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Recurrent Acute Promyelocytic Leukemia with PML-RARA

MedGen UID:
1741304
Concept ID:
C5418301
Neoplastic Process
Synonym: Recurrent Acute Promyelocytic Leukemia with PML::RARA

Definition

The reemergence of acute promyelocytic leukemia with PML-RARA after a period of remission. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRecurrent Acute Promyelocytic Leukemia with PML-RARA

Professional guidelines

PubMed

Yanada M
Ann Hematol 2022 Dec;101(12):2575-2582. Epub 2022 Aug 16 doi: 10.1007/s00277-022-04954-0. PMID: 35972562
Sanz MA, Fenaux P, Tallman MS, Estey EH, Löwenberg B, Naoe T, Lengfelder E, Döhner H, Burnett AK, Chen SJ, Mathews V, Iland H, Rego E, Kantarjian H, Adès L, Avvisati G, Montesinos P, Platzbecker U, Ravandi F, Russell NH, Lo-Coco F
Blood 2019 Apr 11;133(15):1630-1643. Epub 2019 Feb 25 doi: 10.1182/blood-2019-01-894980. PMID: 30803991Free PMC Article
Sanz MA, Grimwade D, Tallman MS, Lowenberg B, Fenaux P, Estey EH, Naoe T, Lengfelder E, Büchner T, Döhner H, Burnett AK, Lo-Coco F
Blood 2009 Feb 26;113(9):1875-91. Epub 2008 Sep 23 doi: 10.1182/blood-2008-04-150250. PMID: 18812465

Recent clinical studies

Etiology

Stahl M, Tallman MS
Leuk Lymphoma 2019 Dec;60(13):3107-3115. Epub 2019 Dec 16 doi: 10.1080/10428194.2019.1613540. PMID: 31842650Free PMC Article
Sanz MA, Fenaux P, Tallman MS, Estey EH, Löwenberg B, Naoe T, Lengfelder E, Döhner H, Burnett AK, Chen SJ, Mathews V, Iland H, Rego E, Kantarjian H, Adès L, Avvisati G, Montesinos P, Platzbecker U, Ravandi F, Russell NH, Lo-Coco F
Blood 2019 Apr 11;133(15):1630-1643. Epub 2019 Feb 25 doi: 10.1182/blood-2019-01-894980. PMID: 30803991Free PMC Article
Kayser S, Levis MJ
Eur J Haematol 2019 Jan;102(1):20-35. Epub 2018 Oct 23 doi: 10.1111/ejh.13172. PMID: 30203623Free PMC Article
Kayser S, Schlenk RF, Platzbecker U
Leukemia 2018 Jun;32(6):1277-1294. Epub 2018 Apr 24 doi: 10.1038/s41375-018-0139-4. PMID: 29743722
Sanz MA, Grimwade D, Tallman MS, Lowenberg B, Fenaux P, Estey EH, Naoe T, Lengfelder E, Büchner T, Döhner H, Burnett AK, Lo-Coco F
Blood 2009 Feb 26;113(9):1875-91. Epub 2008 Sep 23 doi: 10.1182/blood-2008-04-150250. PMID: 18812465

Diagnosis

Sanz MA, Fenaux P, Tallman MS, Estey EH, Löwenberg B, Naoe T, Lengfelder E, Döhner H, Burnett AK, Chen SJ, Mathews V, Iland H, Rego E, Kantarjian H, Adès L, Avvisati G, Montesinos P, Platzbecker U, Ravandi F, Russell NH, Lo-Coco F
Blood 2019 Apr 11;133(15):1630-1643. Epub 2019 Feb 25 doi: 10.1182/blood-2019-01-894980. PMID: 30803991Free PMC Article
Kayser S, Levis MJ
Eur J Haematol 2019 Jan;102(1):20-35. Epub 2018 Oct 23 doi: 10.1111/ejh.13172. PMID: 30203623Free PMC Article
Kayser S, Schlenk RF, Platzbecker U
Leukemia 2018 Jun;32(6):1277-1294. Epub 2018 Apr 24 doi: 10.1038/s41375-018-0139-4. PMID: 29743722
Grimwade D, Ivey A, Huntly BJ
Blood 2016 Jan 7;127(1):29-41. Epub 2015 Dec 10 doi: 10.1182/blood-2015-07-604496. PMID: 26660431Free PMC Article
Sanz MA, Grimwade D, Tallman MS, Lowenberg B, Fenaux P, Estey EH, Naoe T, Lengfelder E, Büchner T, Döhner H, Burnett AK, Lo-Coco F
Blood 2009 Feb 26;113(9):1875-91. Epub 2008 Sep 23 doi: 10.1182/blood-2008-04-150250. PMID: 18812465

