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Lung Rhabdomyosarcoma

MedGen UID:
1789550
Concept ID:
C2200351
Neoplastic Process
Synonym: Pulmonary Rhabdomyosarcoma

Definition

A rare rhabdomyosarcoma that arises from the lung. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLung Rhabdomyosarcoma

Professional guidelines

PubMed

Martin-Giacalone BA, Li H, Scheurer ME, Casey DL, Dugan-Perez S, Marquez-Do DA, Muzny D, Gibbs RA, Barkauskas DA, Hall D, Stewart DR, Schiffman JD, McEvoy MT, Khan J, Malkin D, Linardic CM, Crompton BD, Shern JF, Skapek SX, Venkatramani R, Hawkins DS, Sabo A, Plon SE, Lupo PJ
JAMA Netw Open 2024 Mar 4;7(3):e244170. doi: 10.1001/jamanetworkopen.2024.4170. PMID: 38546643Free PMC Article
Ahmeti H, Jüttner E, Röcken C, Jansen O, Laudes M, Synowitz M
J Neurol Surg A Cent Eur Neurosurg 2023 May;84(3):295-299. Epub 2021 Nov 15 doi: 10.1055/s-0041-1735857. PMID: 34781400
Barbolosi D, Ciccolini J, Meille C, Elharrar X, Faivre C, Lacarelle B, André N, Barlesi F
Cancer Chemother Pharmacol 2014 Sep;74(3):647-52. Epub 2014 Aug 1 doi: 10.1007/s00280-014-2546-1. PMID: 25082520

Recent clinical studies

Etiology

Strausz S, Ruotsalainen S, Ollila HM, Karjalainen J, Kiiskinen T, Reeve M, Kurki M, Mars N, Havulinna AS, Luonsi E, Mansour Aly D, Ahlqvist E, Teder-Laving M, Palta P, Groop L, Mägi R, Mäkitie A, Salomaa V, Bachour A, Tuomi T; FinnGen, Palotie A, Palotie T, Ripatti S
Eur Respir J 2021 May;57(5) Epub 2021 May 6 doi: 10.1183/13993003.03091-2020. PMID: 33243845
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Dobrenkov K, Cheung NK
Semin Oncol 2014 Oct;41(5):589-612. Epub 2014 Jul 21 doi: 10.1053/j.seminoncol.2014.07.003. PMID: 25440605Free PMC Article
Katoh M, Katoh M
Int J Oncol 2004 Nov;25(5):1495-500. PMID: 15492844
Gladish GW, Sabloff BM, Munden RF, Truong MT, Erasmus JJ, Chasen MH
Radiographics 2002 May-Jun;22(3):621-37. doi: 10.1148/radiographics.22.3.g02ma17621. PMID: 12006691

Diagnosis

Parrack PH, Mariño-Enríquez A, Fletcher CDM, Hornick JL, Papke DJ Jr
Am J Surg Pathol 2023 Apr 1;47(4):453-460. Epub 2023 Jan 23 doi: 10.1097/PAS.0000000000002018. PMID: 36693363
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Katoh M, Nakagama H
Med Res Rev 2014 Mar;34(2):280-300. Epub 2013 May 21 doi: 10.1002/med.21288. PMID: 23696246
Kim MP, Hofstetter WL
Thorac Surg Clin 2009 Nov;19(4):521-9. doi: 10.1016/j.thorsurg.2009.08.007. PMID: 20112635
Gladish GW, Sabloff BM, Munden RF, Truong MT, Erasmus JJ, Chasen MH
Radiographics 2002 May-Jun;22(3):621-37. doi: 10.1148/radiographics.22.3.g02ma17621. PMID: 12006691

