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Atypical choroid plexus papilloma

MedGen UID:
220431
Concept ID:
C1266176
Neoplastic Process
Synonyms: ACPP; Atypical Choroid Plexus Papilloma; atypical choroid plexus papilloma; atypical choroid plexus papilloma (morphologic abnormality); Atypical CPP; atypical CPP; Atypical papilloma of choroid plexus; atypical papilloma of choroid plexus
SNOMED CT: Atypical choroid plexus papilloma (128904001); Atypical choroid plexus papilloma (1156470000); Atypical papilloma of choroid plexus (1156470000)
 
Monarch Initiative: MONDO:0002684
Orphanet: ORPHA251902

Definition

A very rare type of choroid plexus tumour that in contrast to papilloma of the choroid plexus has an increased likelihood of progression to carcinoma and of recurrence. The disease displays brisk mitoses, nuclear pleomorphism, raised cellular density, obscurity of the papillary growth pattern and cell necrosis. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAtypical choroid plexus papilloma
Follow this link to review classifications for Atypical choroid plexus papilloma in Orphanet.

Professional guidelines

PubMed

Ruiz-Garcia H, Huayllani MT, Incontri D, Whaley JJ, Marenco-Hillembrand L, Ebot J, Chaichana KL, Sheehan J, Quiñones-Hinojosa A, Trifiletti DM
J Neurooncol 2020 Sep;149(2):283-292. Epub 2020 Sep 8 doi: 10.1007/s11060-020-03603-8. PMID: 32897467
Thomas C, Metrock K, Kordes U, Hasselblatt M, Dhall G
J Neurooncol 2020 May;148(1):39-45. Epub 2020 Apr 28 doi: 10.1007/s11060-020-03509-5. PMID: 32342334Free PMC Article
Hosmann A, Hinker F, Dorfer C, Slavc I, Haberler C, Dieckmann K, Knosp E, Czech T
Acta Neurochir (Wien) 2019 Apr;161(4):745-754. Epub 2019 Feb 19 doi: 10.1007/s00701-019-03832-5. PMID: 30783805Free PMC Article

Recent clinical studies

Etiology

Browne-Farmer C, Hazrati LN, Mamatjan Y, Zadeh G, Dirks P, Rutka J, Malkin D, Bouffet E, Huang A, Tabori U, Ramaswamy V, Bartels U
J Neurooncol 2021 Oct;155(1):63-70. Epub 2021 Sep 16 doi: 10.1007/s11060-021-03843-2. PMID: 34529227
Chen Y, Zhao R, Shi W, Li H
Clin Neurol Neurosurg 2021 Jan;200:106345. Epub 2020 Nov 4 doi: 10.1016/j.clineuro.2020.106345. PMID: 33203591
Thomas C, Metrock K, Kordes U, Hasselblatt M, Dhall G
J Neurooncol 2020 May;148(1):39-45. Epub 2020 Apr 28 doi: 10.1007/s11060-020-03509-5. PMID: 32342334Free PMC Article
Crawford JR, Isaacs H Jr
Childs Nerv Syst 2019 Jun;35(6):937-944. Epub 2019 Apr 5 doi: 10.1007/s00381-019-04135-x. PMID: 30953158
Shi YZ, Chen MZ, Huang W, Guo LL, Chen X, Kong D, Zhuang YY, Xu YM, Zhang RR, Bo GJ, Wang ZQ
Acta Radiol 2017 Aug;58(8):983-990. Epub 2017 Mar 30 doi: 10.1177/0284185116676651. PMID: 28358248

Diagnosis

Browne-Farmer C, Hazrati LN, Mamatjan Y, Zadeh G, Dirks P, Rutka J, Malkin D, Bouffet E, Huang A, Tabori U, Ramaswamy V, Bartels U
J Neurooncol 2021 Oct;155(1):63-70. Epub 2021 Sep 16 doi: 10.1007/s11060-021-03843-2. PMID: 34529227
Chen Y, Zhao R, Shi W, Li H
Clin Neurol Neurosurg 2021 Jan;200:106345. Epub 2020 Nov 4 doi: 10.1016/j.clineuro.2020.106345. PMID: 33203591
Thomas C, Metrock K, Kordes U, Hasselblatt M, Dhall G
J Neurooncol 2020 May;148(1):39-45. Epub 2020 Apr 28 doi: 10.1007/s11060-020-03509-5. PMID: 32342334Free PMC Article
Shi YZ, Chen MZ, Huang W, Guo LL, Chen X, Kong D, Zhuang YY, Xu YM, Zhang RR, Bo GJ, Wang ZQ
Acta Radiol 2017 Aug;58(8):983-990. Epub 2017 Mar 30 doi: 10.1177/0284185116676651. PMID: 28358248
Safaee M, Oh MC, Bloch O, Sun MZ, Kaur G, Auguste KI, Tihan T, Parsa AT
Neuro Oncol 2013 Mar;15(3):255-67. Epub 2012 Nov 21 doi: 10.1093/neuonc/nos289. PMID: 23172371Free PMC Article

