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Congenital obstruction of ureteral orifice

MedGen UID:
1779994
•Concept ID:
C5441666
•
Congenital Abnormality
Synonyms: Congenital Ureterovesical Junction Obstruction; Congenital ureterovesical obstruction; Congenital vesicoureteric obstruction
SNOMED CT: Congenital ureterovesical obstruction (373585009); Congenital vesicoureteric obstruction (373585009); Congenital obstruction of ureteral orifice (373585009)

Definition

Complete or partial blockage of the ureter at the point where it enters the bladder that is present at birth. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital obstruction of ureteral orifice

Professional guidelines

PubMed

Endoureterotomy for congenital primary obstructive megaureter: preliminary report.
Bapat S, Bapat M, Kirpekar D
J Endourol 2000 Apr;14(3):263-7. doi: 10.1089/end.2000.14.263. PMID: 10795616
Non-obstructive vesicoureteral reflux in adults: value of conservative treatment.
Senoh K, Iwatsubo E, Momose S, Goto M, Kodama H
J Urol 1977 May;117(5):566-70. doi: 10.1016/s0022-5347(17)58536-5. PMID: 870706

Recent clinical studies

Etiology

Retrospective study to determine the short-term outcomes of a modified pneumovesical Glenn-Anderson procedure for treating primary obstructing megaureter.
Liu X, Liu JH, Zhang DY, Hua Y, Lin T, Wei GH, He DW
J Pediatr Urol 2015 Oct;11(5):266.e1-6. Epub 2015 Jun 4 doi: 10.1016/j.jpurol.2015.03.020. PMID: 26076822
Wrap plication of megaureter around normal-sized ureter for complete duplex system reimplantations.
van den Heijkant MM, Dik P, Klijn AJ, Chrzan R, Kuijper CF, de Jong TP
J Urol 2013 Jan;189(1):295-9. Epub 2012 Nov 20 doi: 10.1016/j.juro.2012.09.004. PMID: 23174243
Congenital mid ureteral strictures.
Hwang AH, McAleer IM, Shapiro E, Miller OF, Krous HF, Kaplan GW
J Urol 2005 Nov;174(5):1999-2002. doi: 10.1097/01.ju.0000176462.56473.0c. PMID: 16217377
Congenital megaureter in adults: endoscopic management with holmium: YAG laser--preliminary experience.
Biyani CS, Powell CS
J Endourol 2001 Oct;15(8):797-9. doi: 10.1089/089277901753205771. PMID: 11724117
Endoureterotomy for congenital primary obstructive megaureter: preliminary report.
Bapat S, Bapat M, Kirpekar D
J Endourol 2000 Apr;14(3):263-7. doi: 10.1089/end.2000.14.263. PMID: 10795616

Diagnosis

Vaginoscopic Management of OHVIRA (Obstructive Hemivagina and Ipsilateral Renal Agenesis).
Paul PG, Sudhakar M, Shah M, Chowdary VS, Paul G
J Minim Invasive Gynecol 2023 May;30(5):361-362. Epub 2023 Feb 11 doi: 10.1016/j.jmig.2023.02.007. PMID: 36775054
Hutch diverticulum: from embryology to clinical practice.
Gkalonaki I, Anastasakis M, Panteli C, Patoulias I
Folia Med Cracov 2022 Dec 29;62(4):57-62. doi: 10.24425/fmc.2022.144083. PMID: 36854087
Modified ureteral orthotopic reimplantation method for managing infant primary obstructive megaureter: a preliminary study.
Liu W, Du G, Guo F, Ma R, Wu R
Int Urol Nephrol 2016 Dec;48(12):1937-1941. Epub 2016 Sep 2 doi: 10.1007/s11255-016-1409-6. PMID: 27590133
An unusual presentation of bilateral Hutch diverticula.
Fanning DM, Morrin M, Power R
BMJ Case Rep 2014 May 23;2014 doi: 10.1136/bcr-2014-204398. PMID: 24859560Free PMC Article
Congenital mid ureteral strictures.
Hwang AH, McAleer IM, Shapiro E, Miller OF, Krous HF, Kaplan GW
J Urol 2005 Nov;174(5):1999-2002. doi: 10.1097/01.ju.0000176462.56473.0c. PMID: 16217377

Therapy

Modified ureteral orthotopic reimplantation method for managing infant primary obstructive megaureter: a preliminary study.
Liu W, Du G, Guo F, Ma R, Wu R
Int Urol Nephrol 2016 Dec;48(12):1937-1941. Epub 2016 Sep 2 doi: 10.1007/s11255-016-1409-6. PMID: 27590133

Prognosis

Retrospective study to determine the short-term outcomes of a modified pneumovesical Glenn-Anderson procedure for treating primary obstructing megaureter.
Liu X, Liu JH, Zhang DY, Hua Y, Lin T, Wei GH, He DW
J Pediatr Urol 2015 Oct;11(5):266.e1-6. Epub 2015 Jun 4 doi: 10.1016/j.jpurol.2015.03.020. PMID: 26076822
Congenital mid ureteral strictures.
Hwang AH, McAleer IM, Shapiro E, Miller OF, Krous HF, Kaplan GW
J Urol 2005 Nov;174(5):1999-2002. doi: 10.1097/01.ju.0000176462.56473.0c. PMID: 16217377
Congenital megaureter in adults: endoscopic management with holmium: YAG laser--preliminary experience.
Biyani CS, Powell CS
J Endourol 2001 Oct;15(8):797-9. doi: 10.1089/089277901753205771. PMID: 11724117

Clinical prediction guides

Mayer-Rokitansky-Küster-Hauser syndrome with rare findings of inferior crossed-fused renal ectopia and Gartner's duct cyst: a video case report.
Liang G, Xia W, Liang Y, Zhu Q, Zou L, Zhang J, Jiang H
Fertil Steril 2021 Feb;115(2):525-527. Epub 2020 Oct 14 doi: 10.1016/j.fertnstert.2020.08.1433. PMID: 33069370

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