U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Prader-Willi syndrome due to imprinting mutation

MedGen UID:
1826086
Concept ID:
C5680510
Disease or Syndrome
Monarch Initiative: MONDO:0015786
Orphanet: ORPHA177910

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrader-Willi syndrome due to imprinting mutation

Professional guidelines

PubMed

Torun D, Akin O
Clin Dysmorphol 2024 Oct 1;33(4):145-151. Epub 2024 Jun 18 doi: 10.1097/MCD.0000000000000506. PMID: 38934057
Mao S, Yang L, Gao Y, Zou C
Clin Genet 2024 Apr;105(4):415-422. Epub 2024 Jan 23 doi: 10.1111/cge.14477. PMID: 38258470
van Bosse HJP, Butler MG
Genes (Basel) 2020 Feb 28;11(3) doi: 10.3390/genes11030260. PMID: 32121146Free PMC Article

Recent clinical studies

Etiology

Mao S, Yang L, Gao Y, Zou C
Clin Genet 2024 Apr;105(4):415-422. Epub 2024 Jan 23 doi: 10.1111/cge.14477. PMID: 38258470
van Bosse HJP, Butler MG
Genes (Basel) 2020 Feb 28;11(3) doi: 10.3390/genes11030260. PMID: 32121146Free PMC Article
Bennett JA, Germani T, Haqq AM, Zwaigenbaum L
Am J Med Genet A 2015 Dec;167A(12):2936-44. Epub 2015 Aug 29 doi: 10.1002/ajmg.a.37286. PMID: 26331980
Eggermann T
Am J Med Genet C Semin Med Genet 2010 Aug 15;154C(3):355-64. doi: 10.1002/ajmg.c.30274. PMID: 20803658
Khan NL, Wood NW
Curr Opin Neurol 1999 Apr;12(2):149-54. doi: 10.1097/00019052-199904000-00004. PMID: 10226746

Diagnosis

Kalsner L, Chamberlain SJ
Pediatr Clin North Am 2015 Jun;62(3):587-606. Epub 2015 Apr 22 doi: 10.1016/j.pcl.2015.03.004. PMID: 26022164Free PMC Article
Adams DJ, Clark DA
Pediatr Clin North Am 2015 Apr;62(2):411-26. Epub 2015 Jan 22 doi: 10.1016/j.pcl.2014.11.005. PMID: 25836705
Eggermann T
Am J Med Genet C Semin Med Genet 2010 Aug 15;154C(3):355-64. doi: 10.1002/ajmg.c.30274. PMID: 20803658
Cassidy SB
J Med Genet 1997 Nov;34(11):917-23. doi: 10.1136/jmg.34.11.917. PMID: 9391886Free PMC Article
Young ID
Lancet 1995 Jun 24;345(8965):1590. doi: 10.1016/s0140-6736(95)90112-4. PMID: 7783534

Therapy

Oldzej J, Manazir J, Gold JA, Mahmoud R, Osann K, Flodman P, Cassidy SB, Kimonis VE
Am J Med Genet A 2020 Jan;182(1):169-175. Epub 2019 Nov 29 doi: 10.1002/ajmg.a.61408. PMID: 31782896
Botezatu A, Puiu M, Cucu N, Diaconu CC, Badiu C, Arsene C, Iancu IV, Plesa A, Anton G
Gene 2016 Jan 10;575(2 Pt 1):353-8. Epub 2015 Sep 1 doi: 10.1016/j.gene.2015.08.058. PMID: 26335514
Gold JA, Ruth C, Osann K, Flodman P, McManus B, Lee HS, Donkervoort S, Khare M, Roof E, Dykens E, Miller JL, Driscoll DJ, Butler MG, Heinemann J, Cassidy S, Kimonis VE
Genet Med 2014 Feb;16(2):164-9. Epub 2013 Aug 8 doi: 10.1038/gim.2013.97. PMID: 23928912Free PMC Article
Lalande M, Calciano MA
Cell Mol Life Sci 2007 Apr;64(7-8):947-60. doi: 10.1007/s00018-007-6460-0. PMID: 17347796Free PMC Article
Wharton RH, Loechner KJ
Curr Opin Pediatr 1996 Dec;8(6):618-24. doi: 10.1097/00008480-199612000-00013. PMID: 9018447

Prognosis

Cintra HA, Rocha DN, da Costa ACC, Tyszler LS, Freitas S, de Araujo LA, Crozoe LI, de Paula LR, Correia PS, Gomes LHF, da Cunha Guida L
Orphanet J Rare Dis 2024 Jun 20;19(1):240. doi: 10.1186/s13023-024-03157-2. PMID: 38902749Free PMC Article
Yang-Li D, Ke H, Chao-Chun Z, Guan-Ping D
Indian Pediatr 2019 Sep 15;56(9):789-791. PMID: 31638013
Adams DJ, Clark DA
Pediatr Clin North Am 2015 Apr;62(2):411-26. Epub 2015 Jan 22 doi: 10.1016/j.pcl.2014.11.005. PMID: 25836705
Veltman MW, Craig EE, Bolton PF
Psychiatr Genet 2005 Dec;15(4):243-54. doi: 10.1097/00041444-200512000-00006. PMID: 16314754
Webb T
J Med Genet 1994 Aug;31(8):585-94. doi: 10.1136/jmg.31.8.585. PMID: 7815414Free PMC Article

Clinical prediction guides

Yamada M, Okuno H, Okamoto N, Suzuki H, Miya F, Takenouchi T, Kosaki K
Eur J Med Genet 2023 Feb;66(2):104690. Epub 2022 Dec 30 doi: 10.1016/j.ejmg.2022.104690. PMID: 36587803
van Bosse HJP, Butler MG
Genes (Basel) 2020 Feb 28;11(3) doi: 10.3390/genes11030260. PMID: 32121146Free PMC Article
Manzardo AM, Weisensel N, Ayala S, Hossain W, Butler MG
Clin Genet 2018 Mar;93(3):622-631. Epub 2018 Feb 5 doi: 10.1111/cge.13142. PMID: 28984907Free PMC Article
Eggermann T
Am J Med Genet C Semin Med Genet 2010 Aug 15;154C(3):355-64. doi: 10.1002/ajmg.c.30274. PMID: 20803658
Walter J, Paulsen M
Semin Cell Dev Biol 2003 Feb;14(1):101-10. doi: 10.1016/s1084-9521(02)00142-8. PMID: 12524013

Recent systematic reviews

Bennett JA, Germani T, Haqq AM, Zwaigenbaum L
Am J Med Genet A 2015 Dec;167A(12):2936-44. Epub 2015 Aug 29 doi: 10.1002/ajmg.a.37286. PMID: 26331980
Rocha CF, Paiva CL
Genet Mol Res 2014 Mar 31;13(1):2290-8. doi: 10.4238/2014.March.31.9. PMID: 24737477
Veltman MW, Craig EE, Bolton PF
Psychiatr Genet 2005 Dec;15(4):243-54. doi: 10.1097/00041444-200512000-00006. PMID: 16314754

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...