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Superior mesenteric artery syndrome

MedGen UID:
21404
Concept ID:
C0038828
Disease or Syndrome
Synonyms: Arteriomesenteric duodenal compression syndrome; Cast syndrome; Vascular compression of the duodenum; Wilkie syndrome
SNOMED CT: SMAS - Superior mesenteric artery syndrome (197006009); Superior mesenteric artery syndrome (197006009)
 
Monarch Initiative: MONDO:0002687
Orphanet: ORPHA622099

Definition

A very rare syndrome characterized by compression of the third portion of the duodenum against the aorta. The compression is caused by the superior mesenteric artery. It results in complete or partial duodenal obstruction. Signs and symptoms include nausea, vomiting, abdominal pain and distention, failure to gain weight, and weight loss. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSuperior mesenteric artery syndrome

Professional guidelines

PubMed

Bronswijk M, Fransen L, Vanella G, Hiele M, van der Merwe S
Endoscopy 2021 Feb;53(2):204-205. Epub 2020 Jun 19 doi: 10.1055/a-1190-3228. PMID: 32559775
Jain N, Chopde A, Soni B, Sharma B, Saini S, Mishra S, Mishra S, Gupta R, Bhojwani R
Surg Endosc 2021 May;35(5):2029-2038. Epub 2020 Apr 27 doi: 10.1007/s00464-020-07598-1. PMID: 32342220
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209

Recent clinical studies

Etiology

Beita AKV, Whayne TF
Cardiovasc Hematol Agents Med Chem 2019;17(2):74-81. doi: 10.2174/1871525717666190920100518. PMID: 31538906
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209
Takagi H, Watanabe T, Umemoto T; ALICE(All-Literature Investigation of Cardiovascular Evidence) GROUP
Int Angiol 2015 Oct;34(5):454-8. Epub 2014 Sep 12 PMID: 25216355
Merrett ND, Wilson RB, Cosman P, Biankin AV
J Gastrointest Surg 2009 Feb;13(2):287-92. Epub 2008 Sep 23 doi: 10.1007/s11605-008-0695-4. PMID: 18810558
Ahmed AR, Taylor I
Postgrad Med J 1997 Dec;73(866):776-8. doi: 10.1136/pgmj.73.866.776. PMID: 9497945Free PMC Article

Diagnosis

Kerdiles T, Gras J
N Engl J Med 2023 Jul 27;389(4):359. doi: 10.1056/NEJMicm2213146. PMID: 37494487
Farina R, Foti PV, Cocuzza G, Costanzo V, Costanzo G, Conti A, Torcitto A, Pennisi M
J Ultrasound 2017 Dec;20(4):339-342. Epub 2017 Aug 3 doi: 10.1007/s40477-017-0257-2. PMID: 29204239Free PMC Article
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209
Takagi H, Watanabe T, Umemoto T; ALICE(All-Literature Investigation of Cardiovascular Evidence) GROUP
Int Angiol 2015 Oct;34(5):454-8. Epub 2014 Sep 12 PMID: 25216355
Merrett ND, Wilson RB, Cosman P, Biankin AV
J Gastrointest Surg 2009 Feb;13(2):287-92. Epub 2008 Sep 23 doi: 10.1007/s11605-008-0695-4. PMID: 18810558

Therapy

Lu SB, Guo YQ, Chen RY, Zhang YF
J Invest Surg 2024 Dec;37(1):2387524. Epub 2024 Aug 27 doi: 10.1080/08941939.2024.2387524. PMID: 39191411
Bhatkar D, Mishra G, Gour S, Munje R
Indian J Tuberc 2022 Oct;69(4):702-705. Epub 2021 Aug 19 doi: 10.1016/j.ijtb.2021.08.019. PMID: 36460412
Li X, Tian M, Yang H, Liu Y, Chen J, Tian H
Medicine (Baltimore) 2022 Sep 2;101(35):e30427. doi: 10.1097/MD.0000000000030427. PMID: 36107595Free PMC Article
Fan Y, Cai M, Wang J, Xia L
Ann Vasc Surg 2021 Oct;76:514-535. Epub 2021 Apr 24 doi: 10.1016/j.avsg.2021.03.032. PMID: 33905850
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209

