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Polymyalgia rheumatica

MedGen UID:
19393
Concept ID:
C0032533
Disease or Syndrome
Synonyms: Forestier Certonciny Syndrome; Forestier-Certonciny Syndrome; Peri-Extra-Articular Rheumatism; Polymyalgia Rheumatica; Rheumatism, Peri Extra Articular; Rheumatism, Peri-Extra-Articular; Syndrome, Forestier-Certonciny
SNOMED CT: Polymyalgia rheumatica (65323003); Forestier-Certonciny syndrome (65323003); Senile arthritis (65323003); PMR - Polymyalgia rheumatica (65323003)
 
Monarch Initiative: MONDO:0019735
Orphanet: ORPHA93569

Definition

A rare rheumatologic disease characterized by bilateral morning stiffness which lasts > 45-60 min of duration associated with a subacute-onset of severe pain with active movements, typically affecting the shoulders, proximal upper limbs, neck and/or, less commonly, the pelvic girdle and proximal aspects of thighs, which are exacerbated with inactivity and improve progressively over the day. Muscle tenderness, peripheral synovitis, arthritis, carpal tunnel syndrome or distal tenosynovitis, as well as non-specific symptoms, such as fatigue, asthenia, malaise, low-grade fever, anorexia and weight loss, may be associated. Acute phase reactants (erythrocyte sedimentation rate, C-reactive protein) are increased. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPolymyalgia rheumatica

Professional guidelines

PubMed

Ling ML, Yosar J, Lee BW, Shah SA, Jiang IW, Finniss A, Allende A, Francis IC
Clin Exp Optom 2020 Sep;103(5):572-582. Epub 2019 Oct 29 doi: 10.1111/cxo.12975. PMID: 31663193
Camellino D, Giusti A, Girasole G, Bianchi G, Dejaco C
Drugs Aging 2019 Nov;36(11):1015-1026. doi: 10.1007/s40266-019-00705-5. PMID: 31493201
Ciofalo A, Gulotta G, Iannella G, Pasquariello B, Manno A, Angeletti D, Pace A, Greco A, Altissimi G, de Vincentiis M, Magliulo G
Curr Rheumatol Rev 2019;15(4):259-268. doi: 10.2174/1573397115666190227194014. PMID: 30827250

Recent clinical studies

Etiology

Devauchelle-Pensec V, Carvajal-Alegria G, Dernis E, Richez C, Truchetet ME, Wendling D, Toussirot E, Perdriger A, Gottenberg JE, Felten R, Fautrel BJ, Chiche L, Hilliquin P, Le Henaff C, Dervieux B, Direz G, Chary-Valckenaere I, Cornec D, Guellec D, Marhadour T, Nowak E, Saraux A
JAMA 2022 Sep 20;328(11):1053-1062. doi: 10.1001/jama.2022.15459. PMID: 36125471
Colombo MG, Wetzel AJ, Haumann H, Dally S, Kirtschig G, Joos S
Dtsch Arztebl Int 2022 Jun 17;119(24):411-417. doi: 10.3238/arztebl.m2022.0218. PMID: 35635433Free PMC Article
Camellino D, Giusti A, Girasole G, Bianchi G, Dejaco C
Drugs Aging 2019 Nov;36(11):1015-1026. doi: 10.1007/s40266-019-00705-5. PMID: 31493201
Matteson EL, Dejaco C
Ann Intern Med 2017 May 2;166(9):ITC65-ITC80. doi: 10.7326/AITC201705020. PMID: 28460395
Buttgereit F, Dejaco C, Matteson EL, Dasgupta B
JAMA 2016 Jun 14;315(22):2442-58. doi: 10.1001/jama.2016.5444. PMID: 27299619

Diagnosis

Rosenberg H, Halman S, Yadav K
CMAJ 2021 Nov 22;193(46):E1770. doi: 10.1503/cmaj.210541. PMID: 34810164Free PMC Article
Mahmood SB, Nelson E, Padniewski J, Nasr R
Cleve Clin J Med 2020 Aug 31;87(9):549-556. doi: 10.3949/ccjm.87a.20008. PMID: 32868305
Camellino D, Giusti A, Girasole G, Bianchi G, Dejaco C
Drugs Aging 2019 Nov;36(11):1015-1026. doi: 10.1007/s40266-019-00705-5. PMID: 31493201
González-Gay MA, Matteson EL, Castañeda S
Lancet 2017 Oct 7;390(10103):1700-1712. Epub 2017 Jul 31 doi: 10.1016/S0140-6736(17)31825-1. PMID: 28774422
Matteson EL, Dejaco C
Ann Intern Med 2017 May 2;166(9):ITC65-ITC80. doi: 10.7326/AITC201705020. PMID: 28460395

