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Solitary fibrous tumor

MedGen UID:
224764
Concept ID:
C1266119
Neoplastic Process
Synonyms: Fibrous Tumor, Solitary; Fibrous Tumors, Solitary; Solitary Fibrous Tumor; Solitary Fibrous Tumors; Tumor, Solitary Fibrous; Tumors, Solitary Fibrous
SNOMED CT: Localized fibrous tumor (128736003); Solitary fibrous tumor (128736003); Hemangiopericytoma (128736003)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0016238
Orphanet: ORPHA2126

Definition

A rare spindle cell neoplasm that may be benign or malignant and that most frequently arises from the pleura and peritoneum and rarely from other sites such as head and neck, liver and skeletal muscle. SFT may be clinically asymptomatic or may present with enlarging mass, compressive effects depending on the site involved and rarely with paraneoplastic manifestations (osteoarthropathy or hypoglycemia). [from ORDO]

Professional guidelines

PubMed

Kazazian K, Demicco EG, de Perrot M, Strauss D, Swallow CJ
Surg Oncol Clin N Am 2022 Jul;31(3):459-483. doi: 10.1016/j.soc.2022.03.009. PMID: 35715145
Smrke A, Thway K, H Huang P, Jones RL, Hayes AJ
Future Oncol 2021 Sep;17(27):3627-3636. Epub 2021 Aug 19 doi: 10.2217/fon-2021-0030. PMID: 34409859
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article

Recent clinical studies

Etiology

Smrke A, Thway K, H Huang P, Jones RL, Hayes AJ
Future Oncol 2021 Sep;17(27):3627-3636. Epub 2021 Aug 19 doi: 10.2217/fon-2021-0030. PMID: 34409859
Karpathiou G, Papoudou-Bai A, Ferrand E, Dumollard JM, Peoc'h M
Pathol Res Pract 2021 Jul;223:153477. Epub 2021 May 11 doi: 10.1016/j.prp.2021.153477. PMID: 33991851
Baranov E, Hornick JL
Head Neck Pathol 2020 Mar;14(1):43-58. Epub 2020 Jan 16 doi: 10.1007/s12105-019-01104-3. PMID: 31950474Free PMC Article
Kristensen BW, Priesterbach-Ackley LP, Petersen JK, Wesseling P
Ann Oncol 2019 Aug 1;30(8):1265-1278. doi: 10.1093/annonc/mdz164. PMID: 31124566Free PMC Article
Huang SC, Huang HY
Histol Histopathol 2019 Apr;34(4):313-334. Epub 2018 Nov 15 doi: 10.14670/HH-18-064. PMID: 30431144

Diagnosis

Kazazian K, Demicco EG, de Perrot M, Strauss D, Swallow CJ
Surg Oncol Clin N Am 2022 Jul;31(3):459-483. doi: 10.1016/j.soc.2022.03.009. PMID: 35715145
Kallen ME, Hornick JL
Am J Surg Pathol 2021 Jan;45(1):e1-e23. doi: 10.1097/PAS.0000000000001552. PMID: 32796172
Gunasekaran A, Santos JM, Vandergrift WA 3rd
World Neurosurg 2020 Sep;141:395-401. Epub 2020 Jul 5 doi: 10.1016/j.wneu.2020.06.108. PMID: 32640325
Olson NJ, Linos K
Arch Pathol Lab Med 2018 Jun;142(6):761-766. doi: 10.5858/arpa.2016-0570-RS. PMID: 29848035
Ahluwalia N, Attia R, Green A, Cane P, Routledge T
Ann R Coll Surg Engl 2015 Oct;97(7):e105-7. doi: 10.1308/rcsann.2015.0023. PMID: 26414372Free PMC Article

