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Pancreatic acinar cell cystadenocarcinoma

MedGen UID:
224757
Concept ID:
C1266087
Neoplastic Process
Synonyms: Acinar cell cystadenocarcinoma; Acinar Cell Cystadenocarcinoma; acinar cell cystadenocarcinoma; acinar cell cystadenocarcinoma (morphologic abnormality); Acinar Cell Cystadenocarcinoma of Pancreas; acinar cell cystadenocarcinoma of pancreas; Acinar Cell Cystadenocarcinoma of the Pancreas; acinar cell cystadenocarcinoma of the pancreas; Pancreatic Acinar Cell Cystadenocarcinoma; pancreatic acinar cell cystadenocarcinoma
SNOMED CT: Acinar cell cystadenocarcinoma (128703004)
 
Monarch Initiative: MONDO:0004343

Definition

A cystic adenocarcinoma characterized by the presence of relatively uniform neoplastic cells which produce pancreatic enzymes and are arranged in acinar patterns. Signs and symptoms include abdominal pain, weight loss, nausea, and diarrhea. It usually has an aggressive clinical course. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPancreatic acinar cell cystadenocarcinoma

Recent clinical studies

Diagnosis

Beltraminelli HS, Buechner SA, Häusermann P
Dermatology 2004;208(3):265-7. doi: 10.1159/000077316. PMID: 15118385

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