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Central Nervous System Cavernous Hemangioma

MedGen UID:
199825
Concept ID:
C0752160
Congenital Abnormality
Synonyms: Cavernous Hemangioma, Central Nervous System; Hemangioma, Cavernous, Central Nervous System

Definition

A cavernous hemangioma arising from the central nervous system. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral Nervous System Cavernous Hemangioma

Professional guidelines

PubMed

Bubenikova A, Skalicky P, Benes V Jr, Benes V Sr, Bradac O
J Neurol Neurosurg Psychiatry 2022 May;93(5):475-480. Epub 2022 Mar 10 doi: 10.1136/jnnp-2021-328658. PMID: 35273070
Akers A, Al-Shahi Salman R, A Awad I, Dahlem K, Flemming K, Hart B, Kim H, Jusue-Torres I, Kondziolka D, Lee C, Morrison L, Rigamonti D, Rebeiz T, Tournier-Lasserve E, Waggoner D, Whitehead K
Neurosurgery 2017 May 1;80(5):665-680. doi: 10.1093/neuros/nyx091. PMID: 28387823Free PMC Article
Mouchtouris N, Chalouhi N, Chitale A, Starke RM, Tjoumakaris SI, Rosenwasser RH, Jabbour PM
ScientificWorldJournal 2015;2015:808314. Epub 2015 Jan 5 doi: 10.1155/2015/808314. PMID: 25629087Free PMC Article

Recent clinical studies

Etiology

Hong T, Xiao X, Ren J, Cui B, Zong Y, Zou J, Kou Z, Jiang N, Meng G, Zeng G, Shan Y, Wu H, Chen Z, Liang J, Xiao X, Tang J, Wei Y, Ye M, Sun L, Li G, Hu P, Hui R, Zhang H, Wang Y
Brain 2021 Oct 22;144(9):2648-2658. doi: 10.1093/brain/awab117. PMID: 33729480
Paddock M, Lanham S, Gill K, Sinha S, Connolly DJA
Pediatr Neurol 2021 Mar;116:74-83. Epub 2020 Nov 27 doi: 10.1016/j.pediatrneurol.2020.11.004. PMID: 33494000
Idiculla PS, Gurala D, Philipose J, Rajdev K, Patibandla P
Eur Neurol 2020;83(4):360-368. Epub 2020 Jul 30 doi: 10.1159/000508748. PMID: 32731220
Flemming KD, Lanzino G
Mayo Clin Proc 2020 Sep;95(9):2005-2020. Epub 2020 Jun 27 doi: 10.1016/j.mayocp.2019.11.005. PMID: 32605781
Rosenow F, Alonso-Vanegas MA, Baumgartner C, Blümcke I, Carreño M, Gizewski ER, Hamer HM, Knake S, Kahane P, Lüders HO, Mathern GW, Menzler K, Miller J, Otsuki T, Ozkara C, Pitkänen A, Roper SN, Sakamoto AC, Sure U, Walker MC, Steinhoff BJ; Surgical Task Force, Commission on Therapeutic Strategies of the ILAE
Epilepsia 2013 Dec;54(12):2025-35. Epub 2013 Oct 17 doi: 10.1111/epi.12402. PMID: 24134485

Diagnosis

Paddock M, Lanham S, Gill K, Sinha S, Connolly DJA
Pediatr Neurol 2021 Mar;116:74-83. Epub 2020 Nov 27 doi: 10.1016/j.pediatrneurol.2020.11.004. PMID: 33494000
Idiculla PS, Gurala D, Philipose J, Rajdev K, Patibandla P
Eur Neurol 2020;83(4):360-368. Epub 2020 Jul 30 doi: 10.1159/000508748. PMID: 32731220
Akers A, Al-Shahi Salman R, A Awad I, Dahlem K, Flemming K, Hart B, Kim H, Jusue-Torres I, Kondziolka D, Lee C, Morrison L, Rigamonti D, Rebeiz T, Tournier-Lasserve E, Waggoner D, Whitehead K
Neurosurgery 2017 May 1;80(5):665-680. doi: 10.1093/neuros/nyx091. PMID: 28387823Free PMC Article
Mouchtouris N, Chalouhi N, Chitale A, Starke RM, Tjoumakaris SI, Rosenwasser RH, Jabbour PM
ScientificWorldJournal 2015;2015:808314. Epub 2015 Jan 5 doi: 10.1155/2015/808314. PMID: 25629087Free PMC Article
Smith ER, Scott RM
Neurosurg Clin N Am 2010 Jul;21(3):483-90. doi: 10.1016/j.nec.2010.03.003. PMID: 20561497