Therapy

Zhao M, He H, Cao D, Fan D, Xu M, Zhang X, Ru G
Am J Clin Pathol 2022 Jul 1;158(1):35-46. doi: 10.1093/ajcp/aqab211. PMID: 34999741
Kitada M, Yasuda S, Abe M, Yoshida N, Okazaki S, Ishibashi K
Gen Thorac Cardiovasc Surg 2020 Dec;68(12):1523-1527. Epub 2019 Dec 17 doi: 10.1007/s11748-019-01274-5. PMID: 31848901Free PMC Article
Kristensen BW, Priesterbach-Ackley LP, Petersen JK, Wesseling P
Ann Oncol 2019 Aug 1;30(8):1265-1278. doi: 10.1093/annonc/mdz164. PMID: 31124566Free PMC Article
Ebata T, Shimoi T, Bun S, Miyake M, Yoshida A, Shimomura A, Noguchi E, Yonemori K, Shimizu C, Fujiwara Y, Narita Y, Tamura K
Oncology 2018;94(6):340-344. Epub 2018 Apr 3 doi: 10.1159/000486623. PMID: 29614488
Toulmonde M, Penel N, Adam J, Chevreau C, Blay JY, Le Cesne A, Bompas E, Piperno-Neumann S, Cousin S, Grellety T, Ryckewaert T, Bessede A, Ghiringhelli F, Pulido M, Italiano A
JAMA Oncol 2018 Jan 1;4(1):93-97. doi: 10.1001/jamaoncol.2017.1617. PMID: 28662235Free PMC Article

Prognosis

Karpathiou G, Papoudou-Bai A, Ferrand E, Dumollard JM, Peoc'h M
Pathol Res Pract 2021 Jul;223:153477. Epub 2021 May 11 doi: 10.1016/j.prp.2021.153477. PMID: 33991851
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Kallen ME, Hornick JL
Am J Surg Pathol 2021 Jan;45(1):e1-e23. doi: 10.1097/PAS.0000000000001552. PMID: 32796172
Kristensen BW, Priesterbach-Ackley LP, Petersen JK, Wesseling P
Ann Oncol 2019 Aug 1;30(8):1265-1278. doi: 10.1093/annonc/mdz164. PMID: 31124566Free PMC Article
Olson NJ, Linos K
Arch Pathol Lab Med 2018 Jun;142(6):761-766. doi: 10.5858/arpa.2016-0570-RS. PMID: 29848035

Clinical prediction guides

Karpathiou G, Papoudou-Bai A, Ferrand E, Dumollard JM, Peoc'h M
Pathol Res Pract 2021 Jul;223:153477. Epub 2021 May 11 doi: 10.1016/j.prp.2021.153477. PMID: 33991851
Tariq MU, Din NU, Abdul-Ghafar J, Park YK
Diagn Pathol 2021 Apr 20;16(1):32. doi: 10.1186/s13000-021-01095-2. PMID: 33879215Free PMC Article
Olson NJ, Linos K
Arch Pathol Lab Med 2018 Jun;142(6):761-766. doi: 10.5858/arpa.2016-0570-RS. PMID: 29848035
Mariño-Enriquez A, Nascimento AF, Ligon AH, Liang C, Fletcher CD
Am J Surg Pathol 2017 Feb;41(2):234-244. doi: 10.1097/PAS.0000000000000770. PMID: 27879515
Demicco EG, Park MS, Araujo DM, Fox PS, Bassett RL, Pollock RE, Lazar AJ, Wang WL
Mod Pathol 2012 Sep;25(9):1298-306. Epub 2012 May 11 doi: 10.1038/modpathol.2012.83. PMID: 22575866

Recent systematic reviews

El-Abtah ME, Murayi R, Lee J, Recinos PF, Kshettry VR
World Neurosurg 2023 Feb;170:68-83. Epub 2022 Nov 18 doi: 10.1016/j.wneu.2022.11.062. PMID: 36403933
Tobias S, Jahshan S, Grober Y, Soustiel JF
Acta Neurol Belg 2022 Dec;122(6):1537-1545. Epub 2021 Sep 30 doi: 10.1007/s13760-021-01812-0. PMID: 34595730
Crocetti D, Sapienza P, Lamazza A, DE Felice F, Brachini G, Desiato E, Mingoli A, Fiori E, DE Cesare A
In Vivo 2021 Jul-Aug;35(4):1945-1950. doi: 10.21873/invivo.12461. PMID: 34182467Free PMC Article
de Morais EF, Martins HDD, Rodrigues KS, de França GM, da Silveira ÉJD, Freitas RA
Am J Clin Pathol 2020 Jun 8;154(1):15-22. doi: 10.1093/ajcp/aqaa027. PMID: 32134474
Stanisce L, Ahmad N, Levin K, Deckard N, Enriquez M, Brody J, Koshkareva Y
Head Neck Pathol 2020 Jun;14(2):516-524. Epub 2019 Jul 23 doi: 10.1007/s12105-019-01058-6. PMID: 31338745Free PMC Article

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