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Idiopathic cardiomyopathy

MedGen UID:
18634
Concept ID:
C0033141
Disease or Syndrome
Synonyms: Cardiomyopathies, Primary; Cardiomyopathy, Primary; Disease, Primary Myocardial; Diseases, Primary Myocardial; Myocardial Disease, Primary; Myocardial Diseases, Primary; Primary Cardiomyopathies; Primary Cardiomyopathy; Primary Myocardial Disease; Primary Myocardial Diseases
SNOMED CT: Primary cardiomyopathy (89461002)
 
Monarch Initiative: MONDO:0005110

Definition

Disease of the heart muscle associated with electrical or mechanical dysfunction, in which the heart is the sole or predominantly involved organ. [from SNOMEDCT_US]

Term Hierarchy

Professional guidelines

PubMed

Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Nery PB, Leung E, Birnie DH
Curr Opin Cardiol 2012 Mar;27(2):181-9. doi: 10.1097/HCO.0b013e32834e4c7c. PMID: 22186166

Recent clinical studies

Etiology

Kim Y, Gunnarsdóttir OB, Viveiros A, Reichart D, Quiat D, Willcox JAL, Zhang H, Chen H, Curran JJ, Kim DH, Urschel S, McDonough B, Gorham J, DePalma SR, Seidman JG, Seidman CE, Oudit GY
Circ Genom Precis Med 2023 Oct;16(5):452-461. Epub 2023 Sep 28 doi: 10.1161/CIRCGEN.123.004062. PMID: 37767697Free PMC Article
Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article

Diagnosis

Kim Y, Gunnarsdóttir OB, Viveiros A, Reichart D, Quiat D, Willcox JAL, Zhang H, Chen H, Curran JJ, Kim DH, Urschel S, McDonough B, Gorham J, DePalma SR, Seidman JG, Seidman CE, Oudit GY
Circ Genom Precis Med 2023 Oct;16(5):452-461. Epub 2023 Sep 28 doi: 10.1161/CIRCGEN.123.004062. PMID: 37767697Free PMC Article
Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Hantson P
Clin Toxicol (Phila) 2019 Jan;57(1):1-9. Epub 2018 Sep 27 doi: 10.1080/15563650.2018.1497172. PMID: 30260248
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article

Therapy

Chen HF, Chang YH, Lo HJ, Isfandiari MA, Martini S, Hou WH, Li CY
Cardiovasc Diabetol 2020 Oct 14;19(1):177. doi: 10.1186/s12933-020-01144-y. PMID: 33054769Free PMC Article
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article

Prognosis

Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Kawai C, Matsumori A, Kawamura K
Annu Rev Med 1980;31:139-57. doi: 10.1146/annurev.me.31.020180.001035. PMID: 6994601

Clinical prediction guides

Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Takeda N
Int J Mol Med 2003 Jan;11(1):13-6. PMID: 12469210

Recent systematic reviews

Batchelder K, Mayosi BM
S Afr Med J 2005 Mar;95(3):171-5. PMID: 15832667

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