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Extragonadal Embryonal Carcinoma

MedGen UID:
208964
Concept ID:
C0855159
Neoplastic Process
Synonyms: Extragonadal Primary Embryonal Carcinoma; Primary Extragonadal Embryonal Carcinoma

Definition

An embryonal carcinoma that develops as a primary tumor in an anatomic site other than the testis or ovary. [from NCI]

Professional guidelines

PubMed

Improta L, Tzanis D, Bouhadiba T, Abdelhafidh K, Bonvalot S
Eur J Surg Oncol 2020 Sep;46(9):1573-1579. Epub 2020 May 21 doi: 10.1016/j.ejso.2020.04.054. PMID: 32600897
Mortensen MS, Gundgaard MG, Daugaard G
Int J Androl 2011 Aug;34(4 Pt 2):e32-6. Epub 2011 Jun 9 doi: 10.1111/j.1365-2605.2011.01178.x. PMID: 21651575
Mickisch GH
Curr Opin Urol 2000 Sep;10(5):465-71. doi: 10.1097/00042307-200009000-00017. PMID: 11005453

Recent clinical studies

Etiology

Murray MJ, Huddart RA, Coleman N
Nat Rev Urol 2016 Dec;13(12):715-725. Epub 2016 Oct 18 doi: 10.1038/nrurol.2016.170. PMID: 27754472
Mortensen MS, Gundgaard MG, Daugaard G
Int J Androl 2011 Aug;34(4 Pt 2):e32-6. Epub 2011 Jun 9 doi: 10.1111/j.1365-2605.2011.01178.x. PMID: 21651575
Cheng L, Sung MT, Cossu-Rocca P, Jones TD, MacLennan GT, De Jong J, Lopez-Beltran A, Montironi R, Looijenga LH
J Pathol 2007 Jan;211(1):1-9. doi: 10.1002/path.2105. PMID: 17117392
Mickisch GH
Curr Opin Urol 2000 Sep;10(5):465-71. doi: 10.1097/00042307-200009000-00017. PMID: 11005453
Hainsworth JD, Greco FA
Hematol Oncol Clin North Am 1991 Dec;5(6):1223-31. PMID: 1663941

Diagnosis

Aguiar Bujanda D, Pérez Cabrera D, Croissier Sánchez L
Am J Clin Oncol 2022 Dec 1;45(12):493-500. Epub 2022 Nov 17 doi: 10.1097/COC.0000000000000959. PMID: 36394133
El-Zaatari ZM, Ro JY
Adv Anat Pathol 2021 Sep 1;28(5):335-350. doi: 10.1097/PAP.0000000000000304. PMID: 34029275
Improta L, Tzanis D, Bouhadiba T, Abdelhafidh K, Bonvalot S
Eur J Surg Oncol 2020 Sep;46(9):1573-1579. Epub 2020 May 21 doi: 10.1016/j.ejso.2020.04.054. PMID: 32600897
Ronchi A, Cozzolino I, Montella M, Panarese I, Zito Marino F, Rossetti S, Chieffi P, Accardo M, Facchini G, Franco R
Cancer Med 2019 Nov;8(16):6832-6840. Epub 2019 Sep 30 doi: 10.1002/cam4.2195. PMID: 31568647Free PMC Article
Cheng L, Lyu B, Roth LM
Hum Pathol 2017 Jan;59:10-25. Epub 2016 Aug 26 doi: 10.1016/j.humpath.2016.08.002. PMID: 27569298

Therapy

Cierna Z, Mego M, Miskovska V, Machalekova K, Chovanec M, Svetlovska D, Hainova K, Rejlekova K, Macak D, Spanik S, Ondrus D, Kajo K, Mardiak J, Babal P
Ann Oncol 2016 Feb;27(2):300-5. Epub 2015 Nov 23 doi: 10.1093/annonc/mdv574. PMID: 26598537Free PMC Article
Berardi R, Pellei C, Valeri G, Pistelli M, Onofri A, Morgese F, Caramanti M, Mirza RM, Santoni M, De Lisa M, Savini A, Ballatore Z, Giuseppetti GM, Cascinu S
J Toxicol Environ Health A 2015;78(1):1-6. doi: 10.1080/15287394.2015.958416. PMID: 25424542
Hirasaki S, Moriwaki T, Tsuzuki T, Hirao K, Hyodo I
Intern Med 2003 Nov;42(11):1122-6. doi: 10.2169/internalmedicine.42.1122. PMID: 14686754
Dieckmann KP, Loy V
Eur Urol 1995;28(1):25-30. doi: 10.1159/000475015. PMID: 8521890
Hainsworth JD, Greco FA
Hematol Oncol Clin North Am 1991 Dec;5(6):1223-31. PMID: 1663941

Prognosis

Aguiar Bujanda D, Pérez Cabrera D, Croissier Sánchez L
Am J Clin Oncol 2022 Dec 1;45(12):493-500. Epub 2022 Nov 17 doi: 10.1097/COC.0000000000000959. PMID: 36394133
Ronchi A, Cozzolino I, Montella M, Panarese I, Zito Marino F, Rossetti S, Chieffi P, Accardo M, Facchini G, Franco R
Cancer Med 2019 Nov;8(16):6832-6840. Epub 2019 Sep 30 doi: 10.1002/cam4.2195. PMID: 31568647Free PMC Article
Cheng L, Lyu B, Roth LM
Hum Pathol 2017 Jan;59:10-25. Epub 2016 Aug 26 doi: 10.1016/j.humpath.2016.08.002. PMID: 27569298
Weidner N
Semin Diagn Pathol 1999 Feb;16(1):42-50. PMID: 10355653
Oliver T, Mead G
Curr Opin Oncol 1993 May;5(3):559-67. doi: 10.1097/00001622-199305000-00018. PMID: 8388258

Clinical prediction guides

Aguiar Bujanda D, Pérez Cabrera D, Croissier Sánchez L
Am J Clin Oncol 2022 Dec 1;45(12):493-500. Epub 2022 Nov 17 doi: 10.1097/COC.0000000000000959. PMID: 36394133
Ronchi A, Cozzolino I, Montella M, Panarese I, Zito Marino F, Rossetti S, Chieffi P, Accardo M, Facchini G, Franco R
Cancer Med 2019 Nov;8(16):6832-6840. Epub 2019 Sep 30 doi: 10.1002/cam4.2195. PMID: 31568647Free PMC Article
Cheng L, Lyu B, Roth LM
Hum Pathol 2017 Jan;59:10-25. Epub 2016 Aug 26 doi: 10.1016/j.humpath.2016.08.002. PMID: 27569298
McKenney JK, Heerema-McKenney A, Rouse RV
Adv Anat Pathol 2007 Mar;14(2):69-92. doi: 10.1097/PAP.0b013e31803240e6. PMID: 17471115
Oliver T, Mead G
Curr Opin Oncol 1993 May;5(3):559-67. doi: 10.1097/00001622-199305000-00018. PMID: 8388258

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