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Complete tracheal ring

MedGen UID:
1814133
•Concept ID:
C5558400
•
Anatomical Abnormality
Synonyms: Complete tracheal ring deformity; Complete tracheal rings; CTRD
 
HPO: HP:0041094

Definition

Continuous or nearly continuous configuration of the cartilaginous tracheal ring. [from HPO]

Professional guidelines

PubMed

Diagnosis and management of complete tracheal rings with concurrent tracheoesophageal fistula.
Wolter NE, Kennedy AA, Rutter MJ, Matava C, Honjo O, Chiu PL, Propst EJ
Int J Pediatr Otorhinolaryngol 2020 Jun;133:109971. Epub 2020 Feb 27 doi: 10.1016/j.ijporl.2020.109971. PMID: 32179205

Recent clinical studies

Etiology

Impact of preoperative respiratory distress on outcomes of slide tracheoplasty.
Nguyen KT, Van Nguyen AT, Tran VQ, Nguyen YT, Le CT, Van Dang T, Jun TG, Nguyen TLT
Eur J Cardiothorac Surg 2024 Jun 3;65(6) doi: 10.1093/ejcts/ezae227. PMID: 38830041
Incidence of congenital tracheal stenosis in left pulmonary artery sling diagnosed by bronchoscopy.
Tsuji E, Morita K, Matsuhisa H, Bitoh Y, Hatakeyama T
Pediatr Surg Int 2023 Jul 27;39(1):240. doi: 10.1007/s00383-023-05527-6. PMID: 37498341
Clinical features of a tracheoesophageal fistula associated with complete tracheal rings.
Morita K, Hatakeyama T
Pediatr Surg Int 2023 Jun 24;39(1):218. doi: 10.1007/s00383-023-05503-0. PMID: 37354332
Complete Tracheal Ring Deformity. A Translational Genomics Approach to Pathogenesis.
Sinner DI, Carey B, Zgherea D, Kaufman KM, Leesman L, Wood RE, Rutter MJ, de Alarcon A, Elluru RG, Harley JB, Whitsett JA, Trapnell BC
Am J Respir Crit Care Med 2019 Nov 15;200(10):1267-1281. doi: 10.1164/rccm.201809-1626OC. PMID: 31215789Free PMC Article
Repair of long-segment congenital tracheal stenosis.
Yang JH, Jun TG, Sung K, Choi JH, Lee YT, Park PW
J Korean Med Sci 2007 Jun;22(3):491-6. doi: 10.3346/jkms.2007.22.3.491. PMID: 17596659Free PMC Article

Diagnosis

Clinical features of a tracheoesophageal fistula associated with complete tracheal rings.
Morita K, Hatakeyama T
Pediatr Surg Int 2023 Jun 24;39(1):218. doi: 10.1007/s00383-023-05503-0. PMID: 37354332
Complete Tracheal Ring Deformity, Recurrent Pneumothoraces and Pleuropulmonary Blastoma in a Child: Coincidence or Common Genetic Cause?
Thiemann I, Hoppen T, Laur M, Ohlert M, Lobitz S, Schwerk N, Dingemann J, Länger F, Grychtol RM, Nüßlein T
Klin Padiatr 2022 Sep;234(5):311-313. Epub 2022 Feb 3 doi: 10.1055/a-1699-2026. PMID: 35114704
Tracheal anomalies associated with Down syndrome: A systematic review.
Fockens MM, Hölscher M, Limpens J, Dikkers FG
Pediatr Pulmonol 2021 May;56(5):814-822. Epub 2021 Jan 12 doi: 10.1002/ppul.25203. PMID: 33434377Free PMC Article
Diagnosis and management of complete tracheal rings with concurrent tracheoesophageal fistula.
Wolter NE, Kennedy AA, Rutter MJ, Matava C, Honjo O, Chiu PL, Propst EJ
Int J Pediatr Otorhinolaryngol 2020 Jun;133:109971. Epub 2020 Feb 27 doi: 10.1016/j.ijporl.2020.109971. PMID: 32179205
Complete Tracheal Ring Deformity. A Translational Genomics Approach to Pathogenesis.
Sinner DI, Carey B, Zgherea D, Kaufman KM, Leesman L, Wood RE, Rutter MJ, de Alarcon A, Elluru RG, Harley JB, Whitsett JA, Trapnell BC
Am J Respir Crit Care Med 2019 Nov 15;200(10):1267-1281. doi: 10.1164/rccm.201809-1626OC. PMID: 31215789Free PMC Article