Therapy

Strausz S, Ruotsalainen S, Ollila HM, Karjalainen J, Kiiskinen T, Reeve M, Kurki M, Mars N, Havulinna AS, Luonsi E, Mansour Aly D, Ahlqvist E, Teder-Laving M, Palta P, Groop L, Mägi R, Mäkitie A, Salomaa V, Bachour A, Tuomi T; FinnGen, Palotie A, Palotie T, Ripatti S
Eur Respir J 2021 May;57(5) Epub 2021 May 6 doi: 10.1183/13993003.03091-2020. PMID: 33243845
Doheny D, Manore SG, Wong GL, Lo HW
Cells 2020 Sep 17;9(9) doi: 10.3390/cells9092114. PMID: 32957513Free PMC Article
Dobrenkov K, Cheung NK
Semin Oncol 2014 Oct;41(5):589-612. Epub 2014 Jul 21 doi: 10.1053/j.seminoncol.2014.07.003. PMID: 25440605Free PMC Article
Katoh M, Nakagama H
Med Res Rev 2014 Mar;34(2):280-300. Epub 2013 May 21 doi: 10.1002/med.21288. PMID: 23696246
Wesche J, Haglund K, Haugsten EM
Biochem J 2011 Jul 15;437(2):199-213. doi: 10.1042/BJ20101603. PMID: 21711248

Prognosis

Rassy E, Abou-Jaoude R, Boussios S, Assi T, Kattan J, Khaled H, Pavlidis N
J Egypt Natl Canc Inst 2022 Jun 27;34(1):27. doi: 10.1186/s43046-022-00128-1. PMID: 35754068
González IA, Stewart DR, Schultz KAP, Field AP, Hill DA, Dehner LP
Mod Pathol 2022 Jan;35(1):4-22. Epub 2021 Oct 1 doi: 10.1038/s41379-021-00905-8. PMID: 34599283Free PMC Article
Kaczanowska S, Beury DW, Gopalan V, Tycko AK, Qin H, Clements ME, Drake J, Nwanze C, Murgai M, Rae Z, Ju W, Alexander KA, Kline J, Contreras CF, Wessel KM, Patel S, Hannenhalli S, Kelly MC, Kaplan RN
Cell 2021 Apr 15;184(8):2033-2052.e21. Epub 2021 Mar 24 doi: 10.1016/j.cell.2021.02.048. PMID: 33765443Free PMC Article
Kim MP, Hofstetter WL
Thorac Surg Clin 2009 Nov;19(4):521-9. doi: 10.1016/j.thorsurg.2009.08.007. PMID: 20112635
Donaldson SS
Int J Radiat Oncol Biol Phys 1993 Aug 1;26(5):739-49. doi: 10.1016/0360-3016(93)90487-g. PMID: 8344841

Clinical prediction guides

Behzatoğlu K, Schmitt F
Acta Cytol 2022;66(4):347-356. Epub 2021 Dec 17 doi: 10.1159/000520875. PMID: 34923492
Strausz S, Ruotsalainen S, Ollila HM, Karjalainen J, Kiiskinen T, Reeve M, Kurki M, Mars N, Havulinna AS, Luonsi E, Mansour Aly D, Ahlqvist E, Teder-Laving M, Palta P, Groop L, Mägi R, Mäkitie A, Salomaa V, Bachour A, Tuomi T; FinnGen, Palotie A, Palotie T, Ripatti S
Eur Respir J 2021 May;57(5) Epub 2021 May 6 doi: 10.1183/13993003.03091-2020. PMID: 33243845
Amadou A, Achatz MIW, Hainaut P
Curr Opin Oncol 2018 Jan;30(1):23-29. doi: 10.1097/CCO.0000000000000423. PMID: 29076966
Takita J
Cancer Sci 2017 Oct;108(10):1913-1920. Epub 2017 Aug 24 doi: 10.1111/cas.13333. PMID: 28756644Free PMC Article
Donaldson SS
Int J Radiat Oncol Biol Phys 1993 Aug 1;26(5):739-49. doi: 10.1016/0360-3016(93)90487-g. PMID: 8344841

Recent systematic reviews

Vaarwerk B, Breunis WB, Haveman LM, de Keizer B, Jehanno N, Borgwardt L, van Rijn RR, van den Berg H, Cohen JF, van Dalen EC, Merks JH
Cochrane Database Syst Rev 2021 Nov 9;11(11):CD012325. doi: 10.1002/14651858.CD012325.pub2. PMID: 34753195Free PMC Article
Zhang Q, Wang Q, Sun W, Gao F, Liu L, Cheng L, Li Z
Biomed Res Int 2018;2018:6124927. Epub 2018 Nov 25 doi: 10.1155/2018/6124927. PMID: 30596096Free PMC Article
Gómez FM, Patel PA, Stuart S, Roebuck DJ
Pediatr Radiol 2014 Oct;44(10):1281-9. Epub 2014 May 13 doi: 10.1007/s00247-014-3001-5. PMID: 24821394

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