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Primary polyarteritis nodosa

MedGen UID:
1842954
•Concept ID:
C5680052
•
Disease or Syndrome
Synonyms: Primary PAN; primary PAN; Primary periarteritis nodosa; primary periarteritis nodosa; primary polyarteritis nodosa
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0018593
Orphanet: ORPHA439737

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary polyarteritis nodosa

Professional guidelines

PubMed

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Treatment of systemic necrotizing vasculitides: recent advances and important clinical considerations.
Pagnoux C, Mendel A
Expert Rev Clin Immunol 2019 Sep;15(9):939-949. Epub 2019 Aug 26 doi: 10.1080/1744666X.2019.1656527. PMID: 31414912
Classification and classification criteria for vasculitis: achievements, limitations and prospects.
Mahr A, de Menthon M
Curr Opin Rheumatol 2015 Jan;27(1):1-9. doi: 10.1097/BOR.0000000000000134. PMID: 25415531

Recent clinical studies

Etiology

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
The Incidence of Primary Systemic Vasculitis in Jerusalem: A 20-year Hospital-based Retrospective Study.
Nesher G, Ben-Chetrit E, Mazal B, Breuer GS
J Rheumatol 2016 Jun;43(6):1072-7. Epub 2016 Apr 15 doi: 10.3899/jrheum.150557. PMID: 27084915
Vasculitis and infections: contribution to the issue of autoimmunity reviews devoted to "autoimmunity and infection".
Kallenberg CG, Tadema H
Autoimmun Rev 2008 Oct;8(1):29-32. Epub 2008 Aug 12 doi: 10.1016/j.autrev.2008.07.020. PMID: 18703171Free PMC Article
Nosology of primary vasculitis.
Jennette JC, Falk RJ
Curr Opin Rheumatol 2007 Jan;19(1):10-6. doi: 10.1097/BOR.0b013e3280119877. PMID: 17143090
Ehrlichiosis associated vasculitis.
Pick N, Potasman I, Strenger C, Keysary A, Schwartz I
J Intern Med 2000 Jun;247(6):674-8. doi: 10.1046/j.1365-2796.2000.00680.x. PMID: 10886489

Diagnosis

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article
Vasculitic neuropathy.
Vrancken AF, Said G
Handb Clin Neurol 2013;115:463-83. doi: 10.1016/B978-0-444-52902-2.00026-6. PMID: 23931796
Panniculitis.
Ter Poorten MC, Thiers BH
Dermatol Clin 2002 Jul;20(3):421-33, vi. doi: 10.1016/s0733-8635(02)00008-6. PMID: 12170876
Ehrlichiosis associated vasculitis.
Pick N, Potasman I, Strenger C, Keysary A, Schwartz I
J Intern Med 2000 Jun;247(6):674-8. doi: 10.1046/j.1365-2796.2000.00680.x. PMID: 10886489

Therapy

Cardiac involvement in the adult primary vasculitides.
Pazzola G, Pipitone N, Salvarani C
Expert Rev Clin Immunol 2020 Oct;16(10):985-991. Epub 2020 Dec 24 doi: 10.1080/1744666X.2021.1823219. PMID: 32954889
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article
Vasculitis and infections: contribution to the issue of autoimmunity reviews devoted to "autoimmunity and infection".
Kallenberg CG, Tadema H
Autoimmun Rev 2008 Oct;8(1):29-32. Epub 2008 Aug 12 doi: 10.1016/j.autrev.2008.07.020. PMID: 18703171Free PMC Article
Vasculitic neuropathies.
Burns TM, Schaublin GA, Dyck PJ
Neurol Clin 2007 Feb;25(1):89-113. doi: 10.1016/j.ncl.2006.11.002. PMID: 17324722
Central nervous system polyarteritis nodosa.
Rosenberg MR, Parshley M, Gibson S, Wernick R
West J Med 1990 Nov;153(5):553-6. PMID: 1979706Free PMC Article

Prognosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Cardiac involvement in the adult primary vasculitides.
Pazzola G, Pipitone N, Salvarani C
Expert Rev Clin Immunol 2020 Oct;16(10):985-991. Epub 2020 Dec 24 doi: 10.1080/1744666X.2021.1823219. PMID: 32954889
Lymphocytic thrombophilic arteritis complicated by systemic involvement.
Wee E, Nikpour M, Balta S, Williams RA, Kelly RI
Australas J Dermatol 2018 Aug;59(3):223-225. Epub 2018 Apr 6 doi: 10.1111/ajd.12798. PMID: 29624649
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
Polyarteritis nodosa.
Bonsib SM
Semin Diagn Pathol 2001 Feb;18(1):14-23. PMID: 11296989

Clinical prediction guides

Clusters in Pediatric Rheumatic Diseases.
Sag E, Demir S, Ozen S
Curr Rheumatol Rep 2020 May 20;22(7):28. doi: 10.1007/s11926-020-00908-5. PMID: 32436006
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Vasculitis and infections: contribution to the issue of autoimmunity reviews devoted to "autoimmunity and infection".
Kallenberg CG, Tadema H
Autoimmun Rev 2008 Oct;8(1):29-32. Epub 2008 Aug 12 doi: 10.1016/j.autrev.2008.07.020. PMID: 18703171Free PMC Article
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537
Uveitis in connective tissue disorders.
Martenet AC
Trans Ophthalmol Soc U K (1962) 1981 Sep;101 (Pt 3)(3):376-9. PMID: 6134360

Recent systematic reviews

Systematic review of childhood-onset polyarteritis nodosa and DADA2.
Kasap Cuceoglu M, Sener S, Batu ED, Kaya Akca U, Demir S, Sag E, Atalay E, Balık Z, Basaran O, Bilginer Y, Ozen S
Semin Arthritis Rheum 2021 Jun;51(3):559-564. Epub 2021 Apr 19 doi: 10.1016/j.semarthrit.2021.04.009. PMID: 33901990
Haemophagocytic syndrome in rheumatic patients. A systematic review.
Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A
Eur Rev Med Pharmacol Sci 2012 Oct;16(10):1414-24. PMID: 23104659

Supplemental Content

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    Clinical resources

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