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Idiopathic cardiomyopathy

MedGen UID:
18634
•Concept ID:
C0033141
•
Disease or Syndrome
Synonyms: Cardiomyopathies, Primary; Cardiomyopathy, Primary; Disease, Primary Myocardial; Diseases, Primary Myocardial; Myocardial Disease, Primary; Myocardial Diseases, Primary; Primary Cardiomyopathies; Primary Cardiomyopathy; Primary Myocardial Disease; Primary Myocardial Diseases
SNOMED CT: Primary cardiomyopathy (89461002)
 
Monarch Initiative: MONDO:0005110

Definition

Disease of the heart muscle associated with electrical or mechanical dysfunction, in which the heart is the sole or predominantly involved organ. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIdiopathic cardiomyopathy

Professional guidelines

PubMed

Anesthetic management of peripartum cardiomyopathy.
Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Arrhythmias in cardiac sarcoidosis: diagnosis and treatment.
Nery PB, Leung E, Birnie DH
Curr Opin Cardiol 2012 Mar;27(2):181-9. doi: 10.1097/HCO.0b013e32834e4c7c. PMID: 22186166

Recent clinical studies

Etiology

Complications of Endomyocardial Fibrosis and Their Physiological Compromise: A Review.
Lungu ND, Dujawara A
Curr Probl Cardiol 2023 Aug;48(8):101730. Epub 2023 Mar 31 doi: 10.1016/j.cpcardiol.2023.101730. PMID: 37003449
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Alcoholic cardiomyopathy : The result of dosage and individual predisposition.
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article

Diagnosis

Mechanisms of toxic cardiomyopathy.
Hantson P
Clin Toxicol (Phila) 2019 Jan;57(1):1-9. Epub 2018 Sep 27 doi: 10.1080/15563650.2018.1497172. PMID: 30260248
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Alcoholic cardiomyopathy : The result of dosage and individual predisposition.
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article
Myocardial biopsy.
Kawai C, Matsumori A, Kawamura K
Annu Rev Med 1980;31:139-57. doi: 10.1146/annurev.me.31.020180.001035. PMID: 6994601

Therapy

Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Alcoholic cardiomyopathy : The result of dosage and individual predisposition.
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Intravenous immunoglobulin therapy for patients with idiopathic cardiomyopathy and endomyocardial biopsy-proven high PVB19 viral load.
Dennert R, Velthuis S, Schalla S, Eurlings L, van Suylen RJ, van Paassen P, Tervaert JW, Wolffs P, Goossens VJ, Bruggeman C, Waltenberger J, Crijns HJ, Heymans S
Antivir Ther 2010;15(2):193-201. doi: 10.3851/IMP1516. PMID: 20386074

Prognosis

Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Myocardial biopsy.
Kawai C, Matsumori A, Kawamura K
Annu Rev Med 1980;31:139-57. doi: 10.1146/annurev.me.31.020180.001035. PMID: 6994601

Clinical prediction guides

Anesthetic management of peripartum cardiomyopathy.
Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Differences between idiopathic and ischemic dilated cardiomyopathy.
Fennira S, Zairi I, Jnifene Z, Lakhal M, Kammoun S, Kraiem S
Tunis Med 2016 Aug-Sep;94(8-9):535-540. PMID: 28603826
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article

Recent systematic reviews

Pentoxifylline for heart failure: a systematic review.
Batchelder K, Mayosi BM
S Afr Med J 2005 Mar;95(3):171-5. PMID: 15832667

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