Therapy

Liu J, Luo M, Lv S, Tao S, Wu Z, Yu L, Lin D, Huang L, Wu L, Liao X, Zi J, Lai X, Yuan Y, Zhang W, Yang L
Front Endocrinol (Lausanne) 2022;13:865913. Epub 2022 Jul 5 doi: 10.3389/fendo.2022.865913. PMID: 35865311Free PMC Article
Wolff JE, Van Gool SW, Kutluk T, Diez B, Kebudi R, Timmermann B, Garami M, Sterba J, Fuller GN, Bison B, Kordes UR
J Neurooncol 2022 Feb;156(3):599-613. Epub 2022 Jan 8 doi: 10.1007/s11060-021-03942-0. PMID: 34997889Free PMC Article
Qi Q, Ni S, Zhou X, Huang B, Li X
World Neurosurg 2015 Dec;84(6):1660-7. Epub 2015 Jul 11 doi: 10.1016/j.wneu.2015.07.004. PMID: 26171890
Wrede B, Hasselblatt M, Peters O, Thall PF, Kutluk T, Moghrabi A, Mahajan A, Rutkowski S, Diez B, Wang X, Pietsch T, Kortmann RD, Paulus W, Jeibmann A, Wolff JEA
J Neurooncol 2009 Dec;95(3):383-392. Epub 2009 Jun 20 doi: 10.1007/s11060-009-9936-y. PMID: 19543851Free PMC Article
Banka S, Walsh R, Brundler MA
Childs Nerv Syst 2007 May;23(5):587-9. Epub 2006 Nov 15 doi: 10.1007/s00381-006-0249-6. PMID: 17106748

Prognosis

Yang Z, Jiang H, He D, Zhang S, Huang L, Gao P, Huang H, Cao J, Zhan Z
Sci Rep 2024 May 28;14(1):12219. doi: 10.1038/s41598-024-63218-1. PMID: 38806680Free PMC Article
Wolff JE, Van Gool SW, Kutluk T, Diez B, Kebudi R, Timmermann B, Garami M, Sterba J, Fuller GN, Bison B, Kordes UR
J Neurooncol 2022 Feb;156(3):599-613. Epub 2022 Jan 8 doi: 10.1007/s11060-021-03942-0. PMID: 34997889Free PMC Article
Ruiz-Garcia H, Huayllani MT, Incontri D, Whaley JJ, Marenco-Hillembrand L, Ebot J, Chaichana KL, Sheehan J, Quiñones-Hinojosa A, Trifiletti DM
J Neurooncol 2020 Sep;149(2):283-292. Epub 2020 Sep 8 doi: 10.1007/s11060-020-03603-8. PMID: 32897467
Thomas C, Metrock K, Kordes U, Hasselblatt M, Dhall G
J Neurooncol 2020 May;148(1):39-45. Epub 2020 Apr 28 doi: 10.1007/s11060-020-03509-5. PMID: 32342334Free PMC Article
Zhou WJ, Wang X, Peng JY, Ma SC, Zhang DN, Guan XD, Diao JF, Niu JX, Li CD, Jia W
Chin Med J (Engl) 2018 Dec 20;131(24):2938-2946. doi: 10.4103/0366-6999.247195. PMID: 30539906Free PMC Article

Clinical prediction guides

Yankelevich M, Finlay JL, Gorsi H, Kupsky W, Boue DR, Koschmann CJ, Kumar-Sinha C, Mody R
Cold Spring Harb Mol Case Stud 2021 Feb;7(1) Epub 2021 Feb 19 doi: 10.1101/mcs.a005272. PMID: 33608379Free PMC Article
Chen Y, Zhao R, Shi W, Li H
Clin Neurol Neurosurg 2021 Jan;200:106345. Epub 2020 Nov 4 doi: 10.1016/j.clineuro.2020.106345. PMID: 33203591
Ruiz-Garcia H, Huayllani MT, Incontri D, Whaley JJ, Marenco-Hillembrand L, Ebot J, Chaichana KL, Sheehan J, Quiñones-Hinojosa A, Trifiletti DM
J Neurooncol 2020 Sep;149(2):283-292. Epub 2020 Sep 8 doi: 10.1007/s11060-020-03603-8. PMID: 32897467
Trybula SJ, Karras C, Bowman RM, Alden TD, DiPatri AJ, Tomita T
Childs Nerv Syst 2020 Aug;36(8):1761-1766. Epub 2020 Mar 2 doi: 10.1007/s00381-020-04532-7. PMID: 32123998Free PMC Article
Bahar M, Hashem H, Tekautz T, Worley S, Tang A, de Blank P, Wolff J
J Neurooncol 2017 May;132(3):427-432. Epub 2017 Mar 13 doi: 10.1007/s11060-017-2384-1. PMID: 28290001

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