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Turner syndrome(MX)

MedGen UID:
21734
Concept ID:
C0041408
Disease or Syndrome
Synonyms: Bonnevie-Ulrich syndrome; MX; Schereshevkii Turner Syndrome; Turner Varny Syndrome; Turner's syndrome; Ullrich-Turner syndrome
SNOMED CT: Turner's syndrome (38804009); TS - Turner's syndrome (38804009); Turner syndrome (38804009); Pterygolymphangiectasia syndrome (38804009)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0019499
Orphanet: ORPHA881

Definition

Turner syndrome is a chromosomal condition that affects development in people who are assigned female at birth. Females typically have two X chromosomes, but in individuals with Turner syndrome, one copy of the X chromosome is missing or altered.

The most common feature of Turner syndrome is short stature, which becomes evident by about age 5. Reduced functioning of the ovaries, the female reproductive organs that produce egg cells (oocytes) and female sex hormones, is also very common. The ovaries develop normally at first, but egg cells usually die prematurely and most ovarian tissue breaks down before birth. 

Many affected individuals do not undergo puberty unless they receive hormone therapy, and most are unable to become pregnant naturally. A small percentage of people with Turner syndrome retain normal ovarian function through young adulthood.

About 30 percent of individuals with Turner syndrome have extra folds of skin on the neck (webbed neck), a low hairline at the back of the neck, puffiness or swelling (lymphedema) of the hands and feet, skeletal abnormalities, or kidney problems. One-third to one-half of individuals with Turner syndrome are born with a heart defect, such as a narrowing of the large artery that leaves the heart (coarctation of the aorta) or abnormalities of the valve that connects the aorta to the heart (the aortic valve). Complications associated with these heart defects can be life-threatening.

Most people with Turner syndrome have normal intelligence. Developmental delays, nonverbal learning disabilities, and behavioral problems are possible, although these characteristics vary among affected individuals. [from MedlinePlus Genetics]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVTurner syndrome
Follow this link to review classifications for Turner syndrome in Orphanet.

Professional guidelines

PubMed

Gravholt CH, Viuff MH, Brun S, Stochholm K, Andersen NH
Nat Rev Endocrinol 2019 Oct;15(10):601-614. Epub 2019 Jun 18 doi: 10.1038/s41574-019-0224-4. PMID: 31213699
Gravholt CH, Andersen NH, Conway GS, Dekkers OM, Geffner ME, Klein KO, Lin AE, Mauras N, Quigley CA, Rubin K, Sandberg DE, Sas TCJ, Silberbach M, Söderström-Anttila V, Stochholm K, van Alfen-van derVelden JA, Woelfle J, Backeljauw PF; International Turner Syndrome Consensus Group
Eur J Endocrinol 2017 Sep;177(3):G1-G70. doi: 10.1530/EJE-17-0430. PMID: 28705803
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142

Recent clinical studies

Etiology

Hutaff-Lee C, Bennett E, Howell S, Tartaglia N
Am J Med Genet C Semin Med Genet 2019 Mar;181(1):126-134. Epub 2019 Feb 14 doi: 10.1002/ajmg.c.31687. PMID: 30767374Free PMC Article
Donato B, Ferreira MJ
Rev Port Cardiol (Engl Ed) 2018 Jul;37(7):607-621. Epub 2018 Jun 1 doi: 10.1016/j.repc.2017.08.008. PMID: 29866389
Álvarez-Nava F, Lanes R
Clin Epigenetics 2018;10:45. Epub 2018 Apr 6 doi: 10.1186/s13148-018-0477-0. PMID: 29636833Free PMC Article
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142
Kesler SR
Child Adolesc Psychiatr Clin N Am 2007 Jul;16(3):709-22. doi: 10.1016/j.chc.2007.02.004. PMID: 17562588Free PMC Article

Diagnosis

Steiner M, Saenger P
Adv Pediatr 2022 Aug;69(1):177-202. Epub 2022 Jun 17 doi: 10.1016/j.yapd.2022.03.004. PMID: 35985709
Gravholt CH, Viuff MH, Brun S, Stochholm K, Andersen NH
Nat Rev Endocrinol 2019 Oct;15(10):601-614. Epub 2019 Jun 18 doi: 10.1038/s41574-019-0224-4. PMID: 31213699
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142
Kesler SR
Child Adolesc Psychiatr Clin N Am 2007 Jul;16(3):709-22. doi: 10.1016/j.chc.2007.02.004. PMID: 17562588Free PMC Article
Ranke MB, Saenger P
Lancet 2001 Jul 28;358(9278):309-14. doi: 10.1016/S0140-6736(01)05487-3. PMID: 11498234