Prognosis

Incidence of congenital tracheal stenosis in left pulmonary artery sling diagnosed by bronchoscopy.
Tsuji E, Morita K, Matsuhisa H, Bitoh Y, Hatakeyama T
Pediatr Surg Int 2023 Jul 27;39(1):240. doi: 10.1007/s00383-023-05527-6. PMID: 37498341
Lethal severe congenital tracheal stenosis with tracheal ring complicating respiratory distress syndrome in an extremely premature infant: first reported case in Qatar with a literature review.
Nimeri N, Ali H, Mahmoud N
BMJ Case Rep 2020 Dec 12;13(12) doi: 10.1136/bcr-2020-236107. PMID: 33310828Free PMC Article
Complete Tracheal Ring Deformity. A Translational Genomics Approach to Pathogenesis.
Sinner DI, Carey B, Zgherea D, Kaufman KM, Leesman L, Wood RE, Rutter MJ, de Alarcon A, Elluru RG, Harley JB, Whitsett JA, Trapnell BC
Am J Respir Crit Care Med 2019 Nov 15;200(10):1267-1281. doi: 10.1164/rccm.201809-1626OC. PMID: 31215789Free PMC Article
Repair of long-segment congenital tracheal stenosis.
Yang JH, Jun TG, Sung K, Choi JH, Lee YT, Park PW
J Korean Med Sci 2007 Jun;22(3):491-6. doi: 10.3346/jkms.2007.22.3.491. PMID: 17596659Free PMC Article
Subglottic ductal cysts associated with complete tracheal ring deformity: coexistence of two rare airway abnormalities with fatal outcome.
Bokhari A, Heller DS, Fonseca C, Mirani N
Pediatr Dev Pathol 2004 May-Jun;7(3):273-6. Epub 2004 Mar 17 doi: 10.1007/s10024-003-0106-5. PMID: 15022057

Clinical prediction guides

Multilevel Airway Stenosis Being Bypassed by a Customized Tracheostomy Tube in an Infant with Myhre Syndrome.
Jeon MJ, Kim MJ, Kim JH, Park JS, Yim J, Kim M, Kwon SK, Lee S, Ko JM, Chae JH, Suh DI
Pediatr Allergy Immunol Pulmonol 2021 Jun;34(2):83-87. doi: 10.1089/ped.2021.0029. PMID: 34143683Free PMC Article
Development pattern of tracheal cartilage in human embryos.
Fockens MM, de Bakker BS, Oostra RJ, Dikkers FG
Clin Anat 2021 Jul;34(5):668-672. Epub 2020 Oct 8 doi: 10.1002/ca.23688. PMID: 32986245Free PMC Article
Complete Tracheal Ring Deformity. A Translational Genomics Approach to Pathogenesis.
Sinner DI, Carey B, Zgherea D, Kaufman KM, Leesman L, Wood RE, Rutter MJ, de Alarcon A, Elluru RG, Harley JB, Whitsett JA, Trapnell BC
Am J Respir Crit Care Med 2019 Nov 15;200(10):1267-1281. doi: 10.1164/rccm.201809-1626OC. PMID: 31215789Free PMC Article

Recent systematic reviews

Tracheal anomalies associated with Down syndrome: A systematic review.
Fockens MM, Hölscher M, Limpens J, Dikkers FG
Pediatr Pulmonol 2021 May;56(5):814-822. Epub 2021 Jan 12 doi: 10.1002/ppul.25203. PMID: 33434377Free PMC Article
Diagnosis and management of complete tracheal rings with concurrent tracheoesophageal fistula.
Wolter NE, Kennedy AA, Rutter MJ, Matava C, Honjo O, Chiu PL, Propst EJ
Int J Pediatr Otorhinolaryngol 2020 Jun;133:109971. Epub 2020 Feb 27 doi: 10.1016/j.ijporl.2020.109971. PMID: 32179205

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