Therapy

Lundberg IE, Sharma A, Turesson C, Mohammad AJ
J Intern Med 2022 Nov;292(5):717-732. Epub 2022 Jun 11 doi: 10.1111/joim.13525. PMID: 35612524Free PMC Article
Mahmood SB, Nelson E, Padniewski J, Nasr R
Cleve Clin J Med 2020 Aug 31;87(9):549-556. doi: 10.3949/ccjm.87a.20008. PMID: 32868305
Camellino D, Giusti A, Girasole G, Bianchi G, Dejaco C
Drugs Aging 2019 Nov;36(11):1015-1026. doi: 10.1007/s40266-019-00705-5. PMID: 31493201
González-Gay MA, Matteson EL, Castañeda S
Lancet 2017 Oct 7;390(10103):1700-1712. Epub 2017 Jul 31 doi: 10.1016/S0140-6736(17)31825-1. PMID: 28774422
Matteson EL, Dejaco C
Ann Intern Med 2017 May 2;166(9):ITC65-ITC80. doi: 10.7326/AITC201705020. PMID: 28460395

Prognosis

Lundberg IE, Sharma A, Turesson C, Mohammad AJ
J Intern Med 2022 Nov;292(5):717-732. Epub 2022 Jun 11 doi: 10.1111/joim.13525. PMID: 35612524Free PMC Article
Hahn J, Cook NR, Alexander EK, Friedman S, Walter J, Bubes V, Kotler G, Lee IM, Manson JE, Costenbader KH
BMJ 2022 Jan 26;376:e066452. doi: 10.1136/bmj-2021-066452. PMID: 35082139Free PMC Article
Camellino D, Giusti A, Girasole G, Bianchi G, Dejaco C
Drugs Aging 2019 Nov;36(11):1015-1026. doi: 10.1007/s40266-019-00705-5. PMID: 31493201
Ciofalo A, Gulotta G, Iannella G, Pasquariello B, Manno A, Angeletti D, Pace A, Greco A, Altissimi G, de Vincentiis M, Magliulo G
Curr Rheumatol Rev 2019;15(4):259-268. doi: 10.2174/1573397115666190227194014. PMID: 30827250
Matteson EL, Dejaco C
Ann Intern Med 2017 May 2;166(9):ITC65-ITC80. doi: 10.7326/AITC201705020. PMID: 28460395

Clinical prediction guides

Devauchelle-Pensec V, Carvajal-Alegria G, Dernis E, Richez C, Truchetet ME, Wendling D, Toussirot E, Perdriger A, Gottenberg JE, Felten R, Fautrel BJ, Chiche L, Hilliquin P, Le Henaff C, Dervieux B, Direz G, Chary-Valckenaere I, Cornec D, Guellec D, Marhadour T, Nowak E, Saraux A
JAMA 2022 Sep 20;328(11):1053-1062. doi: 10.1001/jama.2022.15459. PMID: 36125471
Lundberg IE, Sharma A, Turesson C, Mohammad AJ
J Intern Med 2022 Nov;292(5):717-732. Epub 2022 Jun 11 doi: 10.1111/joim.13525. PMID: 35612524Free PMC Article
Stone JH, McDowell PJ, Jayne DRW, Merkel PA, Robson J, Patel NJ, Zhang Y, Yue H, Bekker P, Heaney LG
Semin Arthritis Rheum 2022 Aug;55:152010. Epub 2022 Apr 15 doi: 10.1016/j.semarthrit.2022.152010. PMID: 35486995
Sugihara T
Mod Rheumatol 2022 Apr 18;32(3):493-499. doi: 10.1093/mr/roab087. PMID: 34791359
van der Geest KSM, Treglia G, Glaudemans AWJM, Brouwer E, Jamar F, Slart RHJA, Gheysens O
Eur J Nucl Med Mol Imaging 2021 Jun;48(6):1876-1889. Epub 2020 Dec 28 doi: 10.1007/s00259-020-05162-6. PMID: 33372248Free PMC Article

Recent systematic reviews

Nielsen AW, Frølund LL, Våben C, Bonde AR, Gormsen LC, de Thurah AL, Hauge EM, Keller KK
Semin Arthritis Rheum 2022 Oct;56:152069. Epub 2022 Jul 13 doi: 10.1016/j.semarthrit.2022.152069. PMID: 35858507
van der Geest KSM, Treglia G, Glaudemans AWJM, Brouwer E, Jamar F, Slart RHJA, Gheysens O
Eur J Nucl Med Mol Imaging 2021 Jun;48(6):1876-1889. Epub 2020 Dec 28 doi: 10.1007/s00259-020-05162-6. PMID: 33372248Free PMC Article
Dejaco C, Ramiro S, Duftner C, Besson FL, Bley TA, Blockmans D, Brouwer E, Cimmino MA, Clark E, Dasgupta B, Diamantopoulos AP, Direskeneli H, Iagnocco A, Klink T, Neill L, Ponte C, Salvarani C, Slart RHJA, Whitlock M, Schmidt WA
Ann Rheum Dis 2018 May;77(5):636-643. Epub 2018 Jan 22 doi: 10.1136/annrheumdis-2017-212649. PMID: 29358285
Buttgereit F, Dejaco C, Matteson EL, Dasgupta B
JAMA 2016 Jun 14;315(22):2442-58. doi: 10.1001/jama.2016.5444. PMID: 27299619
Buchbinder R, Green S, Youd JM
Cochrane Database Syst Rev 2003;2003(1):CD004016. doi: 10.1002/14651858.CD004016. PMID: 12535501Free PMC Article

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