Prognosis

Lu SB, Guo YQ, Chen RY, Zhang YF
J Invest Surg 2024 Dec;37(1):2387524. Epub 2024 Aug 27 doi: 10.1080/08941939.2024.2387524. PMID: 39191411
Ren PLJ, Gupta A
J Radiol Case Rep 2020 Mar;14(3):14-23. Epub 2020 Mar 31 doi: 10.3941/jrcr.v14i3.3830. PMID: 33082917Free PMC Article
Farina R, Foti PV, Cocuzza G, Costanzo V, Costanzo G, Conti A, Torcitto A, Pennisi M
J Ultrasound 2017 Dec;20(4):339-342. Epub 2017 Aug 3 doi: 10.1007/s40477-017-0257-2. PMID: 29204239Free PMC Article
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209
Chang J, Boules M, Rodriguez J, Walsh M, Rosenthal R, Kroh M
Surg Endosc 2017 Mar;31(3):1180-1185. Epub 2016 Jul 12 doi: 10.1007/s00464-016-5088-2. PMID: 27405482

Clinical prediction guides

Lu SB, Guo YQ, Chen RY, Zhang YF
J Invest Surg 2024 Dec;37(1):2387524. Epub 2024 Aug 27 doi: 10.1080/08941939.2024.2387524. PMID: 39191411
Jonas JP, Rössler F, Ghafoor S, Kobe A, Pfammatter T, Schlag C, Gutschow CA, Petrowsky H, Müller PC, Oberkofler CE
Langenbecks Arch Surg 2023 Jan 24;408(1):59. doi: 10.1007/s00423-023-02803-w. PMID: 36690823Free PMC Article
Warncke ES, Gursahaney DL, Mascolo M, Dee E
Abdom Radiol (NY) 2019 Sep;44(9):3188-3194. doi: 10.1007/s00261-019-02066-4. PMID: 31127323
Ananthan K, Onida S, Davies AH
Eur J Vasc Endovasc Surg 2017 Jun;53(6):886-894. Epub 2017 Mar 27 doi: 10.1016/j.ejvs.2017.02.015. PMID: 28356209
Nana AM, Closset J, Muls V, Kouame J, Jeanmart J, van Gossum A, Gelin M, El Nakadi I
Surg Endosc 2003 Apr;17(4):659. Epub 2003 Feb 10 doi: 10.1007/s00464-002-4252-z. PMID: 12574933

Recent systematic reviews

Pappalardo G, Pola E, Bertini FA, Nasto LA, Eschweiler J, Schäfer L, Migliorini F
Eur J Med Res 2024 Aug 8;29(1):410. doi: 10.1186/s40001-024-02002-3. PMID: 39118170Free PMC Article
Jonas JP, Rössler F, Ghafoor S, Kobe A, Pfammatter T, Schlag C, Gutschow CA, Petrowsky H, Müller PC, Oberkofler CE
Langenbecks Arch Surg 2023 Jan 24;408(1):59. doi: 10.1007/s00423-023-02803-w. PMID: 36690823Free PMC Article
Fan Y, Cai M, Wang J, Xia L
Ann Vasc Surg 2021 Oct;76:514-535. Epub 2021 Apr 24 doi: 10.1016/j.avsg.2021.03.032. PMID: 33905850
Norris ML, Harrison ME, Isserlin L, Robinson A, Feder S, Sampson M
Int J Eat Disord 2016 Mar;49(3):216-37. Epub 2015 Sep 26 doi: 10.1002/eat.22462. PMID: 26407541
Munene G, Knab M, Parag B
Am Surg 2010 Mar;76(3):321-4. PMID: 20349665

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