 doi: 10.1007/s00401-016-1540-6. PMID: 26857854
Hart J, Gardner JM, Edgar M, Weiss SW
Am J Surg Pathol 2016 May;40(5):704-13. doi: 10.1097/PAS.0000000000000589. PMID: 26752543
Luzar B, Shanesmith R, Ramakrishnan R, Fisher C, Calonje E
Histopathology 2016 Jan;68(2):286-96. Epub 2015 Jul 28 doi: 10.1111/his.12756. PMID: 26096054
Fanburg-Smith JC, Miettinen M
Hum Pathol 2001 Sep;32(9):976-83. doi: 10.1053/hupa.2001.27602. PMID: 11567228

Diagnosis

Acharya AM, Bhat AK, Pai G M, Bansal E
BMJ Case Rep 2023 Nov 24;16(11) doi: 10.1136/bcr-2023-256900. PMID: 38000811Free PMC Article
Bai M, Govindaraj V, Chauhan AS, Srinivas BH, Sree Rekha J, Narenchandra V
Monaldi Arch Chest Dis 2021 May 6;91(2) doi: 10.4081/monaldi.2021.1658. PMID: 34256542
Diaz-Perez JA, Spasic S, Velez-Torres JM, McCarthy EF, Rosenberg AE
Am J Clin Pathol 2021 Apr 26;155(5):729-737. doi: 10.1093/ajcp/aqaa180. PMID: 33247294
Luzar B, Falconieri G
Surg Pathol Clin 2017 Jun;10(2):337-343. Epub 2017 Mar 14 doi: 10.1016/j.path.2017.01.008. PMID: 28477884
Hart J, Mandavilli S
Arch Pathol Lab Med 2011 Feb;135(2):268-72. doi: 10.5858/135.2.268. PMID: 21284449

Prognosis

Acharya AM, Bhat AK, Pai G M, Bansal E
BMJ Case Rep 2023 Nov 24;16(11) doi: 10.1136/bcr-2023-256900. PMID: 38000811Free PMC Article
Carter CS, Patel RM
Mod Pathol 2020 Jan;33(Suppl 1):66-82. Epub 2019 Nov 4 doi: 10.1038/s41379-019-0387-5. PMID: 31685962
Iannaci G, Crispino M, Cifarelli P, Montella M, Panarese I, Ronchi A, Russo R, Tremiterra G, Luise R, Sapere P
World J Surg Oncol 2016 Feb 3;14(1):29. doi: 10.1186/s12957-016-0789-5. PMID: 26842370Free PMC Article
Luzar B, Shanesmith R, Ramakrishnan R, Fisher C, Calonje E
Histopathology 2016 Jan;68(2):286-96. Epub 2015 Jul 28 doi: 10.1111/his.12756. PMID: 26096054
Karaki S, Mochida J, Lee YH, Nishimura K, Tsutsumi Y
Pathol Int 1999 Sep;49(9):820-5. doi: 10.1046/j.1440-1827.1999.00948.x. PMID: 10504555

Clinical prediction guides

Carter CS, Patel RM
Mod Pathol 2020 Jan;33(Suppl 1):66-82. Epub 2019 Nov 4 doi: 10.1038/s41379-019-0387-5. PMID: 31685962
Luzar B, Shanesmith R, Ramakrishnan R, Fisher C, Calonje E
Histopathology 2016 Jan;68(2):286-96. Epub 2015 Jul 28 doi: 10.1111/his.12756. PMID: 26096054

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