Therapy

Danowitz M, Grimberg A
Adv Pediatr 2022 Aug;69(1):203-217. Epub 2022 Jun 17 doi: 10.1016/j.yapd.2022.03.005. PMID: 35985710Free PMC Article
Gravholt CH, Viuff MH, Brun S, Stochholm K, Andersen NH
Nat Rev Endocrinol 2019 Oct;15(10):601-614. Epub 2019 Jun 18 doi: 10.1038/s41574-019-0224-4. PMID: 31213699
Milbrandt T, Thomas E
Pediatr Rev 2013 Sep;34(9):420-1. doi: 10.1542/pir.34-9-420. PMID: 24000347
Morgan T
Am Fam Physician 2007 Aug 1;76(3):405-10. PMID: 17708142
Kesler SR
Child Adolesc Psychiatr Clin N Am 2007 Jul;16(3):709-22. doi: 10.1016/j.chc.2007.02.004. PMID: 17562588Free PMC Article

Prognosis

Viuff M, Gravholt CH
Ann Endocrinol (Paris) 2022 Aug;83(4):244-249. Epub 2022 Jun 18 doi: 10.1016/j.ando.2022.06.001. PMID: 35728697
Calanchini M, Aye CYL, Orchard E, Baker K, Child T, Fabbri A, Mackillop L, Turner HE
Fertil Steril 2020 Jul;114(1):144-154. doi: 10.1016/j.fertnstert.2020.03.002. PMID: 32622407
Al Shaikh A, Daftardar H, Alghamdi AA, Jamjoom M, Awidah S, Ahmed ME, Soliman AT
Acta Biomed 2020 Mar 19;91(1):29-40. doi: 10.23750/abm.v91i1.9182. PMID: 32191651Free PMC Article
Mavridi A, Ntali G, Theodora M, Stamatelopoulos K, Michala L
J Pediatr Adolesc Gynecol 2018 Dec;31(6):651-654. Epub 2018 Aug 20 doi: 10.1016/j.jpag.2018.07.005. PMID: 30012427
Smith CC, Bevelaqua AC
Phys Med Rehabil Clin N Am 2014 May;25(2):265-77. Epub 2014 Mar 18 doi: 10.1016/j.pmr.2014.01.001. PMID: 24787332

Clinical prediction guides

Yoon SH, Kim GY, Choi GT, Do JT
Cells 2023 May 11;12(10) doi: 10.3390/cells12101365. PMID: 37408200Free PMC Article
Isojima T, Yokoya S
Front Endocrinol (Lausanne) 2022;13:1068128. Epub 2023 Jan 12 doi: 10.3389/fendo.2022.1068128. PMID: 36714599Free PMC Article
Aksoy E, Cogulu O, Pariltay E, Ozen S, Ata A, Karaca E, Darcan S
J Pediatr Endocrinol Metab 2022 Sep 27;35(9):1161-1168. Epub 2022 Aug 12 doi: 10.1515/jpem-2022-0153. PMID: 35953302
Calanchini M, Aye CYL, Orchard E, Baker K, Child T, Fabbri A, Mackillop L, Turner HE
Fertil Steril 2020 Jul;114(1):144-154. doi: 10.1016/j.fertnstert.2020.03.002. PMID: 32622407
Hutaff-Lee C, Bennett E, Howell S, Tartaglia N
Am J Med Genet C Semin Med Genet 2019 Mar;181(1):126-134. Epub 2019 Feb 14 doi: 10.1002/ajmg.c.31687. PMID: 30767374Free PMC Article

Recent systematic reviews

Elwenspoek MM, Thom H, Sheppard AL, Keeney E, O'Donnell R, Jackson J, Roadevin C, Dawson S, Lane D, Stubbs J, Everitt H, Watson JC, Hay AD, Gillett P, Robins G, Jones HE, Mallett S, Whiting PF
Health Technol Assess 2022 Oct;26(44):1-310. doi: 10.3310/ZUCE8371. PMID: 36321689Free PMC Article
Craciunas L, Zdoukopoulos N, Vinayagam S, Mohiyiddeen L
Cochrane Database Syst Rev 2022 Oct 6;10(10):CD008209. doi: 10.1002/14651858.CD008209.pub2. PMID: 36200708Free PMC Article
Badeau M, Lindsay C, Blais J, Nshimyumukiza L, Takwoingi Y, Langlois S, Légaré F, Giguère Y, Turgeon AF, Witteman W, Rousseau F
Cochrane Database Syst Rev 2017 Nov 10;11(11):CD011767. doi: 10.1002/14651858.CD011767.pub2. PMID: 29125628Free PMC Article
Gravholt CH, Andersen NH, Conway GS, Dekkers OM, Geffner ME, Klein KO, Lin AE, Mauras N, Quigley CA, Rubin K, Sandberg DE, Sas TCJ, Silberbach M, Söderström-Anttila V, Stochholm K, van Alfen-van derVelden JA, Woelfle J, Backeljauw PF; International Turner Syndrome Consensus Group
Eur J Endocrinol 2017 Sep;177(3):G1-G70. doi: 10.1530/EJE-17-0430. PMID: 28705803
van Alfen N, van Engelen BG, Hughes RA
Cochrane Database Syst Rev 2009 Jul 8;2009(3):CD006976. doi: 10.1002/14651858.CD006976.pub2. PMID: 19588414Free PMC Article

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