Therapy

Lanfranconi S, Scola E, Meessen JMTA, Pallini R, Bertani GA, Al-Shahi Salman R, Dejana E, Latini R; Treat_CCM Investigators
Lancet Neurol 2023 Jan;22(1):35-44. Epub 2022 Nov 17 doi: 10.1016/S1474-4422(22)00409-4. PMID: 36403580
Bubenikova A, Skalicky P, Benes V Jr, Benes V Sr, Bradac O
J Neurol Neurosurg Psychiatry 2022 May;93(5):475-480. Epub 2022 Mar 10 doi: 10.1136/jnnp-2021-328658. PMID: 35273070
Zafar A, Quadri SA, Farooqui M, Ikram A, Robinson M, Hart BL, Mabray MC, Vigil C, Tang AT, Kahn ML, Yonas H, Lawton MT, Kim H, Morrison L
Stroke 2019 May;50(5):1294-1301. doi: 10.1161/STROKEAHA.118.022314. PMID: 30909834Free PMC Article
Akers A, Al-Shahi Salman R, A Awad I, Dahlem K, Flemming K, Hart B, Kim H, Jusue-Torres I, Kondziolka D, Lee C, Morrison L, Rigamonti D, Rebeiz T, Tournier-Lasserve E, Waggoner D, Whitehead K
Neurosurgery 2017 May 1;80(5):665-680. doi: 10.1093/neuros/nyx091. PMID: 28387823Free PMC Article
Rosenow F, Alonso-Vanegas MA, Baumgartner C, Blümcke I, Carreño M, Gizewski ER, Hamer HM, Knake S, Kahane P, Lüders HO, Mathern GW, Menzler K, Miller J, Otsuki T, Ozkara C, Pitkänen A, Roper SN, Sakamoto AC, Sure U, Walker MC, Steinhoff BJ; Surgical Task Force, Commission on Therapeutic Strategies of the ILAE
Epilepsia 2013 Dec;54(12):2025-35. Epub 2013 Oct 17 doi: 10.1111/epi.12402. PMID: 24134485

Prognosis

Hong T, Xiao X, Ren J, Cui B, Zong Y, Zou J, Kou Z, Jiang N, Meng G, Zeng G, Shan Y, Wu H, Chen Z, Liang J, Xiao X, Tang J, Wei Y, Ye M, Sun L, Li G, Hu P, Hui R, Zhang H, Wang Y
Brain 2021 Oct 22;144(9):2648-2658. doi: 10.1093/brain/awab117. PMID: 33729480
Idiculla PS, Gurala D, Philipose J, Rajdev K, Patibandla P
Eur Neurol 2020;83(4):360-368. Epub 2020 Jul 30 doi: 10.1159/000508748. PMID: 32731220
Flemming KD, Lanzino G
Mayo Clin Proc 2020 Sep;95(9):2005-2020. Epub 2020 Jun 27 doi: 10.1016/j.mayocp.2019.11.005. PMID: 32605781
Goldstein HE, Solomon RA
Handb Clin Neurol 2017;143:241-247. doi: 10.1016/B978-0-444-63640-9.00023-0. PMID: 28552146
Mouchtouris N, Chalouhi N, Chitale A, Starke RM, Tjoumakaris SI, Rosenwasser RH, Jabbour PM
ScientificWorldJournal 2015;2015:808314. Epub 2015 Jan 5 doi: 10.1155/2015/808314. PMID: 25629087Free PMC Article

Clinical prediction guides

Lanfranconi S, Scola E, Meessen JMTA, Pallini R, Bertani GA, Al-Shahi Salman R, Dejana E, Latini R; Treat_CCM Investigators
Lancet Neurol 2023 Jan;22(1):35-44. Epub 2022 Nov 17 doi: 10.1016/S1474-4422(22)00409-4. PMID: 36403580
Arkar U, Vipotnik Vesnaver T, Maver A, Perković Benedik M, Peterlin B, Osredkar D
Eur J Paediatr Neurol 2021 Nov;35:61-66. Epub 2021 Oct 7 doi: 10.1016/j.ejpn.2021.10.001. PMID: 34634677
Hong T, Xiao X, Ren J, Cui B, Zong Y, Zou J, Kou Z, Jiang N, Meng G, Zeng G, Shan Y, Wu H, Chen Z, Liang J, Xiao X, Tang J, Wei Y, Ye M, Sun L, Li G, Hu P, Hui R, Zhang H, Wang Y
Brain 2021 Oct 22;144(9):2648-2658. doi: 10.1093/brain/awab117. PMID: 33729480
Missori P, Peschillo S, Ambrosone A, Martini S, Rastelli E, Mancarella C, Vigliotta M, Paolini S
Clin Neurol Neurosurg 2020 Oct;197:106167. Epub 2020 Aug 22 doi: 10.1016/j.clineuro.2020.106167. PMID: 32861039
Petr O, Lanzino G
J Neurosurg Sci 2015 Sep;59(3):271-82. Epub 2015 May 6 PMID: 25943871

Recent systematic reviews

Patet G, Bartoli A, Meling TR
Neurosurg Rev 2022 Feb;45(1):243-251. Epub 2021 Jul 4 doi: 10.1007/s10143-021-01598-y. PMID: 34218360Free PMC Article
Harris L, Poorthuis MHF, Grover P, Kitchen N, Al-Shahi Salman R
Neurosurg Rev 2022 Feb;45(1):231-241. Epub 2021 Jun 30 doi: 10.1007/s10143-021-01591-5. PMID: 34191202
Merlino L, Del Prete F, Titi L, Piccioni MG
J Gynecol Obstet Hum Reprod 2021 Jan;50(1):101927. Epub 2020 Oct 6 doi: 10.1016/j.jogoh.2020.101927. PMID: 33035718
Akers A, Al-Shahi Salman R, A Awad I, Dahlem K, Flemming K, Hart B, Kim H, Jusue-Torres I, Kondziolka D, Lee C, Morrison L, Rigamonti D, Rebeiz T, Tournier-Lasserve E, Waggoner D, Whitehead K
Neurosurgery 2017 May 1;80(5):665-680. doi: 10.1093/neuros/nyx091. PMID: 28387823Free PMC Article
Gross BA, Batjer HH, Awad IA, Bendok BR
Neurosurgery 2009 May;64(5):E805-18; discussion E818. doi: 10.1227/01.NEU.0000343668.44288.18. PMID: 19404127

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