Therapy

Stahl M, Tallman MS
Leuk Lymphoma 2019 Dec;60(13):3107-3115. Epub 2019 Dec 16 doi: 10.1080/10428194.2019.1613540. PMID: 31842650Free PMC Article
Sanz MA, Fenaux P, Tallman MS, Estey EH, Löwenberg B, Naoe T, Lengfelder E, Döhner H, Burnett AK, Chen SJ, Mathews V, Iland H, Rego E, Kantarjian H, Adès L, Avvisati G, Montesinos P, Platzbecker U, Ravandi F, Russell NH, Lo-Coco F
Blood 2019 Apr 11;133(15):1630-1643. Epub 2019 Feb 25 doi: 10.1182/blood-2019-01-894980. PMID: 30803991Free PMC Article
Grimwade D, Ivey A, Huntly BJ
Blood 2016 Jan 7;127(1):29-41. Epub 2015 Dec 10 doi: 10.1182/blood-2015-07-604496. PMID: 26660431Free PMC Article
Welch JS, Ley TJ, Link DC, Miller CA, Larson DE, Koboldt DC, Wartman LD, Lamprecht TL, Liu F, Xia J, Kandoth C, Fulton RS, McLellan MD, Dooling DJ, Wallis JW, Chen K, Harris CC, Schmidt HK, Kalicki-Veizer JM, Lu C, Zhang Q, Lin L, O'Laughlin MD, McMichael JF, Delehaunty KD, Fulton LA, Magrini VJ, McGrath SD, Demeter RT, Vickery TL, Hundal J, Cook LL, Swift GW, Reed JP, Alldredge PA, Wylie TN, Walker JR, Watson MA, Heath SE, Shannon WD, Varghese N, Nagarajan R, Payton JE, Baty JD, Kulkarni S, Klco JM, Tomasson MH, Westervelt P, Walter MJ, Graubert TA, DiPersio JF, Ding L, Mardis ER, Wilson RK
Cell 2012 Jul 20;150(2):264-78. doi: 10.1016/j.cell.2012.06.023. PMID: 22817890Free PMC Article
Sanz MA, Grimwade D, Tallman MS, Lowenberg B, Fenaux P, Estey EH, Naoe T, Lengfelder E, Büchner T, Döhner H, Burnett AK, Lo-Coco F
Blood 2009 Feb 26;113(9):1875-91. Epub 2008 Sep 23 doi: 10.1182/blood-2008-04-150250. PMID: 18812465

Prognosis

Yilmaz M, Kadia T, Ravandi F
Expert Rev Anticancer Ther 2020 Jul;20(7):591-601. Epub 2020 Jun 30 doi: 10.1080/14737140.2020.1782749. PMID: 32552126
Xiao H, Liang S, Wang L
Clin Chim Acta 2020 Oct;509:108-116. Epub 2020 May 29 doi: 10.1016/j.cca.2020.05.045. PMID: 32479763
Stahl M, Tallman MS
Leuk Lymphoma 2019 Dec;60(13):3107-3115. Epub 2019 Dec 16 doi: 10.1080/10428194.2019.1613540. PMID: 31842650Free PMC Article
Kayser S, Levis MJ
Eur J Haematol 2019 Jan;102(1):20-35. Epub 2018 Oct 23 doi: 10.1111/ejh.13172. PMID: 30203623Free PMC Article
Grimwade D, Ivey A, Huntly BJ
Blood 2016 Jan 7;127(1):29-41. Epub 2015 Dec 10 doi: 10.1182/blood-2015-07-604496. PMID: 26660431Free PMC Article

Clinical prediction guides

Xiao H, Liang S, Wang L
Clin Chim Acta 2020 Oct;509:108-116. Epub 2020 May 29 doi: 10.1016/j.cca.2020.05.045. PMID: 32479763
Chen S, Li X, Ma S, Xing X, Wang X, Zhu Z
Ann Hematol 2020 Apr;99(4):753-763. Epub 2020 Feb 4 doi: 10.1007/s00277-019-03888-4. PMID: 32016577
Osumi T, Tsujimoto SI, Tamura M, Uchiyama M, Nakabayashi K, Okamura K, Yoshida M, Tomizawa D, Watanabe A, Takahashi H, Hori T, Yamamoto S, Hamamoto K, Migita M, Ogata-Kawata H, Uchiyama T, Kizawa H, Ueno-Yokohata H, Shirai R, Seki M, Ohki K, Takita J, Inukai T, Ogawa S, Kitamura T, Matsumoto K, Hata K, Kiyokawa N, Goyama S, Kato M
Cancer Res 2018 Aug 15;78(16):4452-4458. Epub 2018 Jun 19 doi: 10.1158/0008-5472.CAN-18-0840. PMID: 29921692
Grimwade D, Ivey A, Huntly BJ
Blood 2016 Jan 7;127(1):29-41. Epub 2015 Dec 10 doi: 10.1182/blood-2015-07-604496. PMID: 26660431Free PMC Article
Cripe LD
Curr Probl Cancer 1997 Jan-Feb;21(1):1-64. doi: 10.1016/s0147-0272(97)80006-2. PMID: 9058027

Recent systematic reviews

Ahrari A, Al-Ani F, Wang YP, Lazo-Langner A
Thromb Res 2019 Jun;178:1-6. Epub 2019 Mar 20 doi: 10.1016/j.thromres.2019.03.014. PMID: 30921533
Küley-Bagheri Y, Kreuzer KA, Monsef I, Lübbert M, Skoetz N
Cochrane Database Syst Rev 2018 Aug 6;8(8):CD011960. doi: 10.1002/14651858.CD011960.pub2. PMID: 30080246Free PMC Article

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