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Localized Angiosarcoma

MedGen UID:
208926
Concept ID:
C0854893
Neoplastic Process
Synonyms: Angiosarcoma Nonmetastatic; Non-Metastatic Angiosarcoma; Non-Metastatic Hemangiosarcoma

Definition

Angiosarcoma that is confined to a specific site without evidence of spread to other anatomic sites. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLocalized Angiosarcoma

Professional guidelines

PubMed

Kobayashi K, Hanai N, Yoshimoto S, Saito Y, Homma A
Jpn J Clin Oncol 2023 Aug 30;53(9):743-756. doi: 10.1093/jjco/hyad048. PMID: 37309253Free PMC Article
Dufresne A, Meeus P, Sunyach MP
Curr Opin Oncol 2023 Jul 1;35(4):296-300. Epub 2023 May 12 doi: 10.1097/CCO.0000000000000958. PMID: 37222197
Budd GT
Curr Oncol Rep 2002 Nov;4(6):515-9. doi: 10.1007/s11912-002-0066-3. PMID: 12354365

Recent clinical studies

Etiology

Conforti F, Gronchi A, Penel N, Jones RL, Broto JM, Sala I, Bagnardi V, Napolitano A, Pala L, Pennacchioli E, Catania C, Queirolo P, Grigani G, Merlini A, Stacchiotti S, Comandone A, Vincenzi B, Quagliuolo V, Bertuzzi A, Boglione A, Palassini E, Baldi GG, Blay JY, Ryckewaert T, Toulmonde M, Italiano A, Le Cesne A, Ray-Coquard I, Cruz J, Hernández-León CN, Trufero JM, da Silva Moura D, Muñiz NH, De Pas T
Eur J Cancer 2022 Aug;171:183-192. Epub 2022 Jun 18 doi: 10.1016/j.ejca.2022.04.030. PMID: 35728378
Sinnamon AJ, Neuwirth MG, McMillan MT, Ecker BL, Bartlett EK, Zhang PJ, Kelz RR, Fraker DL, Roses RE, Karakousis GC
J Surg Oncol 2016 Oct;114(5):557-563. Epub 2016 Jul 4 doi: 10.1002/jso.24352. PMID: 27378102

Therapy

Conforti F, Gronchi A, Penel N, Jones RL, Broto JM, Sala I, Bagnardi V, Napolitano A, Pala L, Pennacchioli E, Catania C, Queirolo P, Grigani G, Merlini A, Stacchiotti S, Comandone A, Vincenzi B, Quagliuolo V, Bertuzzi A, Boglione A, Palassini E, Baldi GG, Blay JY, Ryckewaert T, Toulmonde M, Italiano A, Le Cesne A, Ray-Coquard I, Cruz J, Hernández-León CN, Trufero JM, da Silva Moura D, Muñiz NH, De Pas T
Eur J Cancer 2022 Aug;171:183-192. Epub 2022 Jun 18 doi: 10.1016/j.ejca.2022.04.030. PMID: 35728378

Prognosis

Conforti F, Gronchi A, Penel N, Jones RL, Broto JM, Sala I, Bagnardi V, Napolitano A, Pala L, Pennacchioli E, Catania C, Queirolo P, Grigani G, Merlini A, Stacchiotti S, Comandone A, Vincenzi B, Quagliuolo V, Bertuzzi A, Boglione A, Palassini E, Baldi GG, Blay JY, Ryckewaert T, Toulmonde M, Italiano A, Le Cesne A, Ray-Coquard I, Cruz J, Hernández-León CN, Trufero JM, da Silva Moura D, Muñiz NH, De Pas T
Eur J Cancer 2022 Aug;171:183-192. Epub 2022 Jun 18 doi: 10.1016/j.ejca.2022.04.030. PMID: 35728378
Sinnamon AJ, Neuwirth MG, McMillan MT, Ecker BL, Bartlett EK, Zhang PJ, Kelz RR, Fraker DL, Roses RE, Karakousis GC
J Surg Oncol 2016 Oct;114(5):557-563. Epub 2016 Jul 4 doi: 10.1002/jso.24352. PMID: 27378102

Clinical prediction guides

Conforti F, Gronchi A, Penel N, Jones RL, Broto JM, Sala I, Bagnardi V, Napolitano A, Pala L, Pennacchioli E, Catania C, Queirolo P, Grigani G, Merlini A, Stacchiotti S, Comandone A, Vincenzi B, Quagliuolo V, Bertuzzi A, Boglione A, Palassini E, Baldi GG, Blay JY, Ryckewaert T, Toulmonde M, Italiano A, Le Cesne A, Ray-Coquard I, Cruz J, Hernández-León CN, Trufero JM, da Silva Moura D, Muñiz NH, De Pas T
Eur J Cancer 2022 Aug;171:183-192. Epub 2022 Jun 18 doi: 10.1016/j.ejca.2022.04.030. PMID: 35728378

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