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Sinonasal Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

MedGen UID:
1748578
•Concept ID:
C5420081
•
Neoplastic Process

Definition

Ewing sarcoma/peripheral primitive neuroectodermal tumor arising from the nasal cavity and paranasal sinuses. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSinonasal Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

Professional guidelines

PubMed

Adamantinoma-like Ewing family tumors of the head and neck: a pitfall in the differential diagnosis of basaloid and myoepithelial carcinomas.
Bishop JA, Alaggio R, Zhang L, Seethala RR, Antonescu CR
Am J Surg Pathol 2015 Sep;39(9):1267-74. doi: 10.1097/PAS.0000000000000460. PMID: 26034869Free PMC Article
"Undifferentiated" small round cell tumors of the sinonasal tract: differential diagnosis update.
Iezzoni JC, Mills SE
Am J Clin Pathol 2005 Dec;124 Suppl:S110-21. doi: 10.1309/59RBT2RK6LQE4YHB. PMID: 16468421

Recent clinical studies

Etiology

Neuroectodermal tumours of the sino-nasal tract: a clinicopathological study of 18 cases with a newly proposed revised classification and a brief review of literature.
Stephen N, Srinivas BH, Ravi S, Ganesh RN, Badhe BA, Toi P, Jinkala S, Sekar R, Alexander A, Narendhar, Pandjatcharam J
Eur Arch Otorhinolaryngol 2022 Mar;279(3):1181-1191. Epub 2021 Sep 27 doi: 10.1007/s00405-021-07051-6. PMID: 34568968
Sinonasal primitive neuroectodermal tumor arising in a long-term survivor of heritable unilateral retinoblastoma.
Klein EA, Anzil AP, Mezzacappa P, Borderon M, Ho V
Cancer 1992 Jul 15;70(2):423-31. doi: 10.1002/1097-0142(19920715)70:2<423::aid-cncr2820700209>3.0.co;2-b. PMID: 1319815

Diagnosis

Adamantinoma-like Ewing Sarcoma (ALES) May Harbor FUS Rearrangements : A Potential Diagnostic Pitfall.
Palsgrove DN, Foss RD, Yu W, Garcia J, Rooper LM, Rekhtman N, Antonescu C, Gagan J, Agaimy A, Bishop JA
Am J Surg Pathol 2023 Nov 1;47(11):1243-1251. Epub 2023 Jul 27 doi: 10.1097/PAS.0000000000002100. PMID: 37494548
Neuroectodermal tumours of the sino-nasal tract: a clinicopathological study of 18 cases with a newly proposed revised classification and a brief review of literature.
Stephen N, Srinivas BH, Ravi S, Ganesh RN, Badhe BA, Toi P, Jinkala S, Sekar R, Alexander A, Narendhar, Pandjatcharam J
Eur Arch Otorhinolaryngol 2022 Mar;279(3):1181-1191. Epub 2021 Sep 27 doi: 10.1007/s00405-021-07051-6. PMID: 34568968
Sinonasal small round blue cell tumors: An approach to diagnosis.
Simons SA, Bridge JA, Leon ME
Semin Diagn Pathol 2016 Mar;33(2):91-103. Epub 2015 Sep 10 doi: 10.1053/j.semdp.2015.09.010. PMID: 26585346
Adamantinoma-like Ewing family tumors of the head and neck: a pitfall in the differential diagnosis of basaloid and myoepithelial carcinomas.
Bishop JA, Alaggio R, Zhang L, Seethala RR, Antonescu CR
Am J Surg Pathol 2015 Sep;39(9):1267-74. doi: 10.1097/PAS.0000000000000460. PMID: 26034869Free PMC Article
"Undifferentiated" small round cell tumors of the sinonasal tract: differential diagnosis update.
Iezzoni JC, Mills SE
Am J Clin Pathol 2005 Dec;124 Suppl:S110-21. doi: 10.1309/59RBT2RK6LQE4YHB. PMID: 16468421

Prognosis

Neuroectodermal tumours of the sino-nasal tract: a clinicopathological study of 18 cases with a newly proposed revised classification and a brief review of literature.
Stephen N, Srinivas BH, Ravi S, Ganesh RN, Badhe BA, Toi P, Jinkala S, Sekar R, Alexander A, Narendhar, Pandjatcharam J
Eur Arch Otorhinolaryngol 2022 Mar;279(3):1181-1191. Epub 2021 Sep 27 doi: 10.1007/s00405-021-07051-6. PMID: 34568968
Sinonasal small round blue cell tumors: An approach to diagnosis.
Simons SA, Bridge JA, Leon ME
Semin Diagn Pathol 2016 Mar;33(2):91-103. Epub 2015 Sep 10 doi: 10.1053/j.semdp.2015.09.010. PMID: 26585346
Adamantinoma-like Ewing family tumors of the head and neck: a pitfall in the differential diagnosis of basaloid and myoepithelial carcinomas.
Bishop JA, Alaggio R, Zhang L, Seethala RR, Antonescu CR
Am J Surg Pathol 2015 Sep;39(9):1267-74. doi: 10.1097/PAS.0000000000000460. PMID: 26034869Free PMC Article

Clinical prediction guides

Sinonasal small round blue cell tumors: An approach to diagnosis.
Simons SA, Bridge JA, Leon ME
Semin Diagn Pathol 2016 Mar;33(2):91-103. Epub 2015 Sep 10 doi: 10.1053/j.semdp.2015.09.010. PMID: 26585346
Adamantinoma-like Ewing family tumors of the head and neck: a pitfall in the differential diagnosis of basaloid and myoepithelial carcinomas.
Bishop JA, Alaggio R, Zhang L, Seethala RR, Antonescu CR
Am J Surg Pathol 2015 Sep;39(9):1267-74. doi: 10.1097/PAS.0000000000000460. PMID: 26034869Free PMC Article

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